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Childhood malignant schwannoma

MedGen UID:
83582
Concept ID:
C0279987
Neoplastic Process
Synonyms: Childhood Malignant Neoplasm of Peripheral Nerve Sheath; childhood malignant neoplasm of peripheral nerve sheath; Childhood Malignant Neoplasm of the Peripheral Nerve Sheath; childhood malignant neoplasm of the peripheral nerve sheath; Childhood Malignant Neurilemmoma; childhood malignant neurilemmoma; Childhood Malignant Peripheral Nerve Sheath Neoplasm; childhood malignant peripheral nerve sheath neoplasm; Childhood Malignant Peripheral Nerve Sheath Tumor; childhood malignant peripheral nerve sheath tumor; childhood malignant peripheral nerve sheath tumour; Childhood Malignant Schwannoma; childhood malignant schwannoma; Childhood Malignant Tumor of Peripheral Nerve Sheath; childhood malignant tumor of peripheral nerve sheath; Childhood Malignant Tumor of the Peripheral Nerve Sheath; childhood malignant tumor of the peripheral nerve sheath; childhood malignant tumour of peripheral nerve sheath; childhood malignant tumour of the peripheral nerve sheath; Childhood MPNST; childhood MPNST; childhood neurofibrosarcoma; childhood neurogenic sarcoma; paediatric malignant neoplasm of peripheral nerve sheath; paediatric malignant neoplasm of the peripheral nerve sheath; paediatric malignant neurilemmoma; paediatric malignant peripheral nerve sheath neoplasm; paediatric malignant peripheral nerve sheath tumour; paediatric malignant schwannoma; paediatric malignant tumour of peripheral nerve sheath; paediatric malignant tumour of the peripheral nerve sheath; paediatric MPNST; Pediatric Malignant Neoplasm of Peripheral Nerve Sheath; pediatric malignant neoplasm of peripheral nerve sheath; Pediatric Malignant Neoplasm of the Peripheral Nerve Sheath; pediatric malignant neoplasm of the peripheral nerve sheath; Pediatric Malignant Neurilemmoma; pediatric malignant neurilemmoma; Pediatric Malignant Peripheral Nerve Sheath Neoplasm; pediatric malignant peripheral nerve sheath neoplasm; Pediatric Malignant Peripheral Nerve Sheath Tumor; pediatric malignant peripheral nerve sheath tumor; Pediatric Malignant Schwannoma; pediatric malignant schwannoma; Pediatric Malignant Tumor of Peripheral Nerve Sheath; pediatric malignant tumor of peripheral nerve sheath; Pediatric Malignant Tumor of the Peripheral Nerve Sheath; pediatric malignant tumor of the peripheral nerve sheath; Pediatric MPNST; pediatric MPNST
 
Monarch Initiative: MONDO:0004345

Definition

A malignant peripheral nerve sheath tumor occurring in children. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood malignant schwannoma

Professional guidelines

PubMed

Nguyen TMK, Behnert A, Pietsch T, Vokuhl C, Kratz CP
Fam Cancer 2021 Oct;20(4):273-277. Epub 2021 Feb 26 doi: 10.1007/s10689-021-00234-4. PMID: 33634344Free PMC Article
Schomberg PJ, Gunderson LL, Moir CR, Gilchrist GS, Smithson WA
Cancer 1997 Jun 1;79(11):2251-6. PMID: 9179074

Recent clinical studies

Therapy

Nguyen TMK, Behnert A, Pietsch T, Vokuhl C, Kratz CP
Fam Cancer 2021 Oct;20(4):273-277. Epub 2021 Feb 26 doi: 10.1007/s10689-021-00234-4. PMID: 33634344Free PMC Article
Evans DG, Birch JM, Ramsden RT, Sharif S, Baser ME
J Med Genet 2006 Apr;43(4):289-94. Epub 2005 Sep 9 doi: 10.1136/jmg.2005.036319. PMID: 16155191Free PMC Article
Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Horowitz ME, Pratt CB, Webber BL, Hustu HO, Etcubanas E, Miliauskas J, Rao BN, Fleming ID, Mahesh Kumar AP, Green AA
J Clin Oncol 1986 Apr;4(4):559-64. doi: 10.1200/JCO.1986.4.4.559. PMID: 3514805
Donaldson SS
Cancer 1985 May 1;55(9 Suppl):2184-97. doi: 10.1002/1097-0142(19850501)55:9+<2184::aid-cncr2820551422>3.0.co;2-n. PMID: 3884137

Prognosis

Kervarrec T, Pissaloux D, Tirode F, Samimi M, Jacquemus J, Castillo C, de la Fouchardière A
Virchows Arch 2022 Feb;480(2):369-382. Epub 2021 Nov 11 doi: 10.1007/s00428-021-03227-x. PMID: 34761304
Evans DGR, Salvador H, Chang VY, Erez A, Voss SD, Druker H, Scott HS, Tabori U
Clin Cancer Res 2017 Jun 15;23(12):e54-e61. doi: 10.1158/1078-0432.CCR-17-0590. PMID: 28620005
Kurtkaya-Yapicier O, Scheithauer B, Woodruff JM
Histol Histopathol 2003 Jul;18(3):925-34. doi: 10.14670/HH-18.925. PMID: 12792904
Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Crawford AH
Acta Orthop Scand Suppl 1986;218:1-60. PMID: 3083645

Clinical prediction guides

Kervarrec T, Pissaloux D, Tirode F, Samimi M, Jacquemus J, Castillo C, de la Fouchardière A
Virchows Arch 2022 Feb;480(2):369-382. Epub 2021 Nov 11 doi: 10.1007/s00428-021-03227-x. PMID: 34761304
Evans DGR, Salvador H, Chang VY, Erez A, Voss SD, Druker H, Scott HS, Tabori U
Clin Cancer Res 2017 Jun 15;23(12):e54-e61. doi: 10.1158/1078-0432.CCR-17-0590. PMID: 28620005
Rodriguez FJ, Folpe AL, Giannini C, Perry A
Acta Neuropathol 2012 Mar;123(3):295-319. Epub 2012 Feb 12 doi: 10.1007/s00401-012-0954-z. PMID: 22327363Free PMC Article
Matsui I, Tanimura M, Kobayashi N, Sawada T, Nagahara N, Akatsuka J
Cancer 1993 Nov 1;72(9):2746-54. doi: 10.1002/1097-0142(19931101)72:9<2746::aid-cncr2820720936>3.0.co;2-w. PMID: 8402499
O'Tuama LA, Janicek MJ, Barnes PD, Scott RM, Black PM, Sallan SE, Tarbell NJ, Kupsky WJ, Wagenaar D, Ulanski JS
Pediatr Neurol 1991 Jul-Aug;7(4):249-57. doi: 10.1016/0887-8994(91)90040-r. PMID: 1930415

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