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Atrial reentry tachycardia

MedGen UID:
868813
Concept ID:
C4023223
Pathologic Function
HPO: HP:0011699

Term Hierarchy

Conditions with this feature

Heterotaxy, visceral, 5, autosomal
MedGen UID:
501198
Concept ID:
C3495537
Congenital Abnormality
Heterotaxy ('heter' meaning 'other' and 'taxy' meaning 'arrangement'), or situs ambiguus, is a developmental condition characterized by randomization of the placement of visceral organs, including the heart, lungs, liver, spleen, and stomach. The organs are oriented randomly with respect to the left-right axis and with respect to one another (Srivastava, 1997). Heterotaxy is a clinically and genetically heterogeneous disorder. For a discussion of genetic heterogeneity of visceral heterotaxy, see HTX1 (306955).

Professional guidelines

PubMed

Ray L, Geier C, DeWitt KM
Am J Health Syst Pharm 2023 Aug 4;80(16):1039-1055. doi: 10.1093/ajhp/zxad108. PMID: 37227130
Page RL, Joglar JA, Caldwell MA, Calkins H, Conti JB, Deal BJ, Estes NA 3rd, Field ME, Goldberger ZD, Hammill SC, Indik JH, Lindsay BD, Olshansky B, Russo AM, Shen WK, Tracy CM, Al-Khatib SM; Evidence Review Committee Chair‡
Circulation 2016 Apr 5;133(14):e506-74. Epub 2015 Sep 23 doi: 10.1161/CIR.0000000000000311. PMID: 26399663
Page RL, Joglar JA, Caldwell MA, Calkins H, Conti JB, Deal BJ, Estes NA 3rd, Field ME, Goldberger ZD, Hammill SC, Indik JH, Lindsay BD, Olshansky B, Russo AM, Shen WK, Tracy CM, Al-Khatib SM; Evidence Review Committee Chair‡
Circulation 2016 Apr 5;133(14):e471-505. Epub 2015 Sep 23 doi: 10.1161/CIR.0000000000000310. PMID: 26399662

Recent clinical studies

Etiology

Ozturk E, Sisko SG, Sahin GT, Tanıdır IC, Guzeltas A, Haydin S, Hatemi AC, Ergul Y
Cardiol Young 2023 Dec;33(12):2498-2503. Epub 2023 Mar 21 doi: 10.1017/S1047951123000513. PMID: 36942512
Egbe AC, Connolly HM, Khan AR, Niaz T, Said SS, Dearani JA, Warnes CA, Deshmukh AJ, Kapa S, McLeod CJ
Am Heart J 2017 Apr;186:12-20. Epub 2017 Jan 2 doi: 10.1016/j.ahj.2016.12.015. PMID: 28454826
LaPage MJ, Rhee EK, Canter CE
J Heart Lung Transplant 2010 Mar;29(3):273-7. Epub 2009 Sep 26 doi: 10.1016/j.healun.2009.07.003. PMID: 19783173
Mavroudis C, Deal BJ, Backer CL
Int J Cardiol 2004 Dec;97 Suppl 1:39-51. doi: 10.1016/j.ijcard.2004.08.008. PMID: 15590078
Hebe J
Thorac Cardiovasc Surg 2000 Aug;48(4):214-9. doi: 10.1055/s-2000-6897. PMID: 11005595

Diagnosis

Ozturk E, Sisko SG, Sahin GT, Tanıdır IC, Guzeltas A, Haydin S, Hatemi AC, Ergul Y
Cardiol Young 2023 Dec;33(12):2498-2503. Epub 2023 Mar 21 doi: 10.1017/S1047951123000513. PMID: 36942512
Bernier M, Marelli AJ, Pilote L, Bouchardy J, Bottega N, Martucci G, Therrien J
Am J Cardiol 2010 Aug 15;106(4):547-51. doi: 10.1016/j.amjcard.2010.03.068. PMID: 20691314
Horlitz M, Schley P, Shin DI, Ghouzi A, Sause A, Wehner M, Müller M, Klein RM, Bufe A, Gülker H
Z Kardiol 2004 Jun;93(6):463-73. doi: 10.1007/s00392-004-0087-z. PMID: 15252740
Hebe J
Thorac Cardiovasc Surg 2000 Aug;48(4):214-9. doi: 10.1055/s-2000-6897. PMID: 11005595
Kanter RJ, Papagiannis J, Carboni MP, Ungerleider RM, Sanders WE, Wharton JM
J Am Coll Cardiol 2000 Feb;35(2):428-41. doi: 10.1016/s0735-1097(99)00557-4. PMID: 10676691

Therapy

Kueffer T, Seiler J, Madaffari A, Mühl A, Asatryan B, Stettler R, Haeberlin A, Noti F, Servatius H, Tanner H, Baldinger SH, Reichlin T, Roten L
J Interv Card Electrophysiol 2023 Sep;66(6):1431-1440. Epub 2022 Dec 11 doi: 10.1007/s10840-022-01436-1. PMID: 36496543Free PMC Article
Myrda K, Buchta P, Ciszewski G, Gąsior M
Kardiol Pol 2020 Oct 23;78(10):1047-1048. Epub 2020 Jul 8 doi: 10.33963/KP.15500. PMID: 32640774
Egbe AC, Connolly HM, Khan AR, Niaz T, Said SS, Dearani JA, Warnes CA, Deshmukh AJ, Kapa S, McLeod CJ
Am Heart J 2017 Apr;186:12-20. Epub 2017 Jan 2 doi: 10.1016/j.ahj.2016.12.015. PMID: 28454826
LaPage MJ, Rhee EK, Canter CE
J Heart Lung Transplant 2010 Mar;29(3):273-7. Epub 2009 Sep 26 doi: 10.1016/j.healun.2009.07.003. PMID: 19783173
Deal BJ, Mavroudis C, Backer CL
Pacing Clin Electrophysiol 2008 Feb;31 Suppl 1:S13-6. doi: 10.1111/j.1540-8159.2008.00947.x. PMID: 18226026

Prognosis

Egbe AC, Connolly HM, Khan AR, Niaz T, Said SS, Dearani JA, Warnes CA, Deshmukh AJ, Kapa S, McLeod CJ
Am Heart J 2017 Apr;186:12-20. Epub 2017 Jan 2 doi: 10.1016/j.ahj.2016.12.015. PMID: 28454826
LaPage MJ, Rhee EK, Canter CE
J Heart Lung Transplant 2010 Mar;29(3):273-7. Epub 2009 Sep 26 doi: 10.1016/j.healun.2009.07.003. PMID: 19783173
Horlitz M, Schley P, Shin DI, Ghouzi A, Sause A, Wehner M, Müller M, Klein RM, Bufe A, Gülker H
Z Kardiol 2004 Jun;93(6):463-73. doi: 10.1007/s00392-004-0087-z. PMID: 15252740
Weinstein S, Cua C, Chan D, Davis JT
J Thorac Cardiovasc Surg 2003 Aug;126(2):529-36. doi: 10.1016/s0022-5223(03)00212-5. PMID: 12928654
Hebe J
Thorac Cardiovasc Surg 2000 Aug;48(4):214-9. doi: 10.1055/s-2000-6897. PMID: 11005595

Clinical prediction guides

Ozturk E, Sisko SG, Sahin GT, Tanıdır IC, Guzeltas A, Haydin S, Hatemi AC, Ergul Y
Cardiol Young 2023 Dec;33(12):2498-2503. Epub 2023 Mar 21 doi: 10.1017/S1047951123000513. PMID: 36942512
Kueffer T, Seiler J, Madaffari A, Mühl A, Asatryan B, Stettler R, Haeberlin A, Noti F, Servatius H, Tanner H, Baldinger SH, Reichlin T, Roten L
J Interv Card Electrophysiol 2023 Sep;66(6):1431-1440. Epub 2022 Dec 11 doi: 10.1007/s10840-022-01436-1. PMID: 36496543Free PMC Article
Horlitz M, Schley P, Shin DI, Ghouzi A, Sause A, Wehner M, Müller M, Klein RM, Bufe A, Gülker H
Z Kardiol 2004 Jun;93(6):463-73. doi: 10.1007/s00392-004-0087-z. PMID: 15252740
Pecht B, Maginot KR, Boramanand NK, Perry JC
J Interv Card Electrophysiol 2002 Aug;7(1):83-8. doi: 10.1023/a:1020828401929. PMID: 12391424

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