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Childhood Malignant Small Intestinal Neoplasm

MedGen UID:
856663
•Concept ID:
C3897069
•
Neoplastic Process

Definition

A rare malignant small intestinal neoplasm that occurs during childhood. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood Malignant Small Intestinal Neoplasm

Professional guidelines

PubMed

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
The spectrum of celiac disease: epidemiology, clinical aspects and treatment.
Tack GJ, Verbeek WH, Schreurs MW, Mulder CJ
Nat Rev Gastroenterol Hepatol 2010 Apr;7(4):204-13. Epub 2010 Mar 9 doi: 10.1038/nrgastro.2010.23. PMID: 20212505
Cholelithiasis after treatment for childhood cancer.
Mahmoud H, Schell M, Pui CH
Cancer 1991 Mar 1;67(5):1439-42. doi: 10.1002/1097-0142(19910301)67:5<1439::aid-cncr2820670529>3.0.co;2-r. PMID: 1899356

Recent clinical studies

Etiology

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
Coffee and cancer risk: a summary overview.
Alicandro G, Tavani A, La Vecchia C
Eur J Cancer Prev 2017 Sep;26(5):424-432. doi: 10.1097/CEJ.0000000000000341. PMID: 28288025
Colorectal polyps in childhood.
Thakkar K, Fishman DS, Gilger MA
Curr Opin Pediatr 2012 Oct;24(5):632-7. doi: 10.1097/MOP.0b013e328357419f. PMID: 22890064
Intussusception in adults.
Balik AA, Ozturk G, Aydinli B, Alper F, Gumus H, Yildirgan MI, Basoglu M
Acta Chir Belg 2006 Jul-Aug;106(4):409-12. doi: 10.1080/00015458.2006.11679917. PMID: 17017694
Juvenile polyposis.
Desai DC, Neale KF, Talbot IC, Hodgson SV, Phillips RK
Br J Surg 1995 Jan;82(1):14-7. doi: 10.1002/bjs.1800820106. PMID: 7881943

Diagnosis

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
Inflammatory bowel disease and risk of small bowel cancer: a binational population-based cohort study from Denmark and Sweden.
Axelrad JE, Olén O, Sachs MC, Erichsen R, Pedersen L, Halfvarson J, Askling J, Ekbom A, Sørensen HT, Ludvigsson JF
Gut 2021 Feb;70(2):297-308. Epub 2020 May 30 doi: 10.1136/gutjnl-2020-320945. PMID: 32474410
Colorectal polyps in childhood.
Thakkar K, Fishman DS, Gilger MA
Curr Opin Pediatr 2012 Oct;24(5):632-7. doi: 10.1097/MOP.0b013e328357419f. PMID: 22890064
Vascular, polypoid, and other lesions of the small bowel.
Yano T, Yamamoto H
Best Pract Res Clin Gastroenterol 2009;23(1):61-74. doi: 10.1016/j.bpg.2008.12.001. PMID: 19258187
Gastrointestinal bleeding in infancy and childhood.
Vinton NE
Gastroenterol Clin North Am 1994 Mar;23(1):93-122. PMID: 8132302

Therapy

A Multi-Institutional Cohort of Therapy-Associated Polyposis in Childhood and Young Adulthood Cancer Survivors.
Biller LH, Ukaegbu C, Dhingra TG, Burke CA, Chertock Y, Chittenden A, Church JM, Koeppe ES, Leach BH, Levinson E, Lim RM, Lutz M, Salo-Mullen E, Sheikh R, Idos G, Kastrinos F, Stoffel E, Weiss JM, Hall MJ, Kalady MF, Stadler ZK, Syngal S, Yurgelun MB
Cancer Prev Res (Phila) 2020 Mar;13(3):291-298. Epub 2020 Feb 12 doi: 10.1158/1940-6207.CAPR-19-0416. PMID: 32051178Free PMC Article
Coffee and cancer risk: a summary overview.
Alicandro G, Tavani A, La Vecchia C
Eur J Cancer Prev 2017 Sep;26(5):424-432. doi: 10.1097/CEJ.0000000000000341. PMID: 28288025
Colorectal polyps in childhood.
Thakkar K, Fishman DS, Gilger MA
Curr Opin Pediatr 2012 Oct;24(5):632-7. doi: 10.1097/MOP.0b013e328357419f. PMID: 22890064
The emerging pathogenic and therapeutic importance of the anaplastic lymphoma kinase gene.
Kelleher FC, McDermott R
Eur J Cancer 2010 Sep;46(13):2357-68. Epub 2010 May 5 doi: 10.1016/j.ejca.2010.04.006. PMID: 20451371
Oesophageal replacement in children.
Arul GS, Parikh D
Ann R Coll Surg Engl 2008 Jan;90(1):7-12. doi: 10.1308/003588408X242222. PMID: 18201490Free PMC Article

Prognosis

Inflammatory bowel disease and risk of small bowel cancer: a binational population-based cohort study from Denmark and Sweden.
Axelrad JE, Olén O, Sachs MC, Erichsen R, Pedersen L, Halfvarson J, Askling J, Ekbom A, Sørensen HT, Ludvigsson JF
Gut 2021 Feb;70(2):297-308. Epub 2020 May 30 doi: 10.1136/gutjnl-2020-320945. PMID: 32474410
Malignant rhabdoid tumor of the small intestine in adults: a brief review of the literature and report of a case.
Voglino C, Scheiterle M, Di Mare G, Mariani F, De Stefano A, Ginori A, De Franco L, Ferrara F
Surg Today 2015 Jul;45(7):924-8. Epub 2014 Jun 25 doi: 10.1007/s00595-014-0955-8. PMID: 24957511
Paediatric intestinal cancer and polyposis due to bi-allelic PMS2 mutations: case series, review and follow-up guidelines.
Herkert JC, Niessen RC, Olderode-Berends MJ, Veenstra-Knol HE, Vos YJ, van der Klift HM, Scheenstra R, Tops CM, Karrenbeld A, Peters FT, Hofstra RM, Kleibeuker JH, Sijmons RH
Eur J Cancer 2011 May;47(7):965-82. Epub 2011 Mar 4 doi: 10.1016/j.ejca.2011.01.013. PMID: 21376568
Vascular, polypoid, and other lesions of the small bowel.
Yano T, Yamamoto H
Best Pract Res Clin Gastroenterol 2009;23(1):61-74. doi: 10.1016/j.bpg.2008.12.001. PMID: 19258187
Multifocal atrophic gastritis and gastric carcinoma.
Faraji EI, Frank BB
Gastroenterol Clin North Am 2002 Jun;31(2):499-516. doi: 10.1016/s0889-8553(02)00008-0. PMID: 12134615

Clinical prediction guides

In-Hospital Clinical Features, Morbidity, and Mortality of Patients with Neurofibromatosis 1 in France: A Nationwide, Population-Based Retrospective Cohort Study.
Diaz E, Bergqvist C, Peiffer B, Fertitta L, Jannic A, Ferkal S, Zehou O, Hemery F, Sbidian E, Wolkenstein P
J Invest Dermatol 2023 Dec;143(12):2408-2415.e7. Epub 2023 May 29 doi: 10.1016/j.jid.2023.04.034. PMID: 37257636
Italian cancer figures--Report 2015: The burden of rare cancers in Italy.
AIRTUM Working Group, Busco S, Buzzoni C, Mallone S, Trama A, Castaing M, Bella F, Amodio R, Bizzoco S, Cassetti T, Cirilli C, Cusimano R, De Angelis R, Fusco M, Gatta G, Gennaro V, Giacomin A, Giorgi Rossi P, Mangone L, Mannino S, Rossi S, Pierannunzio D, Tavilla A, Tognazzo S, Tumino R, Vicentini M, Vitale MF, Crocetti E, Dal Maso L
Epidemiol Prev 2016 Jan-Feb;40(1 Suppl 2):1-120. doi: 10.19191/EP16.1S2.P001.035. PMID: 26951748
Diversity of the clinical presentation of the MMR gene biallelic mutations.
Bougeard G, Olivier-Faivre L, Baert-Desurmont S, Tinat J, Martin C, Bouvignies E, Vasseur S, Huet F, Couillault G, Vabres P, Le Pessot F, Chapusot C, Malka D, Bressac-de Paillerets B, Tosi M, Frebourg T
Fam Cancer 2014 Mar;13(1):131-5. doi: 10.1007/s10689-013-9676-1. PMID: 24068316
Comparison of short bowel syndrome acquired early in life and during adolescence.
Bruzoni M, Sudan DL, Cusick RA, Thompson JS
Transplantation 2008 Jul 15;86(1):63-6. doi: 10.1097/TP.0b013e3181734995. PMID: 18622279
Peutz-Jeghers syndrome: case report and literature review.
Georgescu EF, Stănescu L, Simionescu C, Georgescu I, Ionescu R, Florescu G
Rom J Morphol Embryol 2008;49(2):241-5. PMID: 18516333

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