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Anomalous muscle bundle of the right ventricle

MedGen UID:
902167
•Concept ID:
C4280792
•
Congenital Abnormality
Synonym: Right ventricular anomalous muscle bundle
 
HPO: HP:0030740

Definition

An accessory (not normally present) muscle bundle in the right ventricle which obstructs the right ventricular outflow tract. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnomalous muscle bundle of the right ventricle

Recent clinical studies

Etiology

Spatial relationship between the ventricular septal defect and the anomalous muscle bundle in a double-chambered right ventricle.
Hubail ZJ, Ramaciotti C
Congenit Heart Dis 2007 Nov-Dec;2(6):421-3. doi: 10.1111/j.1747-0803.2007.00135.x. PMID: 18377435
The role of echocardiography in diagnosing double chambered right ventricle in adults.
Hoffman P, Wójcik AW, Rózański J, Siudalska H, Jakubowska E, Włodarska EK, Kowalski M
Heart 2004 Jul;90(7):789-93. doi: 10.1136/hrt.2003.017137. PMID: 15201250Free PMC Article
Development of a double-chambered right ventricle after repair of tetralogy of Fallot.
Moran AM, Hornberger LK, Jonas RA, Keane JF
J Am Coll Cardiol 1998 Apr;31(5):1127-33. doi: 10.1016/s0735-1097(98)00034-5. PMID: 9562018
Double-chambered right ventricle.
Simpson WF Jr, Sade RM, Crawford FA, Taylor AB, Fyfe DA
Ann Thorac Surg 1987 Jul;44(1):7-10. doi: 10.1016/s0003-4975(10)62343-0. PMID: 3606262
Complete transposition of the great arteries and coarctation of the aorta.
Vogel M, Freedom RM, Smallhorn JF, Williams WG, Trusler GA, Rowe RD
Am J Cardiol 1984 Jun 1;53(11):1627-32. doi: 10.1016/0002-9149(84)90591-5. PMID: 6731307

Diagnosis

Double-chambered Right Ventricle in Children.
Yuan SM
J Coll Physicians Surg Pak 2019 Dec;29(12):1193-1198. doi: 10.29271/jcpsp.2019.12.1193. PMID: 31839094
Surgical management of double-chambered right ventricle in adults.
Darwazah AK, Eida M, Bader V, Khalil M
Tex Heart Inst J 2011;38(3):301-4. PMID: 21720479Free PMC Article
Quadrichambered ventricles.
Akdemir R, Balci MM, Ozer C, Karcaaltincaba M, Acikel S
Cardiol J 2010;17(3):303-5. PMID: 20535723
Double-chambered right ventricle.
Simpson WF Jr, Sade RM, Crawford FA, Taylor AB, Fyfe DA
Ann Thorac Surg 1987 Jul;44(1):7-10. doi: 10.1016/s0003-4975(10)62343-0. PMID: 3606262
Anomalous muscle bundle of the right ventricle. Its recognition and surgical treatment.
Li MD, Coles JC, McDonald AC
Br Heart J 1978 Sep;40(9):1040-5. doi: 10.1136/hrt.40.9.1040. PMID: 708529Free PMC Article

Therapy

Double-chambered right ventricle associated with mural and pulmonic valve endocarditis: description of a clinical case and review of the literature.
López-Pardo F, Aguilera A, Villa M, Granado C, Campos A, Cisneros JM
Echocardiography 2004 Feb;21(2):171-3. doi: 10.1111/j.0742-2822.2004.02171.x. PMID: 14961798
Rhabdomyomatous dysplasia of the newborn lung associated with multiple congenital malformations of the heart and great vessels.
Lienicke U, Hammer H, Schneider M, Heling K, Wauer RR, Mau H, Vogel M
Pediatr Pulmonol 2002 Sep;34(3):222-5. doi: 10.1002/ppul.10114. PMID: 12203852
Dysplasia of AV valve in complete AV canal with tetralogy of Fallot: surgical repair.
Otero-Coto E, Castaneda AR
Pediatr Cardiol 1984 Jul-Sep;5(3):213-5. doi: 10.1007/BF02427048. PMID: 6531264

Prognosis

Double-chambered Right Ventricle in Children.
Yuan SM
J Coll Physicians Surg Pak 2019 Dec;29(12):1193-1198. doi: 10.29271/jcpsp.2019.12.1193. PMID: 31839094
Double-chambered right ventricle associated with mural and pulmonic valve endocarditis: description of a clinical case and review of the literature.
López-Pardo F, Aguilera A, Villa M, Granado C, Campos A, Cisneros JM
Echocardiography 2004 Feb;21(2):171-3. doi: 10.1111/j.0742-2822.2004.02171.x. PMID: 14961798
Double-chambered right ventricle.
Simpson WF Jr, Sade RM, Crawford FA, Taylor AB, Fyfe DA
Ann Thorac Surg 1987 Jul;44(1):7-10. doi: 10.1016/s0003-4975(10)62343-0. PMID: 3606262
The risk of surgical treatment of tetralogy of Fallot: an appraisal.
Rizzoli G, Mazzucco A, Brumana T, Stellin G, Livi U, Faggian G, Canola R, Milanesi O, Gallucci V
Int J Cardiol 1985 Sep;9(1):7-26. doi: 10.1016/0167-5273(85)90398-5. PMID: 2412970
Anomalous muscle bundle of the right ventricle. A report of seven cases.
Shiratsu F, Suzuki T, Ohno M
J Cardiovasc Surg (Torino) 1975 Mar-Apr;16(2):198-204. PMID: 123923

Clinical prediction guides

The potential for subpulmonary obstruction in complete transposition after the arterial switch procedure. An anatomic study.
Boyadjiev K, Ho SY, Anderson RH, Lincoln C
Eur J Cardiothorac Surg 1990;4(4):214-8. doi: 10.1016/1010-7940(90)90008-n. PMID: 2334562
Morphological characteristics of perimembranous ventricular septal defects and their surgical significance.
Ueda M, Becker AE
Int J Cardiol 1985 Jun;8(2):149-61. doi: 10.1016/0167-5273(85)90282-7. PMID: 4008105
The risk of surgical treatment of tetralogy of Fallot: an appraisal.
Rizzoli G, Mazzucco A, Brumana T, Stellin G, Livi U, Faggian G, Canola R, Milanesi O, Gallucci V
Int J Cardiol 1985 Sep;9(1):7-26. doi: 10.1016/0167-5273(85)90398-5. PMID: 2412970

Recent systematic reviews

Double-chambered Right Ventricle in Children.
Yuan SM
J Coll Physicians Surg Pak 2019 Dec;29(12):1193-1198. doi: 10.29271/jcpsp.2019.12.1193. PMID: 31839094

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