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Dissecting aortic dilatation

MedGen UID:
8439
Concept ID:
C0012736
Disease or Syndrome
Synonym: Aortic aneurysm/dissection

Definition

A dissecting aneurysm formed between the intimal and medial layers of the aortic wall due to a tear in the tunica intima. [from NCI]

Professional guidelines

PubMed

Elzanaty AM, Patel N, Sabbagh E, Eltahawy EA
Curr Med Res Opin 2021 Mar;37(3):377-384. Epub 2021 Feb 8 doi: 10.1080/03007995.2021.1876648. PMID: 33460329
Morello F, Santoro M, Fargion AT, Grifoni S, Nazerian P
Intern Emerg Med 2021 Jan;16(1):171-181. Epub 2020 May 1 doi: 10.1007/s11739-020-02354-8. PMID: 32358680
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142

Recent clinical studies

Etiology

Verma R, Cohen G, Colbert J, Fedak PWM
Curr Opin Cardiol 2023 Mar 1;38(2):61-67. Epub 2022 Dec 29 doi: 10.1097/HCO.0000000000001020. PMID: 36718616
Tcheandjieu C, Xiao K, Tejeda H, Lynch JA, Ruotsalainen S, Bellomo T, Palnati M, Judy R, Klarin D, Kember RL, Verma S; Regeneron Genetics Center; VA Million Veterans Program; FinnGen Project, Palotie A, Daly M, Ritchie M, Rader DJ, Rivas MA, Assimes T, Tsao P, Damrauer S, Priest JR
Nat Genet 2022 Jun;54(6):772-782. Epub 2022 May 30 doi: 10.1038/s41588-022-01070-7. PMID: 35637384
Wortmann M, Peters AS, Erhart P, Körfer D, Böckler D, Dihlmann S
Cells 2021 Sep 15;10(9) doi: 10.3390/cells10092433. PMID: 34572082Free PMC Article
Braverman AC, Mittauer E, Harris KM, Evangelista A, Pyeritz RE, Brinster D, Conklin L, Suzuki T, Fanola C, Ouzounian M, Chen E, Myrmel T, Bekeredjian R, Hutchison S, Coselli J, Gilon D, O'Gara P, Davis M, Isselbacher E, Eagle K
JAMA Cardiol 2021 Jan 1;6(1):58-66. doi: 10.1001/jamacardio.2020.4876. PMID: 33052376Free PMC Article
Morello F, Santoro M, Fargion AT, Grifoni S, Nazerian P
Intern Emerg Med 2021 Jan;16(1):171-181. Epub 2020 May 1 doi: 10.1007/s11739-020-02354-8. PMID: 32358680

Diagnosis

Verma R, Cohen G, Colbert J, Fedak PWM
Curr Opin Cardiol 2023 Mar 1;38(2):61-67. Epub 2022 Dec 29 doi: 10.1097/HCO.0000000000001020. PMID: 36718616
Zeigler SM, Sloan B, Jones JA
Adv Exp Med Biol 2021;1348:185-206. doi: 10.1007/978-3-030-80614-9_8. PMID: 34807420Free PMC Article
Wortmann M, Peters AS, Erhart P, Körfer D, Böckler D, Dihlmann S
Cells 2021 Sep 15;10(9) doi: 10.3390/cells10092433. PMID: 34572082Free PMC Article
Braverman AC, Mittauer E, Harris KM, Evangelista A, Pyeritz RE, Brinster D, Conklin L, Suzuki T, Fanola C, Ouzounian M, Chen E, Myrmel T, Bekeredjian R, Hutchison S, Coselli J, Gilon D, O'Gara P, Davis M, Isselbacher E, Eagle K
JAMA Cardiol 2021 Jan 1;6(1):58-66. doi: 10.1001/jamacardio.2020.4876. PMID: 33052376Free PMC Article
Morello F, Santoro M, Fargion AT, Grifoni S, Nazerian P
Intern Emerg Med 2021 Jan;16(1):171-181. Epub 2020 May 1 doi: 10.1007/s11739-020-02354-8. PMID: 32358680

Therapy

Tcheandjieu C, Xiao K, Tejeda H, Lynch JA, Ruotsalainen S, Bellomo T, Palnati M, Judy R, Klarin D, Kember RL, Verma S; Regeneron Genetics Center; VA Million Veterans Program; FinnGen Project, Palotie A, Daly M, Ritchie M, Rader DJ, Rivas MA, Assimes T, Tsao P, Damrauer S, Priest JR
Nat Genet 2022 Jun;54(6):772-782. Epub 2022 May 30 doi: 10.1038/s41588-022-01070-7. PMID: 35637384
Elzanaty AM, Patel N, Sabbagh E, Eltahawy EA
Curr Med Res Opin 2021 Mar;37(3):377-384. Epub 2021 Feb 8 doi: 10.1080/03007995.2021.1876648. PMID: 33460329
Hofmann Bowman MA, Eagle KA, Milewicz DM
JAMA Cardiol 2019 Jul 1;4(7):702-707. doi: 10.1001/jamacardio.2019.1176. PMID: 31066871
Mussa FF, Horton JD, Moridzadeh R, Nicholson J, Trimarchi S, Eagle KA
JAMA 2016 Aug 16;316(7):754-63. doi: 10.1001/jama.2016.10026. PMID: 27533160
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142

Prognosis

Tcheandjieu C, Xiao K, Tejeda H, Lynch JA, Ruotsalainen S, Bellomo T, Palnati M, Judy R, Klarin D, Kember RL, Verma S; Regeneron Genetics Center; VA Million Veterans Program; FinnGen Project, Palotie A, Daly M, Ritchie M, Rader DJ, Rivas MA, Assimes T, Tsao P, Damrauer S, Priest JR
Nat Genet 2022 Jun;54(6):772-782. Epub 2022 May 30 doi: 10.1038/s41588-022-01070-7. PMID: 35637384
Braverman AC, Mittauer E, Harris KM, Evangelista A, Pyeritz RE, Brinster D, Conklin L, Suzuki T, Fanola C, Ouzounian M, Chen E, Myrmel T, Bekeredjian R, Hutchison S, Coselli J, Gilon D, O'Gara P, Davis M, Isselbacher E, Eagle K
JAMA Cardiol 2021 Jan 1;6(1):58-66. doi: 10.1001/jamacardio.2020.4876. PMID: 33052376Free PMC Article
Guo MH, Appoo JJ, Saczkowski R, Smith HN, Ouzounian M, Gregory AJ, Herget EJ, Boodhwani M
JAMA Netw Open 2018 Aug 3;1(4):e181281. doi: 10.1001/jamanetworkopen.2018.1281. PMID: 30646119Free PMC Article
Milewicz DM, Trybus KM, Guo DC, Sweeney HL, Regalado E, Kamm K, Stull JT
Arterioscler Thromb Vasc Biol 2017 Jan;37(1):26-34. Epub 2016 Nov 22 doi: 10.1161/ATVBAHA.116.303229. PMID: 27879251Free PMC Article
Siu SC, Silversides CK
J Am Coll Cardiol 2010 Jun 22;55(25):2789-800. doi: 10.1016/j.jacc.2009.12.068. PMID: 20579534

Clinical prediction guides

Verma R, Cohen G, Colbert J, Fedak PWM
Curr Opin Cardiol 2023 Mar 1;38(2):61-67. Epub 2022 Dec 29 doi: 10.1097/HCO.0000000000001020. PMID: 36718616
Tcheandjieu C, Xiao K, Tejeda H, Lynch JA, Ruotsalainen S, Bellomo T, Palnati M, Judy R, Klarin D, Kember RL, Verma S; Regeneron Genetics Center; VA Million Veterans Program; FinnGen Project, Palotie A, Daly M, Ritchie M, Rader DJ, Rivas MA, Assimes T, Tsao P, Damrauer S, Priest JR
Nat Genet 2022 Jun;54(6):772-782. Epub 2022 May 30 doi: 10.1038/s41588-022-01070-7. PMID: 35637384
Li Y, Ren P, Dawson A, Vasquez HG, Ageedi W, Zhang C, Luo W, Chen R, Li Y, Kim S, Lu HS, Cassis LA, Coselli JS, Daugherty A, Shen YH, LeMaire SA
Circulation 2020 Oct 6;142(14):1374-1388. Epub 2020 Oct 5 doi: 10.1161/CIRCULATIONAHA.120.046528. PMID: 33017217Free PMC Article
Hofmann Bowman MA, Eagle KA, Milewicz DM
JAMA Cardiol 2019 Jul 1;4(7):702-707. doi: 10.1001/jamacardio.2019.1176. PMID: 31066871
Mussa FF, Horton JD, Moridzadeh R, Nicholson J, Trimarchi S, Eagle KA
JAMA 2016 Aug 16;316(7):754-63. doi: 10.1001/jama.2016.10026. PMID: 27533160

Recent systematic reviews

D'Ascenzi F, Valentini F, Pistoresi S, Frascaro F, Piu P, Cavigli L, Valente S, Focardi M, Cameli M, Bonifazi M, Metra M, Mondillo S
Trends Cardiovasc Med 2022 Jul;32(5):299-308. Epub 2021 Jun 22 doi: 10.1016/j.tcm.2021.06.001. PMID: 34166791
Guo MH, Appoo JJ, Saczkowski R, Smith HN, Ouzounian M, Gregory AJ, Herget EJ, Boodhwani M
JAMA Netw Open 2018 Aug 3;1(4):e181281. doi: 10.1001/jamanetworkopen.2018.1281. PMID: 30646119Free PMC Article
Mussa FF, Horton JD, Moridzadeh R, Nicholson J, Trimarchi S, Eagle KA
JAMA 2016 Aug 16;316(7):754-63. doi: 10.1001/jama.2016.10026. PMID: 27533160
Zhang L, Zhao Z, Chen Y, Sun Y, Bao J, Jing Z, Zhou J
J Thorac Cardiovasc Surg 2016 Nov;152(5):1279-1288.e3. Epub 2016 Jun 29 doi: 10.1016/j.jtcvs.2016.06.027. PMID: 27453556
Covella M, Milan A, Totaro S, Cuspidi C, Re A, Rabbia F, Veglio F
J Hypertens 2014 Oct;32(10):1928-35; discussion 1935. doi: 10.1097/HJH.0000000000000286. PMID: 24979304

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