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Bilambdoid synostosis

MedGen UID:
866809
•Concept ID:
C4021163
•
Congenital Abnormality; Finding
Synonyms: Bilateral lambdoid craniosynostosis; Bilateral lambdoid suture synostosis
 
HPO: HP:0011319

Definition

Premature synostosis of both lambdoid sutures. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBilambdoid synostosis

Recent clinical studies

Etiology

Unexpected role of SIX1 variants in craniosynostosis: expanding the phenotype of SIX1-related disorders.
Calpena E, Wurmser M, McGowan SJ, Atique R, Bertola DR, Cunningham ML, Gustafson JA, Johnson D, Morton JEV, Passos-Bueno MR, Timberlake AT, Lifton RP, Wall SA, Twigg SRF, Maire P, Wilkie AOM
J Med Genet 2022 Feb;59(2):165-169. Epub 2021 Jan 12 doi: 10.1136/jmedgenet-2020-107459. PMID: 33436522Free PMC Article
Clinical Features of Bilambdoid and Sagittal Synostosis (BLSS): A Retrospective Multicenter Study in Japan.
Tamada I, Hikosaka M, Sakamoto Y, Tsuda K, Ihara S, Kaneko T, Kishi K
J Craniofac Surg 2021 Sep 1;32(6):2134-2138. doi: 10.1097/SCS.0000000000007482. PMID: 33534322
Secondary Suture Fusion after Primary Correction of Nonsyndromic Craniosynostosis: Recognition of the Problem and Identification of Risk Factors.
Vaca EE, Sheth N, Purnell CA, McGrath JL, Gosain AK
Plast Reconstr Surg 2020 Feb;145(2):493-503. doi: 10.1097/PRS.0000000000006491. PMID: 31985646
Dynamic cranioplasty for brachycephaly in apert syndrome: long-term follow-up study.
Guimarães-Ferreira J, Gewalli F, Sahlin P, Friede H, Owman-Moll P, Olsson R, Lauritzen CG
J Neurosurg 2001 May;94(5):757-64. doi: 10.3171/jns.2001.94.5.0757. PMID: 11354407

Diagnosis

Clinical Features of Bilambdoid and Sagittal Synostosis (BLSS): A Retrospective Multicenter Study in Japan.
Tamada I, Hikosaka M, Sakamoto Y, Tsuda K, Ihara S, Kaneko T, Kishi K
J Craniofac Surg 2021 Sep 1;32(6):2134-2138. doi: 10.1097/SCS.0000000000007482. PMID: 33534322
Secondary Suture Fusion after Primary Correction of Nonsyndromic Craniosynostosis: Recognition of the Problem and Identification of Risk Factors.
Vaca EE, Sheth N, Purnell CA, McGrath JL, Gosain AK
Plast Reconstr Surg 2020 Feb;145(2):493-503. doi: 10.1097/PRS.0000000000006491. PMID: 31985646
The Total Calvarial Remodeling with Transsutural Distraction Osteogenesis of 21 Cases of Craniosynostosis: New, Efficient, Safe and Natural Method in Craniosynostosis Surgery.
Park DH, Yoon SH
Pediatr Neurosurg 2015;50(3):119-27. Epub 2015 May 7 doi: 10.1159/000381860. PMID: 25968990
Bilambdoid and posterior sagittal synostosis: the Mercedes Benz syndrome.
Moore MH, Abbott AH, Netherway DJ, Menard R, Hanieh A
J Craniofac Surg 1998 Sep;9(5):417-22. doi: 10.1097/00001665-199809000-00003. PMID: 9780908

Prognosis

Dynamic cranioplasty for brachycephaly in apert syndrome: long-term follow-up study.
Guimarães-Ferreira J, Gewalli F, Sahlin P, Friede H, Owman-Moll P, Olsson R, Lauritzen CG
J Neurosurg 2001 May;94(5):757-64. doi: 10.3171/jns.2001.94.5.0757. PMID: 11354407

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