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Generalized anhidrosis

MedGen UID:
870423
Concept ID:
C4024869
Finding
Synonyms: Generalised anhidrosis; Generalised anhydrosis; Generalised inability to sweat; Generalized anhydrosis; Generalized inability to sweat
 
HPO: HP:0007459

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVGeneralized anhidrosis

Conditions with this feature

Isolated anhidrosis with normal sweat glands
MedGen UID:
1800259
Concept ID:
C5568836
Disease or Syndrome
Isolated anhidrosis with normal sweat glands (ANHD) is characterized by absence of perspiration and subsequent heat intolerance with normal morphology and number of sweat glands. Teeth, hair, nails, and skin are normal (Klar et al., 2014).

Professional guidelines

PubMed

Chan MMH, Lim GH, Zhao X, Tey HL
Eur J Dermatol 2020 Dec 1;30(6):680-687. doi: 10.1684/ejd.2020.3931. PMID: 33262099
Munetsugu T, Fujimoto T, Oshima Y, Sano K, Murota H, Satoh T, Iwase S, Asahina M, Nakazato Y, Yokozeki H
J Dermatol 2017 Apr;44(4):394-400. Epub 2016 Oct 24 doi: 10.1111/1346-8138.13649. PMID: 27774633
Satoh T
Curr Probl Dermatol 2016;51:75-9. Epub 2016 Aug 30 doi: 10.1159/000446781. PMID: 27584965

Recent clinical studies

Etiology

Kashio M, Derouiche S, Yoshimoto RU, Sano K, Lei J, Kido MA, Tominaga M
Elife 2024 Jul 4;13 doi: 10.7554/eLife.92993. PMID: 38963781Free PMC Article
Shimoda-Komatsu Y, Yamazaki Y, Kimishima M, Mizukawa Y, Ohyama M
J Dermatol Sci 2022 Oct;108(1):12-21. Epub 2022 Oct 8 doi: 10.1016/j.jdermsci.2022.10.001. PMID: 36244887
Takahagi S, Okamoto M, Ishii K, Tanaka A, Mizuno H, Harada N, Yanagida N, Hide M
Allergol Int 2022 Jul;71(3):362-372. Epub 2022 Mar 7 doi: 10.1016/j.alit.2022.01.003. PMID: 35272957
Iida T, Nakamura M, Inazawa M, Munetsugu T, Nishida M, Fujimoto T, Sasaki Y, Ohshima Y, Nakazato Y, Namiki T, Yokozeki H
J Dermatol 2021 Mar;48(3):271-278. Epub 2020 Nov 4 doi: 10.1111/1346-8138.15666. PMID: 33146891Free PMC Article
Chan MMH, Lim GH, Zhao X, Tey HL
Eur J Dermatol 2020 Dec 1;30(6):680-687. doi: 10.1684/ejd.2020.3931. PMID: 33262099

Diagnosis

Kawahara K, Shimomura Y, Oshima Y, Watanabe T, Hori T, Okumura A, Iwayama H
Front Endocrinol (Lausanne) 2022;13:877715. Epub 2022 May 26 doi: 10.3389/fendo.2022.877715. PMID: 35721739Free PMC Article
Iida T, Nakamura M, Inazawa M, Munetsugu T, Nishida M, Fujimoto T, Sasaki Y, Ohshima Y, Nakazato Y, Namiki T, Yokozeki H
J Dermatol 2021 Mar;48(3):271-278. Epub 2020 Nov 4 doi: 10.1111/1346-8138.15666. PMID: 33146891Free PMC Article
Chan MMH, Lim GH, Zhao X, Tey HL
Eur J Dermatol 2020 Dec 1;30(6):680-687. doi: 10.1684/ejd.2020.3931. PMID: 33262099
Satoh T
Curr Probl Dermatol 2016;51:75-9. Epub 2016 Aug 30 doi: 10.1159/000446781. PMID: 27584965
Yilmazer S, Okuyucu E, Melek I, Duman T
Neurosciences (Riyadh) 2013 Apr;18(2):178-9. PMID: 23545621

Therapy

Imafuku K, Yanagi T, Yoshimoto N, Miyazawa H, Iwata H, Ujiie H
Australas J Dermatol 2024 Feb;65(1):55-58. Epub 2023 Oct 27 doi: 10.1111/ajd.14180. PMID: 37888886
Munetsugu T, Fujimoto T, Oshima Y, Sano K, Murota H, Satoh T, Iwase S, Asahina M, Nakazato Y, Yokozeki H
J Dermatol 2017 Apr;44(4):394-400. Epub 2016 Oct 24 doi: 10.1111/1346-8138.13649. PMID: 27774633
Satoh T
Curr Probl Dermatol 2016;51:75-9. Epub 2016 Aug 30 doi: 10.1159/000446781. PMID: 27584965
Fujita K, Hatta K
Dermatology 2013;227(3):270-7. Epub 2013 Oct 26 doi: 10.1159/000355332. PMID: 24191980
Yilmazer S, Okuyucu E, Melek I, Duman T
Neurosciences (Riyadh) 2013 Apr;18(2):178-9. PMID: 23545621

Prognosis

Imafuku K, Yanagi T, Yoshimoto N, Miyazawa H, Iwata H, Ujiie H
Australas J Dermatol 2024 Feb;65(1):55-58. Epub 2023 Oct 27 doi: 10.1111/ajd.14180. PMID: 37888886
Iida T, Nakamura M, Inazawa M, Munetsugu T, Nishida M, Fujimoto T, Sasaki Y, Ohshima Y, Nakazato Y, Namiki T, Yokozeki H
J Dermatol 2021 Mar;48(3):271-278. Epub 2020 Nov 4 doi: 10.1111/1346-8138.15666. PMID: 33146891Free PMC Article
Öktem EÖ, Çankaya Ş, Uykur AB, Erdem NS, Yulug B
Ideggyogy Sz 2020 Sep 30;73(9-10):349-353. doi: 10.18071/isz.73.0349. PMID: 33035413
Chung TS, Lee SH
J Dermatol 1999 Sep;26(9):615-8. doi: 10.1111/j.1346-8138.1999.tb02059.x. PMID: 10535259
Foster KG, Hey EN, O'Connell B
Arch Dis Child 1971 Aug;46(248):444-51. doi: 10.1136/adc.46.248.444. PMID: 4935620Free PMC Article

Clinical prediction guides

Sano K, Asahina M, Araki N, Uehara T, Iwaya M, Okuyama R
J Eur Acad Dermatol Venereol 2023 Oct;37(10):2124-2132. Epub 2023 Jul 4 doi: 10.1111/jdv.19284. PMID: 37338336
Yanagida N, Takahagi S, Aoyama Y, Tanaka A, Hide M
J Dermatol 2022 Jun;49(6):666-670. Epub 2022 Mar 22 doi: 10.1111/1346-8138.16365. PMID: 35315137
Sano K, Asahina M, Uehara T, Araki N, Yamanaka Y, Matsumoto K, Okuyama R
J Dermatol 2021 Apr;48(4):439-446. Epub 2021 Jan 16 doi: 10.1111/1346-8138.15722. PMID: 33454997
Munetsugu T, Fujimoto T, Satoh T, Nakazato Y, Ohshima Y, Asahina M, Yokozeki H
J Dermatol 2017 Jul;44(7):747-752. Epub 2017 Mar 22 doi: 10.1111/1346-8138.13785. PMID: 28328088
Murakami K, Sobue G, Terao S, Mitsuma T
J Neurol 1988 Sep;235(7):428-31. doi: 10.1007/BF00314488. PMID: 3065466

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