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Secondary polyarteritis nodosa

MedGen UID:
891829
•Concept ID:
CN237624
•
Disease or Syndrome
Synonyms: Scondary PAN; secondary PAN; Secondary PAN; Secondary periarteritis nodosa; secondary periarteritis nodosa; secondary polyarteritis nodosa
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0018594
Orphanet: ORPHA439746

Definition

Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN (see this term) characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV). [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSecondary polyarteritis nodosa

Professional guidelines

PubMed

Atypical wounds. Best clinical practice and challenges.
Isoherranen K, O'Brien JJ, Barker J, Dissemond J, Hafner J, Jemec GBE, Kamarachev J, Läuchli S, Montero EC, Nobbe S, Sunderkötter C, Velasco ML
J Wound Care 2019 Jun 1;28(Sup6):S1-S92. doi: 10.12968/jowc.2019.28.Sup6.S1. PMID: 31169055
Classification and classification criteria for vasculitis: achievements, limitations and prospects.
Mahr A, de Menthon M
Curr Opin Rheumatol 2015 Jan;27(1):1-9. doi: 10.1097/BOR.0000000000000134. PMID: 25415531
Recent understanding on diagnosis and management of central nervous system vasculitis in children.
Iannetti L, Zito R, Bruschi S, Papetti L, Ulgiati F, Nicita F, Del Balzo F, Spalice A
Clin Dev Immunol 2012;2012:698327. Epub 2012 Sep 12 doi: 10.1155/2012/698327. PMID: 23008735Free PMC Article

Recent clinical studies

Etiology

The Spectrum of the Deficiency of Adenosine Deaminase 2: An Observational Analysis of a 60 Patient Cohort.
Barron KS, Aksentijevich I, Deuitch NT, Stone DL, Hoffmann P, Videgar-Laird R, Soldatos A, Bergerson J, Toro C, Cudrici C, Nehrebecky M, Romeo T, Jones A, Boehm M, Kanakry JA, Dimitrova D, Calvo KR, Alao H, Kapuria D, Ben-Yakov G, Pichard DC, Hathaway L, Brofferio A, McRae E, Moura NS, Schnappauf O, Rosenzweig S, Heller T, Cowen EW, Kastner DL, Ombrello AK
Front Immunol 2021;12:811473. Epub 2022 Jan 10 doi: 10.3389/fimmu.2021.811473. PMID: 35095905Free PMC Article
Imaging in small and medium vessel vasculitis.
Singhal M, Gupta P, Sharma A
Int J Rheum Dis 2019 Jan;22 Suppl 1:78-85. doi: 10.1111/1756-185X.13390. PMID: 30698353
What's new in autoinflammation?
Ozen S
Pediatr Nephrol 2019 Dec;34(12):2449-2456. Epub 2018 Dec 14 doi: 10.1007/s00467-018-4155-4. PMID: 30552566
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Diagnosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Inflammatory muscle involvement in systemic vasculitis: A systematic review.
Conticini E, d'Alessandro M, Al Khayyat SG, D'Alessandro R, D'Ignazio E, Pata AP, Vallifuoco G, Falsetti P, Baldi C, Bardelli M, Gentileschi S, Fabiani C, Mazzei MA, Guarnieri A, Bargagli E, Cantarini L, Frediani B
Autoimmun Rev 2022 Mar;21(3):103029. Epub 2021 Dec 29 doi: 10.1016/j.autrev.2021.103029. PMID: 34971804
Amyloidosis and Glomerular Diseases in Familial Mediterranean Fever.
Siligato R, Gembillo G, Calabrese V, Conti G, Santoro D
Medicina (Kaunas) 2021 Oct 1;57(10) doi: 10.3390/medicina57101049. PMID: 34684086Free PMC Article
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
Polyarteritis nodosa.
Bonsib SM
Semin Diagn Pathol 2001 Feb;18(1):14-23. PMID: 11296989

Therapy

Efficacy and safety of treatments in cutaneous polyarteritis nodosa: A French observational retrospective study.
Bettuzzi T, Jachiet M, Sbidian E, Frumholtz L, Cordoliani F, Mouthon L, Chasset F, Paule R, Bouaziz JD, Guillevin L, Terrier B, Aractingi S, Dupin N, Régent A
J Am Acad Dermatol 2022 May;86(5):1035-1041. Epub 2021 Jul 2 doi: 10.1016/j.jaad.2021.06.872. PMID: 34224771
Amyloidosis and Glomerular Diseases in Familial Mediterranean Fever.
Siligato R, Gembillo G, Calabrese V, Conti G, Santoro D
Medicina (Kaunas) 2021 Oct 1;57(10) doi: 10.3390/medicina57101049. PMID: 34684086Free PMC Article
Cardiac disease in familial Mediterranean fever.
Erken E, Erken E
Rheumatol Int 2018 Jan;38(1):51-58. Epub 2017 Oct 20 doi: 10.1007/s00296-017-3853-8. PMID: 29051974
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Vasculitic neuropathies.
Burns TM, Schaublin GA, Dyck PJ
Neurol Clin 2007 Feb;25(1):89-113. doi: 10.1016/j.ncl.2006.11.002. PMID: 17324722

Prognosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Amyloidosis and Glomerular Diseases in Familial Mediterranean Fever.
Siligato R, Gembillo G, Calabrese V, Conti G, Santoro D
Medicina (Kaunas) 2021 Oct 1;57(10) doi: 10.3390/medicina57101049. PMID: 34684086Free PMC Article
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421
Polyarteritis nodosa.
Bonsib SM
Semin Diagn Pathol 2001 Feb;18(1):14-23. PMID: 11296989

Clinical prediction guides

The Spectrum of the Deficiency of Adenosine Deaminase 2: An Observational Analysis of a 60 Patient Cohort.
Barron KS, Aksentijevich I, Deuitch NT, Stone DL, Hoffmann P, Videgar-Laird R, Soldatos A, Bergerson J, Toro C, Cudrici C, Nehrebecky M, Romeo T, Jones A, Boehm M, Kanakry JA, Dimitrova D, Calvo KR, Alao H, Kapuria D, Ben-Yakov G, Pichard DC, Hathaway L, Brofferio A, McRae E, Moura NS, Schnappauf O, Rosenzweig S, Heller T, Cowen EW, Kastner DL, Ombrello AK
Front Immunol 2021;12:811473. Epub 2022 Jan 10 doi: 10.3389/fimmu.2021.811473. PMID: 35095905Free PMC Article
Amyloidosis and Glomerular Diseases in Familial Mediterranean Fever.
Siligato R, Gembillo G, Calabrese V, Conti G, Santoro D
Medicina (Kaunas) 2021 Oct 1;57(10) doi: 10.3390/medicina57101049. PMID: 34684086Free PMC Article
Imaging in small and medium vessel vasculitis.
Singhal M, Gupta P, Sharma A
Int J Rheum Dis 2019 Jan;22 Suppl 1:78-85. doi: 10.1111/1756-185X.13390. PMID: 30698353
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Recent systematic reviews

Inflammatory muscle involvement in systemic vasculitis: A systematic review.
Conticini E, d'Alessandro M, Al Khayyat SG, D'Alessandro R, D'Ignazio E, Pata AP, Vallifuoco G, Falsetti P, Baldi C, Bardelli M, Gentileschi S, Fabiani C, Mazzei MA, Guarnieri A, Bargagli E, Cantarini L, Frediani B
Autoimmun Rev 2022 Mar;21(3):103029. Epub 2021 Dec 29 doi: 10.1016/j.autrev.2021.103029. PMID: 34971804
Dermatological Manifestations in Pediatric Inflammatory Bowel Disease.
Diaconescu S, Strat S, Balan GG, Anton C, Stefanescu G, Ioniuc I, Stanescu AMA
Medicina (Kaunas) 2020 Aug 23;56(9) doi: 10.3390/medicina56090425. PMID: 32842528Free PMC Article
Haemophagocytic syndrome in rheumatic patients. A systematic review.
Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A
Eur Rev Med Pharmacol Sci 2012 Oct;16(10):1414-24. PMID: 23104659

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