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Mid-frequency hearing loss

MedGen UID:
868329
Concept ID:
C4022723
Finding
HPO: HP:0012781

Definition

A type of hearing impairment affecting primarily the middle frequencies of sound (1000 Hz to 3000 Hz). [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMid-frequency hearing loss

Professional guidelines

PubMed

Govender SM, Mars M
S Afr J Commun Disord 2018 Jul 5;65(1):e1-e9. doi: 10.4102/sajcd.v65i1.582. PMID: 30035608Free PMC Article
Topsakal V, Hilgert N, van Dinther J, Tranebjaerg L, Rendtorff ND, Zarowski A, Offeciers E, Van Camp G, van de Heyning P
Audiol Neurootol 2010;15(4):211-20. Epub 2009 Nov 5 doi: 10.1159/000255339. PMID: 19893302
Zadeh MH, Storper IS, Spitzer JB
Otolaryngol Head Neck Surg 2003 Jan;128(1):92-8. doi: 10.1067/mhn.2003.50. PMID: 12574765

Recent clinical studies

Etiology

Yasukawa R, Moteki H, Nishio SY, Ishikawa K, Abe S, Honkura Y, Hyogo M, Mihashi R, Ikezono T, Shintani T, Ogasawara N, Shirai K, Yoshihashi H, Ishino T, Otsuki K, Ito T, Sugahara K, Usami SI
Genes (Basel) 2019 Sep 24;10(10) doi: 10.3390/genes10100744. PMID: 31554319Free PMC Article
Yamamoto N, Mutai H, Namba K, Morita N, Masuda S, Nishi Y, Nakano A, Masuda S, Fujioka M, Kaga K, Ogawa K, Matsunaga T
Orphanet J Rare Dis 2017 Sep 25;12(1):157. doi: 10.1186/s13023-017-0708-z. PMID: 28946916Free PMC Article
Rosenhall U, Sundh V
Noise Health 2006 Apr-Jun;8(31):88-94. doi: 10.4103/1463-1741.33539. PMID: 17687184
Kiefer J, Pok M, Adunka O, Stürzebecher E, Baumgartner W, Schmidt M, Tillein J, Ye Q, Gstoettner W
Audiol Neurootol 2005 May-Jun;10(3):134-44. Epub 2005 Feb 17 doi: 10.1159/000084023. PMID: 15724084
Zadeh MH, Storper IS, Spitzer JB
Otolaryngol Head Neck Surg 2003 Jan;128(1):92-8. doi: 10.1067/mhn.2003.50. PMID: 12574765

Diagnosis

Moore BCJ, Cox G
Trends Hear 2024 Jan-Dec;28:23312165241240353. doi: 10.1177/23312165241240353. PMID: 38545653Free PMC Article
Pavlenkova Z, Varga L, Borecka S, Karhanek M, Huckova M, Skopkova M, Profant M, Gasperikova D
Sci Rep 2021 Nov 18;11(1):22488. doi: 10.1038/s41598-021-01876-1. PMID: 34795337Free PMC Article
Kallman JC, Phillips JO, Bramhall NF, Kelly JP, Street VA
Otol Neurotol 2008 Sep;29(6):860-7. doi: 10.1097/MAO.0b013e3181825651. PMID: 18667942Free PMC Article
Zadeh MH, Storper IS, Spitzer JB
Otolaryngol Head Neck Surg 2003 Jan;128(1):92-8. doi: 10.1067/mhn.2003.50. PMID: 12574765
Bitner-Glindzicz M
Br Med Bull 2002;63:73-94. doi: 10.1093/bmb/63.1.73. PMID: 12324385

Therapy

Tsai YJ, Liang JG, Wu WB, Ding YF, Chiang RP, Wu SM
J Laryngol Otol 2011 Feb;125(2):133-7. Epub 2010 Nov 5 doi: 10.1017/S0022215110002124. PMID: 21054907
Kiefer J, Pok M, Adunka O, Stürzebecher E, Baumgartner W, Schmidt M, Tillein J, Ye Q, Gstoettner W
Audiol Neurootol 2005 May-Jun;10(3):134-44. Epub 2005 Feb 17 doi: 10.1159/000084023. PMID: 15724084
Zadeh MH, Storper IS, Spitzer JB
Otolaryngol Head Neck Surg 2003 Jan;128(1):92-8. doi: 10.1067/mhn.2003.50. PMID: 12574765
Bitner-Glindzicz M
Br Med Bull 2002;63:73-94. doi: 10.1093/bmb/63.1.73. PMID: 12324385

Prognosis

Govender SM, Mars M
S Afr J Commun Disord 2018 Jul 5;65(1):e1-e9. doi: 10.4102/sajcd.v65i1.582. PMID: 30035608Free PMC Article
Yamamoto N, Mutai H, Namba K, Morita N, Masuda S, Nishi Y, Nakano A, Masuda S, Fujioka M, Kaga K, Ogawa K, Matsunaga T
Orphanet J Rare Dis 2017 Sep 25;12(1):157. doi: 10.1186/s13023-017-0708-z. PMID: 28946916Free PMC Article
Street VA, Li J, Robbins CA, Kallman JC
J Biol Chem 2011 Apr 29;286(17):15278-86. Epub 2011 Mar 4 doi: 10.1074/jbc.M111.228304. PMID: 21378158Free PMC Article
Zadeh MH, Storper IS, Spitzer JB
Otolaryngol Head Neck Surg 2003 Jan;128(1):92-8. doi: 10.1067/mhn.2003.50. PMID: 12574765
Bitner-Glindzicz M
Br Med Bull 2002;63:73-94. doi: 10.1093/bmb/63.1.73. PMID: 12324385

Clinical prediction guides

Yasukawa R, Moteki H, Nishio SY, Ishikawa K, Abe S, Honkura Y, Hyogo M, Mihashi R, Ikezono T, Shintani T, Ogasawara N, Shirai K, Yoshihashi H, Ishino T, Otsuki K, Ito T, Sugahara K, Usami SI
Genes (Basel) 2019 Sep 24;10(10) doi: 10.3390/genes10100744. PMID: 31554319Free PMC Article
Govender SM, Mars M
S Afr J Commun Disord 2018 Jul 5;65(1):e1-e9. doi: 10.4102/sajcd.v65i1.582. PMID: 30035608Free PMC Article
Yamamoto N, Mutai H, Namba K, Morita N, Masuda S, Nishi Y, Nakano A, Masuda S, Fujioka M, Kaga K, Ogawa K, Matsunaga T
Orphanet J Rare Dis 2017 Sep 25;12(1):157. doi: 10.1186/s13023-017-0708-z. PMID: 28946916Free PMC Article
Kiefer J, Pok M, Adunka O, Stürzebecher E, Baumgartner W, Schmidt M, Tillein J, Ye Q, Gstoettner W
Audiol Neurootol 2005 May-Jun;10(3):134-44. Epub 2005 Feb 17 doi: 10.1159/000084023. PMID: 15724084
Scott AM, Bauch CD, Olsen WO
Am J Audiol 1999 Dec;8(2):101-5. doi: 10.1044/1059-0889(1999/020). PMID: 10646193

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