U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Fusiform descending thoracic aortic aneurysm

MedGen UID:
868359
Concept ID:
C4022753
Anatomical Abnormality
Synonym: Dilatation of the fusiform descending thoracic aorta
 
HPO: HP:0012728

Definition

A concentric abnormal localized widening (dilatation) of the descending thoracic aorta that involves the full circumference of the vessel wall [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVFusiform descending thoracic aortic aneurysm

Professional guidelines

PubMed

Dake MD, Fischbein MP, Bavaria JE, Desai ND, Oderich G, Singh MJ, Fillinger M, Suckow BD, Matsumura JS, Patel HJ
J Vasc Surg 2021 Nov;74(5):1483-1490.e2. Epub 2021 Apr 30 doi: 10.1016/j.jvs.2021.04.025. PMID: 33940079

Recent clinical studies

Etiology

Szeto WY, Vallabhajosyula P, Matsuda H, Moainie SL, Sharafuddin MJ, Corvera J, Smolock CJ, Miyamoto S, Naslund T, Ramaiah V; RelayPro-A Investigators
J Thorac Cardiovasc Surg 2022 May;163(5):1739-1750.e4. Epub 2022 Feb 1 doi: 10.1016/j.jtcvs.2021.10.071. PMID: 35241276
Dake MD, Fischbein MP, Bavaria JE, Desai ND, Oderich G, Singh MJ, Fillinger M, Suckow BD, Matsumura JS, Patel HJ
J Vasc Surg 2021 Nov;74(5):1483-1490.e2. Epub 2021 Apr 30 doi: 10.1016/j.jvs.2021.04.025. PMID: 33940079
Ranney DN, Cox ML, Yerokun BA, Benrashid E, McCann RL, Hughes GC
J Vasc Surg 2018 Feb;67(2):363-368. Epub 2017 Aug 26 doi: 10.1016/j.jvs.2017.06.094. PMID: 28847657Free PMC Article
van Bogerijen GH, Tolenaar JL, Rampoldi V, Moll FL, van Herwaarden JA, Jonker FH, Eagle KA, Trimarchi S
J Vasc Surg 2014 Apr;59(4):1134-43. doi: 10.1016/j.jvs.2014.01.042. PMID: 24661897
Taylor BV, Kalman PG
Ann Vasc Surg 1999 Nov;13(6):555-9. doi: 10.1007/s100169900297. PMID: 10541605

Diagnosis

DeCarlo C, Latz CA, Boitano LT, Kim Y, Tanious A, Schwartz SI, Patell R, Mohebali J, Dua A
Circulation 2021 Oct 5;144(14):1091-1101. Epub 2021 Aug 11 doi: 10.1161/CIRCULATIONAHA.121.054710. PMID: 34376058
Dake MD, Fischbein MP, Bavaria JE, Desai ND, Oderich G, Singh MJ, Fillinger M, Suckow BD, Matsumura JS, Patel HJ
J Vasc Surg 2021 Nov;74(5):1483-1490.e2. Epub 2021 Apr 30 doi: 10.1016/j.jvs.2021.04.025. PMID: 33940079
Lee CJ, Rodriguez HE, Kibbe MR, Malaisrie SC, Eskandari MK
J Vasc Surg 2013 May;57(5):1269-74. Epub 2013 Jan 24 doi: 10.1016/j.jvs.2012.10.124. PMID: 23352360
Alsac JM, Khantalin I, Julia P, Achouh P, Farahmand P, Capdevila C, Isselmou KO, Fabiani JN
Ann Vasc Surg 2011 Apr;25(3):345-51. Epub 2010 Oct 6 doi: 10.1016/j.avsg.2010.08.002. PMID: 20926236
Taylor BV, Kalman PG
Ann Vasc Surg 1999 Nov;13(6):555-9. doi: 10.1007/s100169900297. PMID: 10541605

Therapy

Szeto WY, Vallabhajosyula P, Matsuda H, Moainie SL, Sharafuddin MJ, Corvera J, Smolock CJ, Miyamoto S, Naslund T, Ramaiah V; RelayPro-A Investigators
J Thorac Cardiovasc Surg 2022 May;163(5):1739-1750.e4. Epub 2022 Feb 1 doi: 10.1016/j.jtcvs.2021.10.071. PMID: 35241276
Dake MD, Fischbein MP, Bavaria JE, Desai ND, Oderich G, Singh MJ, Fillinger M, Suckow BD, Matsumura JS, Patel HJ
J Vasc Surg 2021 Nov;74(5):1483-1490.e2. Epub 2021 Apr 30 doi: 10.1016/j.jvs.2021.04.025. PMID: 33940079
Ranney DN, Cox ML, Yerokun BA, Benrashid E, McCann RL, Hughes GC
J Vasc Surg 2018 Feb;67(2):363-368. Epub 2017 Aug 26 doi: 10.1016/j.jvs.2017.06.094. PMID: 28847657Free PMC Article
White RA, Donayre CE, Walot I, Lippmann M, Woody J, Lee J, Kim N, Kopchok GE, Fogarty TJ
J Vasc Surg 2001 May;33(5):927-34. doi: 10.1067/mva.2001.114998. PMID: 11331830
Westaby S, Katsumata T, Vaccari G
Eur J Cardiothorac Surg 1999 Feb;15(2):180-5. doi: 10.1016/s1010-7940(98)00310-8. PMID: 10219551

Prognosis

Ranney DN, Cox ML, Yerokun BA, Benrashid E, McCann RL, Hughes GC
J Vasc Surg 2018 Feb;67(2):363-368. Epub 2017 Aug 26 doi: 10.1016/j.jvs.2017.06.094. PMID: 28847657Free PMC Article
van Bogerijen GH, Tolenaar JL, Rampoldi V, Moll FL, van Herwaarden JA, Jonker FH, Eagle KA, Trimarchi S
J Vasc Surg 2014 Apr;59(4):1134-43. doi: 10.1016/j.jvs.2014.01.042. PMID: 24661897
Patel HJ, Shillingford MS, Williams DM, Upchurch GR Jr, Dasika NL, Prager RL, Deeb GM
Ann Thorac Surg 2007 May;83(5):1628-33; discussion 1633-4. doi: 10.1016/j.athoracsur.2006.12.070. PMID: 17462370
White RA, Donayre CE, Walot I, Lippmann M, Woody J, Lee J, Kim N, Kopchok GE, Fogarty TJ
J Vasc Surg 2001 May;33(5):927-34. doi: 10.1067/mva.2001.114998. PMID: 11331830
Westaby S, Katsumata T, Vaccari G
Eur J Cardiothorac Surg 1999 Feb;15(2):180-5. doi: 10.1016/s1010-7940(98)00310-8. PMID: 10219551

Clinical prediction guides

DeCarlo C, Latz CA, Boitano LT, Kim Y, Tanious A, Schwartz SI, Patell R, Mohebali J, Dua A
Circulation 2021 Oct 5;144(14):1091-1101. Epub 2021 Aug 11 doi: 10.1161/CIRCULATIONAHA.121.054710. PMID: 34376058
Patel HJ, Williams DM, Drews JD, Dasika NL, Eliason JL, Passow MC, Deeb GM
Ann Surg 2014 Oct;260(4):691-6; discussion 696-7. doi: 10.1097/SLA.0000000000000930. PMID: 25203886
van Bogerijen GH, Tolenaar JL, Rampoldi V, Moll FL, van Herwaarden JA, Jonker FH, Eagle KA, Trimarchi S
J Vasc Surg 2014 Apr;59(4):1134-43. doi: 10.1016/j.jvs.2014.01.042. PMID: 24661897
Shang EK, Nathan DP, Sprinkle SR, Fairman RM, Bavaria JE, Gorman RC, Gorman JH 3rd, Jackson BM
Circulation 2013 Sep 10;128(11 Suppl 1):S157-62. doi: 10.1161/CIRCULATIONAHA.112.000200. PMID: 24030401
Patel HJ, Shillingford MS, Williams DM, Upchurch GR Jr, Dasika NL, Prager RL, Deeb GM
Ann Thorac Surg 2007 May;83(5):1628-33; discussion 1633-4. doi: 10.1016/j.athoracsur.2006.12.070. PMID: 17462370

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...