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Disorder of asparagine metabolism

MedGen UID:
831886
Concept ID:
CN227320
Disease or Syndrome
Synonym: disorder of asparagine metabolism
 
Monarch Initiative: MONDO:0018318
Orphanet: ORPHA391381

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDisorder of asparagine metabolism
Follow this link to review classifications for Disorder of asparagine metabolism in Orphanet.

Professional guidelines

PubMed

Kim N, Lee HJ
Biomed Res Int 2020;2020:2010728. Epub 2020 Nov 9 doi: 10.1155/2020/2010728. PMID: 33224974Free PMC Article
Banerji J
Int J Mol Med 2015 Sep;36(3):607-26. Epub 2015 Jul 15 doi: 10.3892/ijmm.2015.2285. PMID: 26178806Free PMC Article
Emadi A, Zokaee H, Sausville EA
Cancer Chemother Pharmacol 2014 May;73(5):875-83. Epub 2014 Feb 11 doi: 10.1007/s00280-014-2402-3. PMID: 24515335

Recent clinical studies

Etiology

Chen C, Liao J, Xia Y, Liu X, Jones R, Haran J, McCormick B, Sampson TR, Alam A, Ye K
Gut 2022 Nov;71(11):2233-2252. Epub 2022 Jan 11 doi: 10.1136/gutjnl-2021-326269. PMID: 35017199
Zhang W, Lin Y
Cells 2021 May 10;10(5) doi: 10.3390/cells10051153. PMID: 34068767Free PMC Article
Mammadova-Bach E, Jaeken J, Gudermann T, Braun A
Int J Mol Sci 2020 Aug 6;21(16) doi: 10.3390/ijms21165630. PMID: 32781578Free PMC Article
de Koning TJ
J Inherit Metab Dis 2017 Jul;40(4):609-620. Epub 2017 Jun 26 doi: 10.1007/s10545-017-0063-1. PMID: 28653176Free PMC Article
Lawicki S, Covin RB, Powers AA
Transfus Med Rev 2017 Jul;31(3):165-172. Epub 2016 Nov 9 doi: 10.1016/j.tmrv.2016.10.003. PMID: 28065763

Diagnosis

Yamashita M, Morio T
Curr Opin Immunol 2021 Oct;72:239-248. Epub 2021 Jul 12 doi: 10.1016/j.coi.2021.06.010. PMID: 34265590
Li S, Li C, Wang W
Vitam Horm 2020;113:129-181. Epub 2019 Nov 8 doi: 10.1016/bs.vh.2019.08.019. PMID: 32138947
de Koning TJ
J Inherit Metab Dis 2017 Jul;40(4):609-620. Epub 2017 Jun 26 doi: 10.1007/s10545-017-0063-1. PMID: 28653176Free PMC Article
Manig F, Kuhne K, von Neubeck C, Schwarzenbolz U, Yu Z, Kessler BM, Pietzsch J, Kunz-Schughart LA
J Biotechnol 2017 Jan 20;242:30-54. Epub 2016 Dec 5 doi: 10.1016/j.jbiotec.2016.12.001. PMID: 27932276
de Luis DA, Perez Castrillón JL, Dueñas A
Minerva Med 2009 Jun;100(3):229-36. Epub 2008 Apr 4 PMID: 19182739

Therapy

Lomelino CL, Andring JT, McKenna R, Kilberg MS
J Biol Chem 2017 Dec 8;292(49):19952-19958. Epub 2017 Oct 30 doi: 10.1074/jbc.R117.819060. PMID: 29084849Free PMC Article
Marini BL, Perissinotti AJ, Bixby DL, Brown J, Burke PW
Blood Rev 2017 Sep;31(5):328-338. Epub 2017 Jul 5 doi: 10.1016/j.blre.2017.06.002. PMID: 28697948
Lawicki S, Covin RB, Powers AA
Transfus Med Rev 2017 Jul;31(3):165-172. Epub 2016 Nov 9 doi: 10.1016/j.tmrv.2016.10.003. PMID: 28065763
de Luis DA, Perez Castrillón JL, Dueñas A
Minerva Med 2009 Jun;100(3):229-36. Epub 2008 Apr 4 PMID: 19182739
Richards NG, Kilberg MS
Annu Rev Biochem 2006;75:629-54. doi: 10.1146/annurev.biochem.75.103004.142520. PMID: 16756505Free PMC Article

Prognosis

Levy RJ, Frater CH, Gallentine WB, Phillips JM, Ruzhnikov MR
J Inherit Metab Dis 2022 May;45(3):571-583. Epub 2022 Mar 11 doi: 10.1002/jimd.12494. PMID: 35243670
Alharby E, Faqeih EA, Saleh M, Alameer S, Almuntashri M, Pastore A, Samman MA, Alnawfal AM, Hashem M, Zaytuni D, Alharbi G, Almannai M, Alasmari A, Mahmoud AA, Alwadei AH, Jad L, AlOtaibi A, Al-Hakami F, Eyaid W, Alkuraya FS, Alfadhel M, Peake RWA, Almontashiri NAM
Genet Med 2020 Dec;22(12):2071-2080. Epub 2020 Aug 3 doi: 10.1038/s41436-020-0919-x. PMID: 32741967
Li S, Li C, Wang W
Vitam Horm 2020;113:129-181. Epub 2019 Nov 8 doi: 10.1016/bs.vh.2019.08.019. PMID: 32138947
Lin Y, Liao K, Miao Y, Qian Z, Fang Z, Yang X, Nie Q, Jiang G, Liu J, Yu Y, Wan J, Zhang X, Hu Y, Jiang J, Qiu Y
J Natl Cancer Inst 2020 Apr 1;112(4):343-355. doi: 10.1093/jnci/djz155. PMID: 31400201Free PMC Article
Fergus C, Barnes D, Alqasem MA, Kelly VP
Nutrients 2015 Apr 15;7(4):2897-929. doi: 10.3390/nu7042897. PMID: 25884661Free PMC Article

Clinical prediction guides

Chen C, Hou G, Zeng C, Ren Y, Chen X, Peng C
Theranostics 2021;11(2):754-767. Epub 2021 Jan 1 doi: 10.7150/thno.51154. PMID: 33391503Free PMC Article
Cheng A, Tse KH, Chow HM, Gan Y, Song X, Ma F, Qian YXY, She W, Herrup K
Autophagy 2021 Aug;17(8):1998-2010. Epub 2020 Aug 14 doi: 10.1080/15548627.2020.1805860. PMID: 32757690Free PMC Article
Mohanty S, Chaudhary BP, Zoetewey D
Biomolecules 2020 Apr 17;10(4) doi: 10.3390/biom10040624. PMID: 32316603Free PMC Article
Tjondro HC, Loke I, Chatterjee S, Thaysen-Andersen M
Biol Rev Camb Philos Soc 2019 Dec;94(6):2068-2100. Epub 2019 Aug 14 doi: 10.1111/brv.12548. PMID: 31410980
de Koning TJ
J Inherit Metab Dis 2017 Jul;40(4):609-620. Epub 2017 Jun 26 doi: 10.1007/s10545-017-0063-1. PMID: 28653176Free PMC Article

Recent systematic reviews

Perna S, Alalwan TA, Alaali Z, Alnashaba T, Gasparri C, Infantino V, Hammad L, Riva A, Petrangolini G, Allegrini P, Rondanelli M
Int J Mol Sci 2019 Oct 22;20(20) doi: 10.3390/ijms20205232. PMID: 31652531Free PMC Article
Hu Y, Liu W, Huang R, Zhang X
J Lipid Res 2006 Sep;47(9):1908-14. Epub 2006 Jun 1 doi: 10.1194/jlr.M600108-JLR200. PMID: 16741292

Supplemental Content

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