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Cutaneous polyarteritis nodosa

MedGen UID:
83358
Concept ID:
C0343190
Disease or Syndrome
Synonyms: Cutaneous livedo with nodules; Cutaneous PAN; cutaneous PAN; Cutaneous periarteritis nodosa; cutaneous periarteritis nodosa; Cutaneous Polyarteritis Nodosa; cutaneous polyarteritis nodosa; Nodular livedo
SNOMED CT: Cutaneous polyarteritis nodosa (239926000); Cutaneous livedo with nodules (239926000); Nodular livedo (239926000)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0018592
Orphanet: ORPHA439729

Definition

Cutaneous polyarteritis nodosa (CPAN) is a rare limited form of polyarteritis nodosa (PAN, see this term), characterized by cutaneous vasculitis and mild and transient extracutaneous manifestations such as mild arthralgia, arthritis,myalgia, and rarely peripheral neuropathy. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCutaneous polyarteritis nodosa

Professional guidelines

PubMed

Elston DM
J Am Acad Dermatol 2022 Dec;87(6):1273-1274. Epub 2022 May 26 doi: 10.1016/j.jaad.2022.05.043. PMID: 35643240
Micheletti RG, Pagnoux C
Presse Med 2020 Oct;49(3):104033. Epub 2020 Jul 6 doi: 10.1016/j.lpm.2020.104033. PMID: 32645416
Ting TV
Pediatr Clin North Am 2014 Apr;61(2):321-46. Epub 2014 Jan 21 doi: 10.1016/j.pcl.2013.11.007. PMID: 24636649

Recent clinical studies

Etiology

Diaconescu S, Strat S, Balan GG, Anton C, Stefanescu G, Ioniuc I, Stanescu AMA
Medicina (Kaunas) 2020 Aug 23;56(9) doi: 10.3390/medicina56090425. PMID: 32842528Free PMC Article
Kato A, Hamada T, Miyake T, Morizane S, Hirai Y, Yamasaki O, Iwatsuki K
JAMA Dermatol 2018 Aug 1;154(8):922-926. doi: 10.1001/jamadermatol.2018.1601. PMID: 29955757Free PMC Article
Collins MP, Hadden RD
Nat Rev Neurol 2017 Apr 27;13(5):302-316. doi: 10.1038/nrneurol.2017.42. PMID: 28447661
Sharma A, Dogra S, Sharma K
Dermatol Clin 2015 Jul;33(3):475-87. doi: 10.1016/j.det.2015.03.012. PMID: 26143427
Bauzá A, España A, Idoate M
Br J Dermatol 2002 Apr;146(4):694-9. doi: 10.1046/j.1365-2133.2002.04624.x. PMID: 11966708

Diagnosis

Munera-Campos M, Bielsa I, Martínez-Morillo M, Aparicio G, Olivé A, Ferrándiz C
J Dtsch Dermatol Ges 2020 Nov;18(11):1250-1259. Epub 2020 Oct 4 doi: 10.1111/ddg.14271. PMID: 33015940
Micheletti RG, Pagnoux C
Presse Med 2020 Oct;49(3):104033. Epub 2020 Jul 6 doi: 10.1016/j.lpm.2020.104033. PMID: 32645416
Kato A, Hamada T, Miyake T, Morizane S, Hirai Y, Yamasaki O, Iwatsuki K
JAMA Dermatol 2018 Aug 1;154(8):922-926. doi: 10.1001/jamadermatol.2018.1601. PMID: 29955757Free PMC Article
Sharma A, Dogra S, Sharma K
Dermatol Clin 2015 Jul;33(3):475-87. doi: 10.1016/j.det.2015.03.012. PMID: 26143427
Bauzá A, España A, Idoate M
Br J Dermatol 2002 Apr;146(4):694-9. doi: 10.1046/j.1365-2133.2002.04624.x. PMID: 11966708

Therapy

Diaconescu S, Strat S, Balan GG, Anton C, Stefanescu G, Ioniuc I, Stanescu AMA
Medicina (Kaunas) 2020 Aug 23;56(9) doi: 10.3390/medicina56090425. PMID: 32842528Free PMC Article
Micheletti RG, Pagnoux C
Presse Med 2020 Oct;49(3):104033. Epub 2020 Jul 6 doi: 10.1016/j.lpm.2020.104033. PMID: 32645416
Sharma A, Dogra S, Sharma K
Dermatol Clin 2015 Jul;33(3):475-87. doi: 10.1016/j.det.2015.03.012. PMID: 26143427
Kawakami T
J Dermatol 2010 Feb;37(2):113-24. doi: 10.1111/j.1346-8138.2009.00761.x. PMID: 20175844
Uthman I
Curr Opin Pharmacol 2004 Apr;4(2):177-82. doi: 10.1016/j.coph.2003.11.004. PMID: 15063363

Prognosis

Kato A, Hamada T, Miyake T, Morizane S, Hirai Y, Yamasaki O, Iwatsuki K
JAMA Dermatol 2018 Aug 1;154(8):922-926. doi: 10.1001/jamadermatol.2018.1601. PMID: 29955757Free PMC Article
Macarenco RS, Galan A, Simoni PM, Macarenco AC, Tintle SJ, Rose R, Halasz CL, Carlson JA
Am J Dermatopathol 2013 Apr;35(2):213-9. doi: 10.1097/DAD.0b013e31825ba0ec. PMID: 22688396
Díaz-Pérez JL, De Lagrán ZM, Díaz-Ramón JL, Winkelmann RK
Semin Cutan Med Surg 2007 Jun;26(2):77-86. doi: 10.1016/j.sder.2007.02.003. PMID: 17544958
Bauzá A, España A, Idoate M
Br J Dermatol 2002 Apr;146(4):694-9. doi: 10.1046/j.1365-2133.2002.04624.x. PMID: 11966708
Siberry GK, Cohen BA, Johnson B
Arch Dermatol 1994 Jul;130(7):884-9. doi: 10.1001/archderm.130.7.884. PMID: 7912919

Clinical prediction guides

Munera-Campos M, Bielsa I, Martínez-Morillo M, Aparicio G, Olivé A, Ferrándiz C
J Dtsch Dermatol Ges 2020 Nov;18(11):1250-1259. Epub 2020 Oct 4 doi: 10.1111/ddg.14271. PMID: 33015940
Kato A, Hamada T, Miyake T, Morizane S, Hirai Y, Yamasaki O, Iwatsuki K
JAMA Dermatol 2018 Aug 1;154(8):922-926. doi: 10.1001/jamadermatol.2018.1601. PMID: 29955757Free PMC Article
Chasset F, Francès C
Clin Rev Allergy Immunol 2017 Dec;53(3):452-468. doi: 10.1007/s12016-017-8612-9. PMID: 28547523
Misago N, Mochizuki Y, Sekiyama-Kodera H, Shirotani M, Suzuki K, Inokuchi A, Narisawa Y
J Dermatol 2001 Dec;28(12):719-27. PMID: 11804068
Siberry GK, Cohen BA, Johnson B
Arch Dermatol 1994 Jul;130(7):884-9. doi: 10.1001/archderm.130.7.884. PMID: 7912919

Recent systematic reviews

Papachristodoulou E, Kakoullis L, Tiniakou E, Parperis K
Rheumatology (Oxford) 2021 Sep 1;60(9):4039-4047. doi: 10.1093/rheumatology/keab402. PMID: 33944902
Diaconescu S, Strat S, Balan GG, Anton C, Stefanescu G, Ioniuc I, Stanescu AMA
Medicina (Kaunas) 2020 Aug 23;56(9) doi: 10.3390/medicina56090425. PMID: 32842528Free PMC Article

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