Y-linked deafness-1 (DFNY1) is characterized by male-limited postlingual progressive sensorineural hearing loss of variable severity, with onset in the first to third decades of life (Wang et al., 2009).
Genetic Heterogeneity of Y-Linked Deafness
DFNY2 (400047) is caused by mutation in the TBL1Y gene (400033). [from
OMIM]