U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Familial Idiopathic Short Stature

MedGen UID:
858751
Concept ID:
C3899157
Finding

Definition

Idiopathic short stature in a child when either one or both parents is short in stature. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVFamilial Idiopathic Short Stature

Professional guidelines

PubMed

Vyas V, Menon RK
Indian J Pediatr 2021 Dec;88(12):1203-1208. Epub 2021 Oct 5 doi: 10.1007/s12098-021-03892-5. PMID: 34609657
Murray PG, Clayton PE, Chernausek SD
Lancet Diabetes Endocrinol 2018 Jul;6(7):564-574. Epub 2018 Feb 1 doi: 10.1016/S2213-8587(18)30034-2. PMID: 29397377
Grimberg A, Allen DB
Curr Opin Pediatr 2017 Aug;29(4):466-471. doi: 10.1097/MOP.0000000000000505. PMID: 28525404Free PMC Article

Recent clinical studies

Etiology

Lin L, Li M, Luo J, Li P, Zhou S, Yang Y, Chen K, Weng Y, Ge X, Mireguli M, Wei H, Yang H, Li G, Sun Y, Cui L, Zhang S, Chen J, Zeng G, Xu L, Luo X, Shen Y
J Clin Endocrinol Metab 2021 Jun 16;106(7):e2711-e2719. doi: 10.1210/clinem/dgab088. PMID: 33606014Free PMC Article
Chiarelli F, Primavera M, Mastromauro C
Minerva Pediatr 2020 Dec;72(6):452-461. Epub 2020 Jul 20 doi: 10.23736/S0026-4946.20.05980-0. PMID: 32686926
Sadler B, Haller G, Antunes L, Nikolov M, Amarillo I, Coe B, Dobbs MB, Gurnett CA
J Med Genet 2020 Dec;57(12):851-857. Epub 2020 Jun 9 doi: 10.1136/jmedgenet-2020-106842. PMID: 32518174Free PMC Article
Pedicelli S, Peschiaroli E, Violi E, Cianfarani S
J Clin Res Pediatr Endocrinol 2009;1(3):105-15. Epub 2009 Feb 1 doi: 10.4008/jcrpe.v1i3.53. PMID: 21274395Free PMC Article
Wit JM, Clayton PE, Rogol AD, Savage MO, Saenger PH, Cohen P
Growth Horm IGF Res 2008 Apr;18(2):89-110. Epub 2008 Jan 7 doi: 10.1016/j.ghir.2007.11.004. PMID: 18182313

Diagnosis

Chiarelli F, Primavera M, Mastromauro C
Minerva Pediatr 2020 Dec;72(6):452-461. Epub 2020 Jul 20 doi: 10.23736/S0026-4946.20.05980-0. PMID: 32686926
Léger J
Ann Endocrinol (Paris) 2017 Jun;78(2):106-107. Epub 2017 Apr 28 doi: 10.1016/j.ando.2017.04.008. PMID: 28457480
Barstow C, Rerucha C
Am Fam Physician 2015 Jul 1;92(1):43-50. PMID: 26132126
Rogol AD, Hayden GF
J Pediatr 2014 May;164(5 Suppl):S1-14.e6. doi: 10.1016/j.jpeds.2014.02.027. PMID: 24731744
Ranke MB
Nat Rev Endocrinol 2013 Jun;9(6):325-34. Epub 2013 Apr 23 doi: 10.1038/nrendo.2013.71. PMID: 23609338

Therapy

Yuan K, Chen J, Chen Q, Chen H, Zhu J, Fang Y, Wang C
J Pediatr Endocrinol Metab 2022 Feb 23;35(2):185-190. Epub 2021 Sep 27 doi: 10.1515/jpem-2021-0332. PMID: 34565054
Vyas V, Menon RK
Indian J Pediatr 2021 Dec;88(12):1203-1208. Epub 2021 Oct 5 doi: 10.1007/s12098-021-03892-5. PMID: 34609657
Lin L, Li M, Luo J, Li P, Zhou S, Yang Y, Chen K, Weng Y, Ge X, Mireguli M, Wei H, Yang H, Li G, Sun Y, Cui L, Zhang S, Chen J, Zeng G, Xu L, Luo X, Shen Y
J Clin Endocrinol Metab 2021 Jun 16;106(7):e2711-e2719. doi: 10.1210/clinem/dgab088. PMID: 33606014Free PMC Article
Grimberg A, Allen DB
Curr Opin Pediatr 2017 Aug;29(4):466-471. doi: 10.1097/MOP.0000000000000505. PMID: 28525404Free PMC Article
Ranke MB
Nat Rev Endocrinol 2013 Jun;9(6):325-34. Epub 2013 Apr 23 doi: 10.1038/nrendo.2013.71. PMID: 23609338

Prognosis

Li L, Chen L, Yang Y, Wang J, Guo L, An J, Ma X, Lu W, Xiao Y, Wang X, Dong Z
Front Endocrinol (Lausanne) 2022;13:890200. Epub 2022 Jun 10 doi: 10.3389/fendo.2022.890200. PMID: 35757432Free PMC Article
Rothermel J, Lass N, Toschke C, Reinehr T
Horm Res Paediatr 2016;86(2):117-125. Epub 2016 Aug 12 doi: 10.1159/000448283. PMID: 27513963
Audí L, Fernández-Cancio M, Camats N, Carrascosa A
Minerva Endocrinol 2013 Mar;38(1):1-16. PMID: 23435439
Diaz-Thomas A, Shulman D
Curr Opin Pediatr 2010 Aug;22(4):501-7. doi: 10.1097/MOP.0b013e32833ab888. PMID: 20489637
Bettendorf M, Graf K, Nelle M, Heinrich UE, Tröger J
Arch Dis Child 1998 Aug;79(2):165-8. doi: 10.1136/adc.79.2.165. PMID: 9797601Free PMC Article

Clinical prediction guides

Stavber L, Gaia MJ, Hovnik T, Jenko Bizjan B, Debeljak M, Kovač J, Omladič JŠ, Battelino T, Kotnik P, Dovč K
Genes (Basel) 2022 Jun 15;13(6) doi: 10.3390/genes13061065. PMID: 35741827Free PMC Article
Backeljauw P, Cappa M, Kiess W, Law L, Cookson C, Sert C, Whalen J, Dattani MT
Growth Horm IGF Res 2021 Apr-Jun;57-58:101392. Epub 2021 Apr 30 doi: 10.1016/j.ghir.2021.101392. PMID: 33975197
Lin L, Li M, Luo J, Li P, Zhou S, Yang Y, Chen K, Weng Y, Ge X, Mireguli M, Wei H, Yang H, Li G, Sun Y, Cui L, Zhang S, Chen J, Zeng G, Xu L, Luo X, Shen Y
J Clin Endocrinol Metab 2021 Jun 16;106(7):e2711-e2719. doi: 10.1210/clinem/dgab088. PMID: 33606014Free PMC Article
Bullinger M
Horm Res Paediatr 2011;76 Suppl 3:20-3. Epub 2011 Sep 7 doi: 10.1159/000330145. PMID: 21912153
Jorge AA, Funari MF, Nishi MY, Mendonca BB
Pediatr Endocrinol Rev 2010 Dec;8(2):79-85. PMID: 21150837

Recent systematic reviews

Lackner L, Quitmann J, Kristensen K, Witt S
Int J Environ Res Public Health 2023 Aug 11;20(16) doi: 10.3390/ijerph20166558. PMID: 37623144Free PMC Article
Backeljauw P, Cappa M, Kiess W, Law L, Cookson C, Sert C, Whalen J, Dattani MT
Growth Horm IGF Res 2021 Apr-Jun;57-58:101392. Epub 2021 Apr 30 doi: 10.1016/j.ghir.2021.101392. PMID: 33975197
Finkelstein BS, Imperiale TF, Speroff T, Marrero U, Radcliffe DJ, Cuttler L
Arch Pediatr Adolesc Med 2002 Mar;156(3):230-40. doi: 10.1001/archpedi.156.3.230. PMID: 11876666

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...