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Meningioangiomatosis

MedGen UID:
890255
Concept ID:
C4054534
Disease or Syndrome

Definition

A rare vascular malformation in the cerebral cortex and overlying leptomeninges. It can occur sporadically or in association with neurofibromatosis type 2. [from NCI]

Term Hierarchy

Professional guidelines

PubMed

Feng R, Hu J, Che X, Pan L, Wang Z, Zhang M, Huang F, Xu B, Mao R, Sun A, Bao W, Zhong P, Wang Y
Clin Neurol Neurosurg 2013 Aug;115(8):1407-14. Epub 2013 Feb 26 doi: 10.1016/j.clineuro.2013.01.021. PMID: 23485253

Recent clinical studies

Etiology

Zhang GB, Ying YZ, Huang HW, Yu WJ, Li HY, Zhang XK, Wang YG, Cui Y, Chen Y, Jiang ZL, Lin S
Neurosurg Rev 2022 Oct;45(5):3405-3415. Epub 2022 Sep 5 doi: 10.1007/s10143-022-01855-8. PMID: 36063221
Grabowski MM, Prayson RA
Clin Neuropathol 2015 Mar-Apr;34(2):76-82. doi: 10.5414/NP300820. PMID: 25601060
Feng R, Hu J, Che X, Pan L, Wang Z, Zhang M, Huang F, Xu B, Mao R, Sun A, Bao W, Zhong P, Wang Y
Clin Neurol Neurosurg 2013 Aug;115(8):1407-14. Epub 2013 Feb 26 doi: 10.1016/j.clineuro.2013.01.021. PMID: 23485253
Prayson RA
Pathology 2010;42(5):426-31. doi: 10.3109/00313025.2010.493870. PMID: 20632818
Mut M, Söylemezoğlu F, Firat MM, Palaoğlu S
J Neurosurg 2000 Apr;92(4):706-10. doi: 10.3171/jns.2000.92.4.0706. PMID: 10761664

Diagnosis

Mansour MA, Tarek M
World Neurosurg 2023 Aug;176:199-201. Epub 2023 May 11 doi: 10.1016/j.wneu.2023.05.021. PMID: 37178916
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Tomkinson C, Lu JQ
J Neurol Sci 2018 Sep 15;392:130-136. Epub 2018 Jul 24 doi: 10.1016/j.jns.2018.07.018. PMID: 30056201
Li P, Cui G, Wang Y, Geng M, Wang Z
BMC Neurol 2014 Feb 20;14:32. doi: 10.1186/1471-2377-14-32. PMID: 24555776Free PMC Article

Therapy

Yust-Katz S, Fuller G, Fichman-Horn S, Michaeli N, Inbar E, Lukman J, Limon D, Steiner I, Siegal T
Neurology 2016 Apr 26;86(17):1643-4. Epub 2016 Mar 30 doi: 10.1212/WNL.0000000000002610. PMID: 27029633Free PMC Article

Prognosis

Zhang GB, Ying YZ, Huang HW, Yu WJ, Li HY, Zhang XK, Wang YG, Cui Y, Chen Y, Jiang ZL, Lin S
Neurosurg Rev 2022 Oct;45(5):3405-3415. Epub 2022 Sep 5 doi: 10.1007/s10143-022-01855-8. PMID: 36063221
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Feng R, Hu J, Che X, Pan L, Wang Z, Zhang M, Huang F, Xu B, Mao R, Sun A, Bao W, Zhong P, Wang Y
Clin Neurol Neurosurg 2013 Aug;115(8):1407-14. Epub 2013 Feb 26 doi: 10.1016/j.clineuro.2013.01.021. PMID: 23485253
Kim NR, Choe G, Shin SH, Wang KC, Cho BK, Choi KS, Chi JG
Neuropathol Appl Neurobiol 2002 Feb;28(1):48-56. doi: 10.1046/j.1365-2990.2002.00365.x. PMID: 11849563

Clinical prediction guides

Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
Roux A, Mellerio C, Lechapt-Zalcman E, Still M, Zerah M, Bourgeois M, Pallud J
World Neurosurg 2018 Jun;114:281-288. Epub 2018 Mar 30 doi: 10.1016/j.wneu.2018.03.145. PMID: 29605698
Prayson RA
Pathology 2010;42(5):426-31. doi: 10.3109/00313025.2010.493870. PMID: 20632818
Mut M, Söylemezoğlu F, Firat MM, Palaoğlu S
J Neurosurg 2000 Apr;92(4):706-10. doi: 10.3171/jns.2000.92.4.0706. PMID: 10761664
Giangaspero F, Guiducci A, Lenz FA, Mastronardi L, Burger PC
Am J Surg Pathol 1999 Aug;23(8):872-5. doi: 10.1097/00000478-199908000-00002. PMID: 10435554

Recent systematic reviews

Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266

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    Practice guidelines

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