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Right aortic arch with left descending aorta and left ductus arteriosus

MedGen UID:
868865
•Concept ID:
C4023276
•
Anatomical Abnormality
HPO: HP:0011597

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRight aortic arch with left descending aorta and left ductus arteriosus

Professional guidelines

PubMed

Prenatal Diagnosis of Vascular Ring: Evaluation of Fetal Diagnosis and Postnatal Outcomes.
Aly S, Papneja K, Mawad W, Seed M, Jaeggi E, Yoo SJ
J Am Soc Echocardiogr 2022 Mar;35(3):312-321. Epub 2021 Sep 29 doi: 10.1016/j.echo.2021.09.010. PMID: 34600045
The Differential Diagnosis of Double Aortic Arch and Right Aortic Arch with Mirror-Image Branches in the Fetus: A Potential Novel Method.
Han J, Zhang Y, Gu X, Liu X, Sun L, Zhao Y, Wang J, He Y
Pediatr Cardiol 2021 Aug;42(6):1405-1409. Epub 2021 Jul 13 doi: 10.1007/s00246-021-02625-x. PMID: 34258648
Prenatal ultrasonic diagnosis and differential diagnosis of isolated right aortic arch with mirror-image branching.
Gao J, Zhu J, Pei Q, Li J
Arch Gynecol Obstet 2017 May;295(5):1291-1295. Epub 2017 Mar 27 doi: 10.1007/s00404-017-4310-3. PMID: 28345111

Recent clinical studies

Etiology

The multiform sonographic spectrum of arterial duct in right aortic arch.
Chiappa E, Ridolfi C, Cordisco A
Int J Cardiovasc Imaging 2021 Dec;37(12):3385-3395. Epub 2021 Jul 8 doi: 10.1007/s10554-021-02325-w. PMID: 34236571Free PMC Article
Ductus arteriosus location in relation to aortic arch position, branching pattern, and viscero-atrial situs.
Sobh DM, Batouty NM, Abdelwahab RM, El-Badrawy A, Tawfik AM
Clin Radiol 2019 Sep;74(9):732.e1-732.e8. Epub 2019 Jun 12 doi: 10.1016/j.crad.2019.05.007. PMID: 31200931
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Prenatal echocardiographic assessment of right aortic arch.
Campanale CM, Pasquini L, Santangelo TP, Iorio FS, Bagolan P, Sanders SP, Toscano A
Ultrasound Obstet Gynecol 2019 Jul;54(1):96-102. Epub 2019 Jun 10 doi: 10.1002/uog.20098. PMID: 30125417
Borderline left ventricle.
Corno AF
Eur J Cardiothorac Surg 2005 Jan;27(1):67-73. doi: 10.1016/j.ejcts.2004.10.034. PMID: 15621473

Diagnosis

Prenatal Diagnosis of Vascular Ring: Evaluation of Fetal Diagnosis and Postnatal Outcomes.
Aly S, Papneja K, Mawad W, Seed M, Jaeggi E, Yoo SJ
J Am Soc Echocardiogr 2022 Mar;35(3):312-321. Epub 2021 Sep 29 doi: 10.1016/j.echo.2021.09.010. PMID: 34600045
Prenatal diagnosis of right aortic arch and aberrant left subclavian artery in association with bilateral ductus arteriosus by two-and four-dimensional echocardiography: a case of rare vascular ring and review of literature.
Sun X, Zhang Y, Wang Y
J Matern Fetal Neonatal Med 2022 Jul;35(14):2678-2683. Epub 2020 Jul 21 doi: 10.1080/14767058.2020.1795825. PMID: 32693651
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Prenatal echocardiographic assessment of right aortic arch.
Campanale CM, Pasquini L, Santangelo TP, Iorio FS, Bagolan P, Sanders SP, Toscano A
Ultrasound Obstet Gynecol 2019 Jul;54(1):96-102. Epub 2019 Jun 10 doi: 10.1002/uog.20098. PMID: 30125417
Right ductus arteriosus: facts and theory.
Bronshtein M, Zimmer EZ, Blazer S, Blumenfeld Z
Eur J Obstet Gynecol Reprod Biol 2011 Dec;159(2):282-8. Epub 2011 Sep 16 doi: 10.1016/j.ejogrb.2011.07.047. PMID: 21925785

Therapy

Pseudoaneurysm of Patent Ductus Arteriosus Following Previous PDA Closure: Case Report and Literature Review.
Mikael A, Andacheh I, Yufa A, Nurick H
Vasc Endovascular Surg 2020 Feb;54(2):165-168. Epub 2019 Nov 10 doi: 10.1177/1538574419886191. PMID: 31707973
Hypoplastic left heart syndrome: a novel surgical strategy for small-volume centres?
Pontailler M, Gaudin R, Lenoir M, Haydar A, Kraiche D, Bonnet D, Vouhé P, Raisky O
Eur J Cardiothorac Surg 2017 May 1;51(5):1003-1008. doi: 10.1093/ejcts/ezx021. PMID: 28329111
Transcatheter closure of patent ductus arteriosus using the AMPLATZER™ duct occluder II (ADO II).
Gruenstein DH, Ebeid M, Radtke W, Moore P, Holzer R, Justino H
Catheter Cardiovasc Interv 2017 May;89(6):1118-1128. Epub 2017 Mar 4 doi: 10.1002/ccd.26968. PMID: 28258658
Anomalous left brachiocephalic vein: important vascular anomaly concomitant with congenital anomalies and heart diseases.
Kahkouee S, Sadr M, Pedarzadeh E, Fardin S, Borhani A, Gholami S, Amjad G
Folia Morphol (Warsz) 2017;76(1):51-57. Epub 2016 Nov 10 doi: 10.5603/FM.a2016.0031. PMID: 27830886
Scoliosis in patients with aortic coarctation and patent ductus arteriosus: does standard posterolateral thoracotomy play a role in the development of the lateral curve of the spine?
Roclawski M, Sabiniewicz R, Potaz P, Smoczynski A, Pankowski R, Mazurek T, Daibo B
Pediatr Cardiol 2009 Oct;30(7):941-5. Epub 2009 Jul 14 doi: 10.1007/s00246-009-9469-3. PMID: 19597861

Prognosis

Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes.
Dizdaroğulları GE, Alpınar A, Demirci O
J Perinat Med 2024 Mar 25;52(3):304-309. Epub 2024 Jan 29 doi: 10.1515/jpm-2023-0410. PMID: 38281095
The multiform sonographic spectrum of arterial duct in right aortic arch.
Chiappa E, Ridolfi C, Cordisco A
Int J Cardiovasc Imaging 2021 Dec;37(12):3385-3395. Epub 2021 Jul 8 doi: 10.1007/s10554-021-02325-w. PMID: 34236571Free PMC Article
Pseudoaneurysm of Patent Ductus Arteriosus Following Previous PDA Closure: Case Report and Literature Review.
Mikael A, Andacheh I, Yufa A, Nurick H
Vasc Endovascular Surg 2020 Feb;54(2):165-168. Epub 2019 Nov 10 doi: 10.1177/1538574419886191. PMID: 31707973
Echocardiographic and pathomorphological features in fetuses with ductal-dependent congenital heart diseases.
Jiang H, Tang Q, Jiang Y, Li N, Tang X, Xia H
Echocardiography 2019 Sep;36(9):1736-1743. Epub 2019 Aug 7 doi: 10.1111/echo.14452. PMID: 31389092
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879

Clinical prediction guides

The multiform sonographic spectrum of arterial duct in right aortic arch.
Chiappa E, Ridolfi C, Cordisco A
Int J Cardiovasc Imaging 2021 Dec;37(12):3385-3395. Epub 2021 Jul 8 doi: 10.1007/s10554-021-02325-w. PMID: 34236571Free PMC Article
Outcomes of aortic coarctation surgical repair in adolescents and adults.
Cho S, Lee CH, Kim ER, Lim JH
Interact Cardiovasc Thorac Surg 2020 Jun 1;30(6):925-931. doi: 10.1093/icvts/ivaa039. PMID: 32221581
Ductus arteriosus location in relation to aortic arch position, branching pattern, and viscero-atrial situs.
Sobh DM, Batouty NM, Abdelwahab RM, El-Badrawy A, Tawfik AM
Clin Radiol 2019 Sep;74(9):732.e1-732.e8. Epub 2019 Jun 12 doi: 10.1016/j.crad.2019.05.007. PMID: 31200931
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Pathogenesis of solitary right aortic arch: a mass effect hypothesis based on observations of serial human embryonic sections.
Jin ZW, Yamada T, Kim JH, Rodríguez-Vázquez JF, Murakami G, Arakawa K
Cardiol Young 2017 Mar;27(2):359-368. Epub 2015 Oct 5 doi: 10.1017/S1047951115002152. PMID: 26435328

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