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Abnormality of the internal auditory canal

MedGen UID:
866802
•Concept ID:
C4021155
•
Anatomical Abnormality
Synonym: Abnormality of the internal acoustic meatus
 
HPO: HP:0011384

Definition

An abnormality of the Internal acoustic meatus, i.e., of the canal in the petrous part of the temporal bone through which the cranial nerve VII and cranial nerve VIII traverse. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormality of the internal auditory canal

Professional guidelines

PubMed

Feasibility of magnetic resonance imaging in the differential diagnosis of isolated acute audiovestibular loss.
Lee SJ, Lee SA, Kim BG, Hong HS, Lee JY, Lee JD
J Vestib Res 2018;28(5-6):385-391. doi: 10.3233/VES-190649. PMID: 30856134
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457
The clinical characteristics and treatment for sudden sensorineural hearing loss with vestibular schwannoma.
Lin C, Gong Q, Zuo W, Zhang R, Zhou A
Eur Arch Otorhinolaryngol 2015 Apr;272(4):839-842. Epub 2014 Jan 23 doi: 10.1007/s00405-014-2885-x. PMID: 24452772

Recent clinical studies

Etiology

Internal auditory canal volume in normal and malformed inner ears.
Bächinger D, Breitsprecher TM, Pscheidl A, Dhanasingh A, Mlynski R, Dazert S, Langner S, Weiss NM
Eur Arch Otorhinolaryngol 2023 May;280(5):2149-2154. Epub 2022 Oct 9 doi: 10.1007/s00405-022-07676-1. PMID: 36210370Free PMC Article
Arachnoid Cysts of the Internal Auditory Canal: Multiplanar Magnetic Resonance Imaging With Audio-Vestibular Correlates.
Di Stadio A, Dipietro L, Messineo D, Ralli M, Ricci G, Greco A, Brenner MJ
Laryngoscope 2021 Oct;131(10):2323-2331. Epub 2021 Jun 21 doi: 10.1002/lary.29699. PMID: 34152614Free PMC Article
Internal Auditory Canal Diverticula in Children: A Congenital Variant.
Muelleman TJ, Kavookjian H, Asmar J, Patel K, Nielsen D, Summers K, Tracy M, Noel-MacDonnell J, Staecker H, Ledbetter L, Weatherly R
Laryngoscope 2021 May;131(5):E1683-E1687. Epub 2020 Nov 17 doi: 10.1002/lary.29278. PMID: 33200834
Arachnoid cysts of the internal auditory canal: An underappreciated entity?
Ungar OJ, Franck M, Nadol JB, Santos F
Laryngoscope 2019 Jul;129(7):1667-1674. Epub 2018 Dec 8 doi: 10.1002/lary.27601. PMID: 30537076
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457

Diagnosis

Deep phenotyping of the neuroimaging and skeletal features in KBG syndrome: a study of 53 patients and review of the literature.
Peluso F, Caraffi SG, Contrò G, Valeri L, Napoli M, Carboni G, Seth A, Zuntini R, Coccia E, Astrea G, Bisgaard AM, Ivanovski I, Maitz S, Brischoux-Boucher E, Carter MT, Dentici ML, Devriendt K, Bellini M, Digilio MC, Doja A, Dyment DA, Farholt S, Ferreira CR, Wolfe LA, Gahl WA, Gnazzo M, Goel H, Grønborg SW, Hammer T, Iughetti L, Kleefstra T, Koolen DA, Lepri FR, Lemire G, Louro P, McCullagh G, Madeo SF, Milone A, Milone R, Nielsen JEK, Novelli A, Ockeloen CW, Pascarella R, Pippucci T, Ricca I, Robertson SP, Sawyer S, Falkenberg Smeland M, Stegmann S, Stumpel CT, Goel A, Taylor JM, Barbuti D, Soresina A, Bedeschi MF, Battini R, Cavalli A, Fusco C, Iascone M, Van Maldergem L, Venkateswaran S, Zuffardi O, Vergano S, Garavelli L, Bayat A
J Med Genet 2023 Nov 27;60(12):1224-1234. doi: 10.1136/jmg-2023-109141. PMID: 37586838Free PMC Article
Internal auditory canal volume in normal and malformed inner ears.
Bächinger D, Breitsprecher TM, Pscheidl A, Dhanasingh A, Mlynski R, Dazert S, Langner S, Weiss NM
Eur Arch Otorhinolaryngol 2023 May;280(5):2149-2154. Epub 2022 Oct 9 doi: 10.1007/s00405-022-07676-1. PMID: 36210370Free PMC Article
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457
Some Remarks on Imaging of the Inner Ear: Options and Limitations.
Giesemann A, Hofmann E
Clin Neuroradiol 2015 Oct;25 Suppl 2:197-203. Epub 2015 Jul 8 doi: 10.1007/s00062-015-0422-y. PMID: 26153464
Temporal bone imaging.
Casselman JW
Neuroimaging Clin N Am 1996 May;6(2):265-89. PMID: 8726907

Therapy

The misplaced cochlear implant electrode array.
Mehanna AM, Gamaleldin OA, Fathalla MF
Int J Pediatr Otorhinolaryngol 2019 Feb;117:96-104. Epub 2018 Nov 23 doi: 10.1016/j.ijporl.2018.11.027. PMID: 30579097
Isolated Internal Auditory Canal Diverticula: A Normal Anatomic Variant Not Associated with Sensorineural Hearing Loss.
Mihal DC, Feng Y, Kodet ML, Lohse CM, Carlson ML, Lane JI
AJNR Am J Neuroradiol 2018 Dec;39(12):2340-2344. Epub 2018 Nov 15 doi: 10.3174/ajnr.A5862. PMID: 30442698Free PMC Article
X-linked Malformation and Cochlear Implantation.
Smeds H, Wales J, Asp F, Löfkvist U, Falahat B, Anderlid BM, Anmyr L, Karltorp E
Otol Neurotol 2017 Jan;38(1):38-46. doi: 10.1097/MAO.0000000000001253. PMID: 27779564
Neurotological parameters and prognosis of Bell's palsy patients.
Chung JH, Lee SK, Kim SH, Yeo SG, Park MS, Byun JY
Audiol Neurootol 2015;20(2):117-121. Epub 2015 Mar 4 doi: 10.1159/000369609. PMID: 25765097
Common surgical pitfalls in the skull.
Keskil S, Gözil R, Calgüner E
Surg Neurol 2003 Mar;59(3):228-31; discussion 231. doi: 10.1016/s0090-3019(02)01038-8. PMID: 12681561

Prognosis

Otopathologic Abnormalities in CHARGE Syndrome.
da Costa Monsanto R, Knoll RM, de Oliveira Penido N, Song G, Santos F, Paparella MM, Cureoglu S
Otolaryngol Head Neck Surg 2022 Feb;166(2):363-372. Epub 2021 Apr 20 doi: 10.1177/01945998211008911. PMID: 33874787
The misplaced cochlear implant electrode array.
Mehanna AM, Gamaleldin OA, Fathalla MF
Int J Pediatr Otorhinolaryngol 2019 Feb;117:96-104. Epub 2018 Nov 23 doi: 10.1016/j.ijporl.2018.11.027. PMID: 30579097
Bony cochlear nerve canal and internal auditory canal measures predict cochlear nerve status.
Tahir E, Bajin MD, Atay G, Mocan BÖ, Sennaroğlu L
J Laryngol Otol 2017 Aug;131(8):676-683. Epub 2017 Jun 1 doi: 10.1017/S0022215117001141. PMID: 28566097
Some Remarks on Imaging of the Inner Ear: Options and Limitations.
Giesemann A, Hofmann E
Clin Neuroradiol 2015 Oct;25 Suppl 2:197-203. Epub 2015 Jul 8 doi: 10.1007/s00062-015-0422-y. PMID: 26153464
Neurotological parameters and prognosis of Bell's palsy patients.
Chung JH, Lee SK, Kim SH, Yeo SG, Park MS, Byun JY
Audiol Neurootol 2015;20(2):117-121. Epub 2015 Mar 4 doi: 10.1159/000369609. PMID: 25765097

Clinical prediction guides

Radiologic Findings in Pediatric Sudden Sensorineural Hearing Loss.
Tey CS, Kadom N, Dedhia K
Otol Neurotol 2021 Sep 1;42(8):1201-1207. doi: 10.1097/MAO.0000000000003188. PMID: 33973955
Internal Auditory Canal Diverticula in Children: A Congenital Variant.
Muelleman TJ, Kavookjian H, Asmar J, Patel K, Nielsen D, Summers K, Tracy M, Noel-MacDonnell J, Staecker H, Ledbetter L, Weatherly R
Laryngoscope 2021 May;131(5):E1683-E1687. Epub 2020 Nov 17 doi: 10.1002/lary.29278. PMID: 33200834
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457
X-linked Malformation and Cochlear Implantation.
Smeds H, Wales J, Asp F, Löfkvist U, Falahat B, Anderlid BM, Anmyr L, Karltorp E
Otol Neurotol 2017 Jan;38(1):38-46. doi: 10.1097/MAO.0000000000001253. PMID: 27779564
Treatment strategy in Goldenhar syndrome.
Bogusiak K, Arkuszewski P, Skorek-Stachnik K, Kozakiewicz M
J Craniofac Surg 2014 Jan;25(1):177-83. doi: 10.1097/SCS.0000000000000387. PMID: 24406574

Recent systematic reviews

Spontaneous Congenital Perilabyrinthine Cerebrospinal Fluid Fistulas.
Lovin BD, Appelbaum EN, Makoshi L, Whitehead WE, Sweeney AD
Ann Otol Rhinol Laryngol 2021 Dec;130(12):1360-1368. Epub 2021 Apr 9 doi: 10.1177/00034894211007242. PMID: 33834882
Sudden hearing loss as an early detector of multiple sclerosis: a systematic review.
Di Stadio A, Dipietro L, Ralli M, Meneghello F, Minni A, Greco A, Stabile MR, Bernitsas E
Eur Rev Med Pharmacol Sci 2018 Jul;22(14):4611-4624. doi: 10.26355/eurrev_201807_15520. PMID: 30058696

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