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Stromal predominant kidney Wilms tumor

MedGen UID:
83529
Concept ID:
C0279610
Neoplastic Process
Synonyms: Stromal Predominant Kidney Adenosarcoma; stromal predominant kidney adenosarcoma; Stromal Predominant Kidney Wilms Tumor; stromal predominant kidney Wilms tumor; stromal predominant kidney Wilms' tumor; stromal predominant kidney Wilms' tumour; Stromal Predominant Nephroblastoma; stromal predominant nephroblastoma; Stromal Predominant Renal Adenosarcoma; stromal predominant renal adenosarcoma; Stromal Predominant Renal Wilm's Tumor; stromal predominant renal Wilm's tumor; stromal predominant renal Wilm's tumour; Stromal Predominant Renal Wilms Tumor; stromal predominant renal Wilms tumor; stromal predominant renal Wilms tumour; Stromal Predominant Renal Wilms' Tumor; stromal predominant renal Wilms' tumor; stromal predominant renal Wilms' tumour; stromal predominant Wilms tumor; stromal predominant Wilms tumour
 
Monarch Initiative: MONDO:0006432

Definition

Wilms tumor of the kidney characterized by the predominance of the mesenchymal component. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVStromal predominant kidney Wilms tumor

Professional guidelines

PubMed

Cullinan N, Villani A, Mourad S, Somers GR, Reichman L, van Engelen K, Stephens D, Weksberg R, Foulkes WD, Malkin D, Grant R, Goudie C
Int J Cancer 2020 Feb 15;146(4):1010-1017. Epub 2019 Jul 30 doi: 10.1002/ijc.32561. PMID: 31286500
Royer-Pokora B, Beier M, Henzler M, Alam R, Schumacher V, Weirich A, Huff V
Am J Med Genet A 2004 Jun 15;127A(3):249-57. doi: 10.1002/ajmg.a.30015. PMID: 15150775

Recent clinical studies

Etiology

Cullinan N, Villani A, Mourad S, Somers GR, Reichman L, van Engelen K, Stephens D, Weksberg R, Foulkes WD, Malkin D, Grant R, Goudie C
Int J Cancer 2020 Feb 15;146(4):1010-1017. Epub 2019 Jul 30 doi: 10.1002/ijc.32561. PMID: 31286500
D'Hooghe E, Mifsud W, Vujanić GM
Am J Surg Pathol 2019 Nov;43(11):1583-1590. doi: 10.1097/PAS.0000000000001335. PMID: 31600178
Kurose N, Takenaka M, Yamashita M, Shimaguchi C, Nakano M, Britni B, Guo X, Futatsuya C, Shioya A, Yamada S
Diagn Pathol 2018 Oct 27;13(1):84. doi: 10.1186/s13000-018-0761-5. PMID: 30368245Free PMC Article
Al-Hussain T, Ali A, Akhtar M
Adv Anat Pathol 2014 May;21(3):166-73. doi: 10.1097/PAP.0000000000000017. PMID: 24713986
Verschuur AC, Vujanic GM, Van Tinteren H, Jones KP, de Kraker J, Sandstedt B
Pediatr Blood Cancer 2010 Aug;55(2):233-8. doi: 10.1002/pbc.22496. PMID: 20582946

Diagnosis

Rashid MU, Naeemi H, Qazi AQ, Muhammad N, Ahmad M, Akhtar N, Rahman N
J Pediatr Hematol Oncol 2020 Apr;42(3):e128-e131. doi: 10.1097/MPH.0000000000001602. PMID: 31574018
Cullinan N, Villani A, Mourad S, Somers GR, Reichman L, van Engelen K, Stephens D, Weksberg R, Foulkes WD, Malkin D, Grant R, Goudie C
Int J Cancer 2020 Feb 15;146(4):1010-1017. Epub 2019 Jul 30 doi: 10.1002/ijc.32561. PMID: 31286500
D'Hooghe E, Mifsud W, Vujanić GM
Am J Surg Pathol 2019 Nov;43(11):1583-1590. doi: 10.1097/PAS.0000000000001335. PMID: 31600178
Kurose N, Takenaka M, Yamashita M, Shimaguchi C, Nakano M, Britni B, Guo X, Futatsuya C, Shioya A, Yamada S
Diagn Pathol 2018 Oct 27;13(1):84. doi: 10.1186/s13000-018-0761-5. PMID: 30368245Free PMC Article
Kadota K, Haba R, Kushida Y, Katsuki N, Hayashi T, Miyai Y, Bando K, Taoka R, Kakehi Y
Pathol Oncol Res 2009 Dec;15(4):665-9. Epub 2009 Apr 24 doi: 10.1007/s12253-009-9169-6. PMID: 19390992

Therapy

Littooij AS, Sebire NJ, Olsen ØE
J Magn Reson Imaging 2017 May;45(5):1316-1324. Epub 2016 Oct 11 doi: 10.1002/jmri.25506. PMID: 27726252
Hales PW, Olsen ØE, Sebire NJ, Pritchard-Jones K, Clark CA
NMR Biomed 2015 Aug;28(8):948-57. Epub 2015 Jun 9 doi: 10.1002/nbm.3337. PMID: 26058670
Verschuur AC, Vujanic GM, Van Tinteren H, Jones KP, de Kraker J, Sandstedt B
Pediatr Blood Cancer 2010 Aug;55(2):233-8. doi: 10.1002/pbc.22496. PMID: 20582946
Reinhard H, Semler O, Bürger D, Bode U, Flentje M, Göbel U, Gutjahr P, Leuschner I, Maass E, Niggli F, Scheel-Walter HG, Stöckle M, Thüroff JW, Tröger J, Weirich A, von Schweinitz D, Zoubek A, Graf N
Klin Padiatr 2004 May-Jun;216(3):132-40. doi: 10.1055/s-2004-822625. PMID: 15175957
Lovvorn HN 3rd, Savani RC, Ruchelli E, Cass DL, Adzick NS
J Pediatr Surg 2000 Jul;35(7):1070-8. doi: 10.1053/jpsu.2000.7774. PMID: 10917299

Prognosis

D'Hooghe E, Mifsud W, Vujanić GM
Am J Surg Pathol 2019 Nov;43(11):1583-1590. doi: 10.1097/PAS.0000000000001335. PMID: 31600178
Al-Hussain T, Ali A, Akhtar M
Adv Anat Pathol 2014 May;21(3):166-73. doi: 10.1097/PAP.0000000000000017. PMID: 24713986
Verschuur AC, Vujanic GM, Van Tinteren H, Jones KP, de Kraker J, Sandstedt B
Pediatr Blood Cancer 2010 Aug;55(2):233-8. doi: 10.1002/pbc.22496. PMID: 20582946
Lovvorn HN 3rd, Savani RC, Ruchelli E, Cass DL, Adzick NS
J Pediatr Surg 2000 Jul;35(7):1070-8. doi: 10.1053/jpsu.2000.7774. PMID: 10917299
Looi LM, Cheah PL
Pathology 1993 Apr;25(2):106-9. doi: 10.3109/00313029309084780. PMID: 8396229

Clinical prediction guides

Lai YC, Lu MY, Wang WC, Hou TC, Kuo CY
Int J Exp Pathol 2022 Jun;103(3):121-128. Epub 2022 Apr 18 doi: 10.1111/iep.12442. PMID: 35436013Free PMC Article
Rashid MU, Naeemi H, Qazi AQ, Muhammad N, Ahmad M, Akhtar N, Rahman N
J Pediatr Hematol Oncol 2020 Apr;42(3):e128-e131. doi: 10.1097/MPH.0000000000001602. PMID: 31574018
Kurose N, Takenaka M, Yamashita M, Shimaguchi C, Nakano M, Britni B, Guo X, Futatsuya C, Shioya A, Yamada S
Diagn Pathol 2018 Oct 27;13(1):84. doi: 10.1186/s13000-018-0761-5. PMID: 30368245Free PMC Article
Huang L, Mokkapati S, Hu Q, Ruteshouser EC, Hicks MJ, Huff V
Neoplasia 2016 Feb;18(2):71-81. doi: 10.1016/j.neo.2015.12.001. PMID: 26936393Free PMC Article
Lovvorn HN 3rd, Savani RC, Ruchelli E, Cass DL, Adzick NS
J Pediatr Surg 2000 Jul;35(7):1070-8. doi: 10.1053/jpsu.2000.7774. PMID: 10917299

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