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Abnormal inner ear nerve morphology

MedGen UID:
868966
•Concept ID:
C4023380
•
Anatomical Abnormality
Synonym: Morphological abnormality of the nerves of the inner ear
 
HPO: HP:0011391

Professional guidelines

PubMed

Current Treatment of Endolymphatic Sac Tumor of the Temporal Bone.
Mendenhall WM, Suárez C, Skálová A, Strojan P, Triantafyllou A, Devaney KO, Williams MD, Rinaldo A, Ferlito A
Adv Ther 2018 Jul;35(7):887-898. Epub 2018 Jun 19 doi: 10.1007/s12325-018-0730-0. PMID: 29923043Free PMC Article
Early complications following cochlear implantation in children and their management.
Li S, Qin Z, Zhang F, Li L, Qi S, Liu L
Int J Pediatr Otorhinolaryngol 2014 Jul;78(7):1040-4. Epub 2014 Apr 12 doi: 10.1016/j.ijporl.2014.03.036. PMID: 24809767
Mandibulofacial dysostosis: CT evaluation of the temporal bones for surgical risk assessment in patients of bilateral aural atresia.
Takegoshi H, Kaga K, Kikuchi S, Ito K
Int J Pediatr Otorhinolaryngol 2000 Aug 11;54(1):33-40. doi: 10.1016/s0165-5876(00)00344-x. PMID: 10960694

Recent clinical studies

Etiology

Cochlear Implantation in Inner Ear Malformations: Considerations Related to Surgical Complications and Communication Skills.
Karamert R, Tutar H, Altinyay Ş, Düzlü M, Yildiz M, Akdulum İ, Uğur MB, Çolak M, Cebeci S, Şahin MM, Orçan E, Bayazit YA
ORL J Otorhinolaryngol Relat Spec 2022;84(3):211-218. Epub 2021 Sep 9 doi: 10.1159/000517562. PMID: 34500448
Classification and Current Management of Inner Ear Malformations.
Sennaroğlu L, Bajin MD
Balkan Med J 2017 Sep 29;34(5):397-411. Epub 2017 Aug 25 doi: 10.4274/balkanmedj.2017.0367. PMID: 28840850Free PMC Article
Cochlear Implantation in Inner Ear Malformations: Systematic Review of Speech Perception Outcomes and Intraoperative Findings.
Farhood Z, Nguyen SA, Miller SC, Holcomb MA, Meyer TA, Rizk HG
Otolaryngol Head Neck Surg 2017 May;156(5):783-793. Epub 2017 Apr 4 doi: 10.1177/0194599817696502. PMID: 28374626
Cochlear synaptopathy in acquired sensorineural hearing loss: Manifestations and mechanisms.
Liberman MC, Kujawa SG
Hear Res 2017 Jun;349:138-147. Epub 2017 Jan 10 doi: 10.1016/j.heares.2017.01.003. PMID: 28087419Free PMC Article
Stapedectomy in children.
House JW, Sheehy JL, Antunez JC
Laryngoscope 1980 Nov;90(11 Pt 1):1804-9. doi: 10.1288/00005537-198011000-00007. PMID: 7432061

Diagnosis

Imaging Guide to Inner Ear Malformations: An Illustrative Review.
Yu FF, Feltrin FS, Bathla G, Raj K, Agarwal A, Lee WC, Booth T, Singh A
Curr Probl Diagn Radiol 2023 Nov-Dec;52(6):576-585. Epub 2023 Jul 4 doi: 10.1067/j.cpradiol.2023.06.010. PMID: 37500297
Auditory neuropathy--neural and synaptic mechanisms.
Moser T, Starr A
Nat Rev Neurol 2016 Mar;12(3):135-49. Epub 2016 Feb 19 doi: 10.1038/nrneurol.2016.10. PMID: 26891769
Some Remarks on Imaging of the Inner Ear: Options and Limitations.
Giesemann A, Hofmann E
Clin Neuroradiol 2015 Oct;25 Suppl 2:197-203. Epub 2015 Jul 8 doi: 10.1007/s00062-015-0422-y. PMID: 26153464
Imaging of the temporal bone.
Abele TA, Wiggins RH 3rd
Radiol Clin North Am 2015 Jan;53(1):15-36. doi: 10.1016/j.rcl.2014.09.010. PMID: 25476172
Branchio-oculo-facial syndrome.
Raveh E, Papsin BC, Forte V
Int J Pediatr Otorhinolaryngol 2000 Jun 30;53(2):149-56. doi: 10.1016/s0165-5876(00)00310-4. PMID: 10906521

Therapy

Cochlear Implantation: Systematic Approach to Preoperative Radiologic Evaluation.
Hiremath SB, Biswas A, Mndebele G, Schramm D, Ertl-Wagner BB, Blaser SI, Chakraborty S
Radiographics 2023 Apr;43(4):e220102. doi: 10.1148/rg.220102. PMID: 36893052
Cochlear Implantation in Inner Ear Malformations: Considerations Related to Surgical Complications and Communication Skills.
Karamert R, Tutar H, Altinyay Ş, Düzlü M, Yildiz M, Akdulum İ, Uğur MB, Çolak M, Cebeci S, Şahin MM, Orçan E, Bayazit YA
ORL J Otorhinolaryngol Relat Spec 2022;84(3):211-218. Epub 2021 Sep 9 doi: 10.1159/000517562. PMID: 34500448
Cochlear Implantation in Inner Ear Malformations: Systematic Review of Speech Perception Outcomes and Intraoperative Findings.
Farhood Z, Nguyen SA, Miller SC, Holcomb MA, Meyer TA, Rizk HG
Otolaryngol Head Neck Surg 2017 May;156(5):783-793. Epub 2017 Apr 4 doi: 10.1177/0194599817696502. PMID: 28374626
Cochlear synaptopathy in acquired sensorineural hearing loss: Manifestations and mechanisms.
Liberman MC, Kujawa SG
Hear Res 2017 Jun;349:138-147. Epub 2017 Jan 10 doi: 10.1016/j.heares.2017.01.003. PMID: 28087419Free PMC Article
Management of surgical difficulties during cochlear implant with inner ear anomalies.
Aldhafeeri AM, Alsanosi AA
Int J Pediatr Otorhinolaryngol 2017 Jan;92:45-49. Epub 2016 Nov 3 doi: 10.1016/j.ijporl.2016.11.001. PMID: 28012532

Prognosis

Otopathologic Abnormalities in CHARGE Syndrome.
da Costa Monsanto R, Knoll RM, de Oliveira Penido N, Song G, Santos F, Paparella MM, Cureoglu S
Otolaryngol Head Neck Surg 2022 Feb;166(2):363-372. Epub 2021 Apr 20 doi: 10.1177/01945998211008911. PMID: 33874787
Congenital anomalies of the optic disc: insights from optical coherence tomography imaging.
Jeng-Miller KW, Cestari DM, Gaier ED
Curr Opin Ophthalmol 2017 Nov;28(6):579-586. doi: 10.1097/ICU.0000000000000425. PMID: 28817389
Cochlear Implantation in Inner Ear Malformations: Systematic Review of Speech Perception Outcomes and Intraoperative Findings.
Farhood Z, Nguyen SA, Miller SC, Holcomb MA, Meyer TA, Rizk HG
Otolaryngol Head Neck Surg 2017 May;156(5):783-793. Epub 2017 Apr 4 doi: 10.1177/0194599817696502. PMID: 28374626
Some Remarks on Imaging of the Inner Ear: Options and Limitations.
Giesemann A, Hofmann E
Clin Neuroradiol 2015 Oct;25 Suppl 2:197-203. Epub 2015 Jul 8 doi: 10.1007/s00062-015-0422-y. PMID: 26153464
Congenital malformation of the inner ear and pediatric cochlear implantation.
Mylanus EA, Rotteveel LJ, Leeuw RL
Otol Neurotol 2004 May;25(3):308-17. doi: 10.1097/00129492-200405000-00019. PMID: 15129111

Clinical prediction guides

Vestibular function in children with vestibulocochlear nerve aplasia/hypoplasia.
Karpeta N, Asp F, Edholm K, Bonnard Å, Wales J, Karltorp E, Duan M, Verrecchia L
Acta Otolaryngol 2023 Oct;143(10):861-866. Epub 2024 Jan 5 doi: 10.1080/00016489.2023.2285453. PMID: 38063358
The spectrum of cochlear malformations in CHARGE syndrome and insights into the role of the CHD7 gene during embryogenesis of the inner ear.
Lewis MA, Juliano A, Robson C, Clement E, Nash R, Rajput K, D'Arco F
Neuroradiology 2023 Apr;65(4):819-834. Epub 2023 Jan 30 doi: 10.1007/s00234-023-03118-9. PMID: 36715725
Symptoms and clinical features in patients affected by endolymphatic sac tumor: a systematic review and meta-analysis.
Gioacchini FM, Kaleci S, Chiarella G, Viola P, Pisani D, Scarpa A, Tulli M, Pace A, Iannella G, Re M
Eur Arch Otorhinolaryngol 2022 Nov;279(11):5081-5088. Epub 2022 Jun 15 doi: 10.1007/s00405-022-07469-6. PMID: 35704074
Classification and Current Management of Inner Ear Malformations.
Sennaroğlu L, Bajin MD
Balkan Med J 2017 Sep 29;34(5):397-411. Epub 2017 Aug 25 doi: 10.4274/balkanmedj.2017.0367. PMID: 28840850Free PMC Article
Clinical outcomes following cochlear implantation in children with inner ear anomalies.
Isaiah A, Lee D, Lenes-Voit F, Sweeney M, Kutz W, Isaacson B, Roland P, Lee KH
Int J Pediatr Otorhinolaryngol 2017 Feb;93:1-6. Epub 2016 Dec 5 doi: 10.1016/j.ijporl.2016.12.001. PMID: 28109477

Recent systematic reviews

Surgical Management of Endolymphatic Sac Tumor: A Systematic Review and Meta-Analysis.
Gioacchini FM, Chiarella G, Kaleci S, Iannella G, Viola P, Pisani D, Scarpa A, Tulli M, Re M
J Int Adv Otol 2023 Jun;19(3):248-254. doi: 10.5152/iao.2023.22957. PMID: 37272644Free PMC Article
Symptoms and clinical features in patients affected by endolymphatic sac tumor: a systematic review and meta-analysis.
Gioacchini FM, Kaleci S, Chiarella G, Viola P, Pisani D, Scarpa A, Tulli M, Pace A, Iannella G, Re M
Eur Arch Otorhinolaryngol 2022 Nov;279(11):5081-5088. Epub 2022 Jun 15 doi: 10.1007/s00405-022-07469-6. PMID: 35704074
Systematic review of cochlear implantation in CHARGE syndrome.
Amin N, Sethukumar P, Pai I, Rajput K, Nash R
Cochlear Implants Int 2019 Sep;20(5):266-280. Epub 2019 Jul 7 doi: 10.1080/14670100.2019.1634857. PMID: 31282293
Cochlear Implantation in Inner Ear Malformations: Systematic Review of Speech Perception Outcomes and Intraoperative Findings.
Farhood Z, Nguyen SA, Miller SC, Holcomb MA, Meyer TA, Rizk HG
Otolaryngol Head Neck Surg 2017 May;156(5):783-793. Epub 2017 Apr 4 doi: 10.1177/0194599817696502. PMID: 28374626
Auditory brainstem implant candidacy in the United States in children 0-17 years old.
Kaplan AB, Kozin ED, Puram SV, Owoc MS, Shah PV, Hight AE, Sethi RKV, Remenschneider AK, Lee DJ
Int J Pediatr Otorhinolaryngol 2015 Mar;79(3):310-315. Epub 2014 Dec 15 doi: 10.1016/j.ijporl.2014.11.023. PMID: 25577282Free PMC Article

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