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Supramitral ring

MedGen UID:
866790
•Concept ID:
C4021142
•
Congenital Abnormality
Synonyms: Membranous supravalvular mitral stenosis; Supravalvular mitral ring
 
HPO: HP:0011572

Definition

A congenital stenotic mitral valvular anomaly with a ring of tissue above the mitral valve. [from HPO]

Recent clinical studies

Etiology

Surgical management of divided atrial chambers.
Sankhyan LK, Anderson RH, Chowdhury UK, George N, Pradeep D, Vaswani P, Pandey NN, Arvind B
J Card Surg 2021 Nov;36(11):4267-4279. Epub 2021 Aug 15 doi: 10.1111/jocs.15896. PMID: 34392568
Valve reconstruction for congenital mitral valve disease.
Quinonez LG, Del Nido PJ
Multimed Man Cardiothorac Surg 2015;2015 Epub 2015 May 26 doi: 10.1093/mmcts/mmv007. PMID: 26012593
Congenital supravalvar mitral ring: an underestimated anomaly.
Toscano A, Pasquini L, Iacobelli R, Di Donato RM, Raimondi F, Carotti A, Di Ciommo V, Sanders SP
J Thorac Cardiovasc Surg 2009 Mar;137(3):538-42. doi: 10.1016/j.jtcvs.2008.08.023. PMID: 19258061
Supramitral ring: good prognosis in a subset of patients with congenital mitral stenosis.
Collison SP, Kaushal SK, Dagar KS, Iyer PU, Girotra S, Radhakrishnan S, Shrivastava S, Iyer KS
Ann Thorac Surg 2006 Mar;81(3):997-1001. doi: 10.1016/j.athoracsur.2005.06.079. PMID: 16488709
Supramitral ring: an unusual cause of congenital mitral stenosis. Case series and review.
Mychaskiw G 2nd, Sachdev V, Braden DA, Heath BJ
J Cardiovasc Surg (Torino) 2002 Apr;43(2):199-202. PMID: 11887055

Diagnosis

Surgical management of divided atrial chambers.
Sankhyan LK, Anderson RH, Chowdhury UK, George N, Pradeep D, Vaswani P, Pandey NN, Arvind B
J Card Surg 2021 Nov;36(11):4267-4279. Epub 2021 Aug 15 doi: 10.1111/jocs.15896. PMID: 34392568
Three-dimensional echocardiography enhances diagnostic accuracy of supramitral ring.
Jone PN, Bremen C, DiMaria M, Campbell DN, Jaggers J, Younoszai A, Ivy DD
Echocardiography 2015 Jun;32(6):1048-50. Epub 2014 Dec 12 doi: 10.1111/echo.12867. PMID: 25496227
An analysis of 24 autopsied cases with supramitral rings.
Vaideeswar P, Baldi MM, Warghade S
Cardiol Young 2009 Feb;19(1):70-5. Epub 2008 Dec 11 doi: 10.1017/S1047951108003399. PMID: 19079810
Supramitral ring: good prognosis in a subset of patients with congenital mitral stenosis.
Collison SP, Kaushal SK, Dagar KS, Iyer PU, Girotra S, Radhakrishnan S, Shrivastava S, Iyer KS
Ann Thorac Surg 2006 Mar;81(3):997-1001. doi: 10.1016/j.athoracsur.2005.06.079. PMID: 16488709
Supramitral ring: an unusual cause of congenital mitral stenosis. Case series and review.
Mychaskiw G 2nd, Sachdev V, Braden DA, Heath BJ
J Cardiovasc Surg (Torino) 2002 Apr;43(2):199-202. PMID: 11887055

Therapy

Outcomes of reparative and transplantation strategies for multilevel left heart obstructions with mitral stenosis.
Malhotra SP, Lacour-Gayet F, Campbell DN, Miyamoto S, Clarke DR, Dines ML, Ivy DD, Mitchell MB
Ann Thorac Surg 2008 Oct;86(4):1305-9; discussion 1310. doi: 10.1016/j.athoracsur.2008.06.020. PMID: 18805182Free PMC Article

Prognosis

Perioperative management of a patient with double orifice mitral valve with supramitral ring with subaortic membrane with ventricular septal defect and severe pulmonary hypertension: Report of a rare case.
Datt V, Khurana P, Aggarwal S, Mishra S, Sujith CN, Virmani S
Ann Card Anaesth 2019 Apr-Jun;22(2):215-220. doi: 10.4103/aca.ACA_123_18. PMID: 30971608Free PMC Article
Valve reconstruction for congenital mitral valve disease.
Quinonez LG, Del Nido PJ
Multimed Man Cardiothorac Surg 2015;2015 Epub 2015 May 26 doi: 10.1093/mmcts/mmv007. PMID: 26012593
Congenital supravalvar mitral ring: an underestimated anomaly.
Toscano A, Pasquini L, Iacobelli R, Di Donato RM, Raimondi F, Carotti A, Di Ciommo V, Sanders SP
J Thorac Cardiovasc Surg 2009 Mar;137(3):538-42. doi: 10.1016/j.jtcvs.2008.08.023. PMID: 19258061
Supramitral ring: good prognosis in a subset of patients with congenital mitral stenosis.
Collison SP, Kaushal SK, Dagar KS, Iyer PU, Girotra S, Radhakrishnan S, Shrivastava S, Iyer KS
Ann Thorac Surg 2006 Mar;81(3):997-1001. doi: 10.1016/j.athoracsur.2005.06.079. PMID: 16488709
Supramitral ring: an unusual cause of congenital mitral stenosis. Case series and review.
Mychaskiw G 2nd, Sachdev V, Braden DA, Heath BJ
J Cardiovasc Surg (Torino) 2002 Apr;43(2):199-202. PMID: 11887055

Clinical prediction guides

Importance of accurate diagnosis using real-time three-dimensional echocardiography in the surgical treatment of congenital intramitral ring in infants.
Pawelec-Wojtalik M, Iorio FS, Anwar AM, El Midany AA
Interact Cardiovasc Thorac Surg 2011 Dec;13(6):669-71. Epub 2011 Oct 6 doi: 10.1510/icvts.2011.277491. PMID: 21979984
Congenital supravalvar mitral ring: an underestimated anomaly.
Toscano A, Pasquini L, Iacobelli R, Di Donato RM, Raimondi F, Carotti A, Di Ciommo V, Sanders SP
J Thorac Cardiovasc Surg 2009 Mar;137(3):538-42. doi: 10.1016/j.jtcvs.2008.08.023. PMID: 19258061

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