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Biventricular noncompaction cardiomyopathy

MedGen UID:
868319
•Concept ID:
C4022713
•
Disease or Syndrome
HPO: HP:0012818

Definition

Noncompaction cardiomyopathy that affects both ventricles. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Biventricular noncompaction cardiomyopathy

Professional guidelines

PubMed

Phenotype/Genotype Relationship in Left Ventricular Noncompaction: Ion Channel Gene Mutations Are Associated With Preserved Left Ventricular Systolic Function and Biventricular Noncompaction: Phenotype/Genotype of Noncompaction.
Cambon-Viala M, Gerard H, Nguyen K, Richard P, Ader F, Pruny JF, Donal E, Eicher JC, Huttin O, Selton-Suty C, Raud-Raynier P, Jondeau G, Mansencal N, Sawka C, Casalta AC, Michel N, Donghi V, Martel H, Faivre L, Charron P, Habib G
J Card Fail 2021 Jun;27(6):677-681. doi: 10.1016/j.cardfail.2021.01.007. PMID: 34088380
Ventricular non-compaction cardiomyopathy: prenatal diagnosis and pathology.
Tian L, Zhou Q, Zhou J, Zeng S, Cao D, Zhang M
Prenat Diagn 2015 Mar;35(3):221-7. Epub 2014 Dec 12 doi: 10.1002/pd.4523. PMID: 25346355

Recent clinical studies

Etiology

Unconventional 2:1 Ventricular Pacing in a Neonate with Congenital Heart Block and Biventricular Noncompaction.
Schneider AE, Wackel PL
Tex Heart Inst J 2019 Apr;46(2):136-138. Epub 2019 Apr 1 doi: 10.14503/THIJ-17-6368. PMID: 31236081Free PMC Article

Diagnosis

Biventricular Noncompaction Cardiomyopathy in a Patient Presenting With a New Cerebrovascular Event.
Madnawat H, Atallah I, Ahmad A, Harjai K
Am J Cardiol 2023 Mar 1;190:110-112. Epub 2023 Jan 6 doi: 10.1016/j.amjcard.2022.11.047. PMID: 36621285
Unconventional 2:1 Ventricular Pacing in a Neonate with Congenital Heart Block and Biventricular Noncompaction.
Schneider AE, Wackel PL
Tex Heart Inst J 2019 Apr;46(2):136-138. Epub 2019 Apr 1 doi: 10.14503/THIJ-17-6368. PMID: 31236081Free PMC Article
Biventricular noncompaction cardiomyopathy with malignant arrhythmia as a cause of sudden death.
Handlos P, Gruszka T, Staňková M, Marecová K, Joukal M
Forensic Sci Med Pathol 2017 Dec;13(4):495-499. Epub 2017 Jun 15 doi: 10.1007/s12024-017-9889-y. PMID: 28616812
Left Ventricular Assist Device Insertion in a Patient With Biventricular Noncompaction Cardiomyopathy, Ebstein Anomaly, and a Left Atrial Mass: A Case Report.
Kumar N, Troianos CA, Baisden JS
A A Case Rep 2016 Dec 15;7(12):251-255. doi: 10.1213/XAA.0000000000000399. PMID: 27749293

Prognosis

Unconventional 2:1 Ventricular Pacing in a Neonate with Congenital Heart Block and Biventricular Noncompaction.
Schneider AE, Wackel PL
Tex Heart Inst J 2019 Apr;46(2):136-138. Epub 2019 Apr 1 doi: 10.14503/THIJ-17-6368. PMID: 31236081Free PMC Article

Supplemental Content

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    Clinical resources

    Practice guidelines

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    Reviews

    Related information

    • ClinVar
      Related medical variations
    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

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