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Moderate sensorineural hearing impairment

MedGen UID:
893142
Concept ID:
C4024664
Finding
Synonym: Moderate neural deafness
 
HPO: HP:0008504

Definition

The presence of a moderate form of sensorineural hearing impairment. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVModerate sensorineural hearing impairment

Professional guidelines

PubMed

Zaw K, Carvalho LS, Aung-Htut MT, Fletcher S, Wilton SD, Chen FK, McLenachan S
Asia Pac J Ophthalmol (Phila) 2022 Jul-Aug 01;11(4):369-379. Epub 2022 Aug 17 doi: 10.1097/APO.0000000000000546. PMID: 36041150
Marx M, Younes E, Chandrasekhar SS, Ito J, Plontke S, O'Leary S, Sterkers O
Eur Ann Otorhinolaryngol Head Neck Dis 2018 Feb;135(1S):S23-S28. Epub 2018 Feb 1 doi: 10.1016/j.anorl.2017.12.011. PMID: 29396226
Le TN, Straatman LV, Lea J, Westerberg B
J Otolaryngol Head Neck Surg 2017 May 23;46(1):41. doi: 10.1186/s40463-017-0219-x. PMID: 28535812Free PMC Article

Recent clinical studies

Etiology

Rohrbach M, Klein A, Köhli-Wiesner A, Veraguth D, Scheer I, Balmer C, Lauener R, Baumgartner MR
J Inherit Metab Dis 2010 Dec;33(6):751-7. Epub 2010 Sep 30 doi: 10.1007/s10545-010-9209-0. PMID: 20882352
Magni C, Freiberger F, Tonn K
Braz J Otorhinolaryngol 2005 Sep-Oct;71(5):650-7. Epub 2006 Mar 31 PMID: 16612528
Norbury CF, Bishop DV, Briscoe J
J Speech Lang Hear Res 2001 Feb;44(1):165-78. doi: 10.1044/1092-4388(2001/015). PMID: 11218100
Rakerd B, Punch J, Hooks W, Amlani A, Vander Velde TJ
J Speech Lang Hear Res 1999 Dec;42(6):1285-94. doi: 10.1044/jslhr.4206.1285. PMID: 10599612

Diagnosis

Reinhart P, Zahorik P, Souza P
J Am Acad Audiol 2020 Jan;31(1):17-29. Epub 2019 Jul 1 doi: 10.3766/jaaa.18048. PMID: 31267958Free PMC Article
Reinhart P, Zahorik P, Souza P
Ear Hear 2019 Sep/Oct;40(5):1098-1105. doi: 10.1097/AUD.0000000000000696. PMID: 31025984Free PMC Article
Gallant E, Francey L, Tsai EA, Berman M, Zhao Y, Fetting H, Kaur M, Deardorff MA, Wilkens A, Clark D, Hakonarson H, Rehm HL, Krantz ID
Am J Med Genet A 2013 Sep;161A(9):2148-57. Epub 2013 Jul 19 doi: 10.1002/ajmg.a.36042. PMID: 23873582Free PMC Article
Norbury CF, Bishop DV, Briscoe J
J Speech Lang Hear Res 2001 Feb;44(1):165-78. doi: 10.1044/1092-4388(2001/015). PMID: 11218100
Hall JW 3rd, Grose JH, Buss E, Hatch DR
J Speech Lang Hear Res 1998 Apr;41(2):340-54. doi: 10.1044/jslhr.4102.340. PMID: 9570587

Therapy

Rohrbach M, Klein A, Köhli-Wiesner A, Veraguth D, Scheer I, Balmer C, Lauener R, Baumgartner MR
J Inherit Metab Dis 2010 Dec;33(6):751-7. Epub 2010 Sep 30 doi: 10.1007/s10545-010-9209-0. PMID: 20882352
Hall JW 3rd, Buss E, Grose JH
J Acoust Soc Am 2008 Aug;124(2):1105-15. doi: 10.1121/1.2940582. PMID: 18681600Free PMC Article

Prognosis

Rohrbach M, Klein A, Köhli-Wiesner A, Veraguth D, Scheer I, Balmer C, Lauener R, Baumgartner MR
J Inherit Metab Dis 2010 Dec;33(6):751-7. Epub 2010 Sep 30 doi: 10.1007/s10545-010-9209-0. PMID: 20882352

Clinical prediction guides

Dirks DD, Kamm CA, Dubno JR, Velde TM
Scand Audiol 1981;10(4):239-46. doi: 10.3109/01050398109076187. PMID: 7323674

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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    Consumer resources

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