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Idiopathic retroperitoneal fibrosis

MedGen UID:
887340
Concept ID:
C4048297
Disease or Syndrome
Synonym: Idiopathic Retroperitoneal Fibrosis
SNOMED CT: Idiopathic retroperitoneal fibrosis (197808006)

Definition

A condition characterized by abnormal proliferation of fibrous tissue in the compartment posterior to the peritoneum, for which no underlying cause has been identified. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIdiopathic retroperitoneal fibrosis

Professional guidelines

PubMed

Adam Z, Čermák A, Adamová Z, Řehák Z, Koukalová R, Pour L
Rozhl Chir 2022 Summer;101(6):265-272. doi: 10.33699/PIS.2022.101.6.265-271. PMID: 35973821
Tanaka T, Masumori N
Int J Urol 2020 May;27(5):387-394. Epub 2020 Mar 12 doi: 10.1111/iju.14218. PMID: 32166828
Swartz RD
Am J Kidney Dis 2009 Sep;54(3):546-53. Epub 2009 Jun 10 doi: 10.1053/j.ajkd.2009.04.019. PMID: 19515472

Recent clinical studies

Etiology

Grasso C, Giacchero F, Crivellari S, Bertolotti M, Maconi A
Curr Environ Health Rep 2023 Sep;10(3):303-311. Epub 2023 Jun 14 doi: 10.1007/s40572-023-00401-y. PMID: 37314670
Giannese D, Moriconi D, Cupisti A, Zucchi A, Pastore AL, Simonato A, Mogorovich A, Claps F, Bartoletti R
Urol Int 2023;107(2):134-147. Epub 2022 Oct 21 doi: 10.1159/000526114. PMID: 36273441
Angarola E, Valeo Chulvi M, Peuchot V, García Rivello H, Jauk F
Medicina (B Aires) 2022;82(1):91-98. PMID: 35037866
Raglianti V, Rossi GM, Vaglio A
Nephrol Dial Transplant 2021 Sep 27;36(10):1773-1781. doi: 10.1093/ndt/gfaa083. PMID: 33005943
Tzou M, Gazeley DJ, Mason PJ
Vasc Med 2014 Oct;19(5):407-14. Epub 2014 Aug 26 doi: 10.1177/1358863X14546160. PMID: 25161213

Diagnosis

Vaglio A, Maritati F
J Am Soc Nephrol 2016 Jul;27(7):1880-9. Epub 2016 Feb 9 doi: 10.1681/ASN.2015101110. PMID: 26860343Free PMC Article
Tzou M, Gazeley DJ, Mason PJ
Vasc Med 2014 Oct;19(5):407-14. Epub 2014 Aug 26 doi: 10.1177/1358863X14546160. PMID: 25161213
Pipitone N, Vaglio A, Salvarani C
Best Pract Res Clin Rheumatol 2012 Aug;26(4):439-48. doi: 10.1016/j.berh.2012.07.004. PMID: 23040359
Vaglio A, Salvarani C, Buzio C
Lancet 2006 Jan 21;367(9506):241-51. doi: 10.1016/S0140-6736(06)68035-5. PMID: 16427494
Kottra JJ, Dunnick NR
Radiol Clin North Am 1996 Nov;34(6):1259-75. PMID: 8898793

Therapy

Adam Z, Čermák A, Adamová Z, Řehák Z, Koukalová R, Pour L
Rozhl Chir 2022 Summer;101(6):265-272. doi: 10.33699/PIS.2022.101.6.265-271. PMID: 35973821
Rossi GM, Rocco R, Accorsi Buttini E, Marvisi C, Vaglio A
Intern Emerg Med 2017 Apr;12(3):287-299. Epub 2017 Jan 9 doi: 10.1007/s11739-016-1599-z. PMID: 28070877
Tzou M, Gazeley DJ, Mason PJ
Vasc Med 2014 Oct;19(5):407-14. Epub 2014 Aug 26 doi: 10.1177/1358863X14546160. PMID: 25161213
Pipitone N, Vaglio A, Salvarani C
Best Pract Res Clin Rheumatol 2012 Aug;26(4):439-48. doi: 10.1016/j.berh.2012.07.004. PMID: 23040359
Vaglio A, Salvarani C, Buzio C
Lancet 2006 Jan 21;367(9506):241-51. doi: 10.1016/S0140-6736(06)68035-5. PMID: 16427494

Prognosis

Raglianti V, Rossi GM, Vaglio A
Nephrol Dial Transplant 2021 Sep 27;36(10):1773-1781. doi: 10.1093/ndt/gfaa083. PMID: 33005943
Raffiotta F, da Silva Escoli R, Quaglini S, Rognoni C, Sacchi L, Binda V, Messa P, Moroni G
Am J Kidney Dis 2019 Dec;74(6):742-750. Epub 2019 Jun 14 doi: 10.1053/j.ajkd.2019.04.020. PMID: 31204195
Yachoui R, Sehgal R, Carmichael B
Clin Rheumatol 2016 Feb;35(2):401-7. Epub 2015 Jul 25 doi: 10.1007/s10067-015-3022-y. PMID: 26208444
Tzou M, Gazeley DJ, Mason PJ
Vasc Med 2014 Oct;19(5):407-14. Epub 2014 Aug 26 doi: 10.1177/1358863X14546160. PMID: 25161213
Kottra JJ, Dunnick NR
Radiol Clin North Am 1996 Nov;34(6):1259-75. PMID: 8898793

Clinical prediction guides

Giannese D, Moriconi D, Cupisti A, Zucchi A, Pastore AL, Simonato A, Mogorovich A, Claps F, Bartoletti R
Urol Int 2023;107(2):134-147. Epub 2022 Oct 21 doi: 10.1159/000526114. PMID: 36273441
Kharagjitsing HHS, Hendriksz TR, Fouraux MA, van Gelder T, van Bommel EFH
Int Urol Nephrol 2022 Oct;54(10):2663-2671. Epub 2022 Mar 31 doi: 10.1007/s11255-022-03196-3. PMID: 35359217
Raffiotta F, da Silva Escoli R, Quaglini S, Rognoni C, Sacchi L, Binda V, Messa P, Moroni G
Am J Kidney Dis 2019 Dec;74(6):742-750. Epub 2019 Jun 14 doi: 10.1053/j.ajkd.2019.04.020. PMID: 31204195
Lian L, Wang C, Tian JL
Int J Rheum Dis 2016 Nov;19(11):1049-1055. Epub 2016 Apr 29 doi: 10.1111/1756-185X.12863. PMID: 27125330
Kottra JJ, Dunnick NR
Radiol Clin North Am 1996 Nov;34(6):1259-75. PMID: 8898793

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