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Pauci-Immune Glomerulonephritis - Renal Limited

MedGen UID:
886335
Concept ID:
C4053792
Disease or Syndrome

Definition

Glomerulonephritis in which anti-neutrophil cytoplasm antibody (ANCA) is almost always present and vasculitis is limited to the kidney. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPauci-Immune Glomerulonephritis - Renal Limited

Professional guidelines

PubMed

Hruskova Z, Tesar V
Blood Purif 2018;45(1-3):213-217. Epub 2018 Jan 26 doi: 10.1159/000485368. PMID: 29478046
Haubitz M
Vasa 2007 May;36(2):81-9. doi: 10.1024/0301-1526.36.2.81. PMID: 17708098
Savige J, Dimech W, Fritzler M, Goeken J, Hagen EC, Jennette JC, McEvoy R, Pusey C, Pollock W, Trevisin M, Wiik A, Wong R; International Group for Consensus Statement on Testing and Reporting of Antineutrophil Cytoplasmic Antibodies (ANCA)
Am J Clin Pathol 2003 Sep;120(3):312-8. doi: 10.1309/WAEP-ADW0-K4LP-UHFN. PMID: 14502794

Recent clinical studies

Etiology

Ronsin C, Georges M, Chapelet-Debout A, Augusto JF, Audard V, Lebourg L, Rubin S, Quemeneur T, Bataille P, Karras A, Daugas E, Titeca-Beauport D, Boffa JJ, Vigneau C, Halimi JM, Isnard-Bagnis C, Durault S, Renaudineau E, Bridoux F, Testa A, Le Quintrec M, Renaudin K, Fakhouri F
Am J Kidney Dis 2022 Jan;79(1):56-68.e1. Epub 2021 Jun 11 doi: 10.1053/j.ajkd.2021.03.027. PMID: 34119564
Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Scaglioni V, Scolnik M, Catoggio LJ, Christiansen SB, Varela CF, Greloni G, Rosa-Diez G, Soriano ER
Clin Exp Rheumatol 2017 Mar-Apr;35 Suppl 103(1):55-58. Epub 2017 Jan 31 PMID: 28229825
Sharma A, Nada R, Naidu GS, Minz RW, Kohli HS, Sakhuja V, Gupta KL, Rathi M
Int J Rheum Dis 2016 Jan;19(1):74-81. Epub 2015 Aug 13 doi: 10.1111/1756-185X.12729. PMID: 26269223
Hung PH, Chiu YL, Lin WC, Chiang WC, Chen YM, Lin SL, Wu KD, Tsai TJ
J Formos Med Assoc 2006 Oct;105(10):804-12. doi: 10.1016/S0929-6646(09)60267-9. PMID: 17000453

Diagnosis

Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Scaglioni V, Scolnik M, Catoggio LJ, Christiansen SB, Varela CF, Greloni G, Rosa-Diez G, Soriano ER
Clin Exp Rheumatol 2017 Mar-Apr;35 Suppl 103(1):55-58. Epub 2017 Jan 31 PMID: 28229825
Kambham N
Adv Anat Pathol 2012 Mar;19(2):111-24. doi: 10.1097/PAP.0b013e318248b7a1. PMID: 22313839
Rutgers A, Sanders JS, Stegeman CA, Kallenberg CG
Rheum Dis Clin North Am 2010 Aug;36(3):559-72. doi: 10.1016/j.rdc.2010.05.002. PMID: 20688250
Gupta RK
Indian J Pathol Microbiol 2003 Jul;46(3):357-66. PMID: 15025274

Therapy

Ronsin C, Georges M, Chapelet-Debout A, Augusto JF, Audard V, Lebourg L, Rubin S, Quemeneur T, Bataille P, Karras A, Daugas E, Titeca-Beauport D, Boffa JJ, Vigneau C, Halimi JM, Isnard-Bagnis C, Durault S, Renaudineau E, Bridoux F, Testa A, Le Quintrec M, Renaudin K, Fakhouri F
Am J Kidney Dis 2022 Jan;79(1):56-68.e1. Epub 2021 Jun 11 doi: 10.1053/j.ajkd.2021.03.027. PMID: 34119564
Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Sharma A, Nada R, Naidu GS, Minz RW, Kohli HS, Sakhuja V, Gupta KL, Rathi M
Int J Rheum Dis 2016 Jan;19(1):74-81. Epub 2015 Aug 13 doi: 10.1111/1756-185X.12729. PMID: 26269223
Chan PT, Mok CC
Clin Rheumatol 2012 Aug;31(8):1273-7. Epub 2012 May 30 doi: 10.1007/s10067-012-2010-8. PMID: 22644090
Rutgers A, Sanders JS, Stegeman CA, Kallenberg CG
Rheum Dis Clin North Am 2010 Aug;36(3):559-72. doi: 10.1016/j.rdc.2010.05.002. PMID: 20688250

Prognosis

Prasad N, Khurana M, Kushwaha R, Patel M, Bhaduaria D, Kaul A, Behera M, Yaccha M, Jain M, Agrawal V
Int Urol Nephrol 2023 Jul;55(7):1847-1855. Epub 2023 Feb 14 doi: 10.1007/s11255-023-03465-9. PMID: 36781681
Sharma A, Nada R, Naidu GS, Minz RW, Kohli HS, Sakhuja V, Gupta KL, Rathi M
Int J Rheum Dis 2016 Jan;19(1):74-81. Epub 2015 Aug 13 doi: 10.1111/1756-185X.12729. PMID: 26269223
Rutgers A, Sanders JS, Stegeman CA, Kallenberg CG
Rheum Dis Clin North Am 2010 Aug;36(3):559-72. doi: 10.1016/j.rdc.2010.05.002. PMID: 20688250
Hung PH, Chiu YL, Lin WC, Chiang WC, Chen YM, Lin SL, Wu KD, Tsai TJ
J Formos Med Assoc 2006 Oct;105(10):804-12. doi: 10.1016/S0929-6646(09)60267-9. PMID: 17000453
Gupta RK
Indian J Pathol Microbiol 2003 Jul;46(3):357-66. PMID: 15025274

Clinical prediction guides

Ronsin C, Georges M, Chapelet-Debout A, Augusto JF, Audard V, Lebourg L, Rubin S, Quemeneur T, Bataille P, Karras A, Daugas E, Titeca-Beauport D, Boffa JJ, Vigneau C, Halimi JM, Isnard-Bagnis C, Durault S, Renaudineau E, Bridoux F, Testa A, Le Quintrec M, Renaudin K, Fakhouri F
Am J Kidney Dis 2022 Jan;79(1):56-68.e1. Epub 2021 Jun 11 doi: 10.1053/j.ajkd.2021.03.027. PMID: 34119564
Sharma A, Nada R, Naidu GS, Minz RW, Kohli HS, Sakhuja V, Gupta KL, Rathi M
Int J Rheum Dis 2016 Jan;19(1):74-81. Epub 2015 Aug 13 doi: 10.1111/1756-185X.12729. PMID: 26269223
Day CJ, Howie AJ, Nightingale P, Shabir S, Adu D, Savage CO, Hewins P
Am J Kidney Dis 2010 Feb;55(2):250-8. Epub 2009 Dec 31 doi: 10.1053/j.ajkd.2009.10.047. PMID: 20045237Free PMC Article
Chen M, Kallenberg CG
Clin Exp Rheumatol 2009 Jan-Feb;27(1 Suppl 52):S108-14. PMID: 19646356
Teplitsky V, Shoenfeld Y, Tanay A
Lupus 2006;15(6):319-25. doi: 10.1191/0961203306lu2306rr. PMID: 16830877

Recent systematic reviews

Floyd L, Morris AD, Elsayed ME, Shetty A, Baksi A, Geetha D, Dhaygude A, Mitra S
Kidney360 2023 Jan 1;4(1):69-77. Epub 2022 Nov 24 doi: 10.34067/KID.0003892022. PMID: 36700906Free PMC Article
Chan PT, Mok CC
Clin Rheumatol 2012 Aug;31(8):1273-7. Epub 2012 May 30 doi: 10.1007/s10067-012-2010-8. PMID: 22644090

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