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Rare Neoplastic Syndrome

MedGen UID:
885398
•Concept ID:
C4054123
•
Disease or Syndrome
Synonym: Rare Tumor-Associated Syndrome

Definition

A broad classification for uncommon disorders in which the development of neoplasms occur in association with a characteristic set of signs or symptoms. These disorders commonly have a genetic basis. The types of neoplasms themselves are not necessarily uncommon. [from NCI]

Professional guidelines

PubMed

The management of desmoid tumours: A joint global consensus-based guideline approach for adult and paediatric patients.
Desmoid Tumor Working Group
Eur J Cancer 2020 Mar;127:96-107. Epub 2020 Jan 28 doi: 10.1016/j.ejca.2019.11.013. PMID: 32004793
Adverse effects of immune-checkpoint inhibitors: epidemiology, management and surveillance.
Martins F, Sofiya L, Sykiotis GP, Lamine F, Maillard M, Fraga M, Shabafrouz K, Ribi C, Cairoli A, Guex-Crosier Y, Kuntzer T, Michielin O, Peters S, Coukos G, Spertini F, Thompson JA, Obeid M
Nat Rev Clin Oncol 2019 Sep;16(9):563-580. doi: 10.1038/s41571-019-0218-0. PMID: 31092901
European evidence-based guidelines on pancreatic cystic neoplasms.
European Study Group on Cystic Tumours of the Pancreas
Gut 2018 May;67(5):789-804. Epub 2018 Mar 24 doi: 10.1136/gutjnl-2018-316027. PMID: 29574408Free PMC Article

Recent clinical studies

Diagnosis

Castleman disease of the hyaline vascular variant transforming to POEMS syndrome as endpoint: a case report.
Ge Y, Da Q, Dai Y
BMC Neurol 2018 Oct 9;18(1):169. doi: 10.1186/s12883-018-1172-7. PMID: 30301456Free PMC Article

Supplemental Content

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    • PMC Articles
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