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Hemangiopericytoma, malignant

MedGen UID:
90803
•Concept ID:
C0334542
•
Neoplastic Process
Synonym: Hemangiopericytoma, Malignant
 
Monarch Initiative: MONDO:0009330
OMIM®: 234820

Definition

An uncommon malignant neoplasm arising from pericytes. Distinction between benign and malignant hemangiopericytoma may be difficult or even impossible on morphologic grounds alone. [from NCI]

Clinical features

From HPO
Abnormality of the cardiovascular system
MedGen UID:
116727
•Concept ID:
C0243050
•
Congenital Abnormality
Any abnormality of the cardiovascular system.
See: Feature record | Search on this feature

Professional guidelines

PubMed

Primary cancer of the sphenoid sinus--a GETTEC study.
Vedrine PO, Thariat J, Merrot O, Percodani J, Dufour X, Choussy O, Toussaint B, Dassonville O, Klossek JM, Santini J, Jankowski R
Head Neck 2009 Mar;31(3):388-97. doi: 10.1002/hed.20966. PMID: 18972425
Possible role of single-voxel (1)H-MRS in differential diagnosis of suprasellar tumors.
Chernov MF, Kawamata T, Amano K, Ono Y, Suzuki T, Nakamura R, Muragaki Y, Iseki H, Kubo O, Hori T, Takakura K
J Neurooncol 2009 Jan;91(2):191-8. Epub 2008 Sep 30 doi: 10.1007/s11060-008-9698-y. PMID: 18825316
The role of radiotherapy in the management of malignant hemangiopericytoma: report of eleven new cases and review of the literature.
Mira JG, Chu FC, Fortner JG
Cancer 1977 Mar;39(3):1254-9. doi: 10.1002/1097-0142(197703)39:3<1254::aid-cncr2820390335>3.0.co;2-j. PMID: 334363

Recent clinical studies

Etiology

Presurgical differentiation between malignant haemangiopericytoma and angiomatous meningioma by a radiomics approach based on texture analysis.
Li X, Lu Y, Xiong J, Wang D, She D, Kuai X, Geng D, Yin B
J Neuroradiol 2019 Sep;46(5):281-287. Epub 2019 Jun 18 doi: 10.1016/j.neurad.2019.05.013. PMID: 31226327
Analysis of Prognostic Factors, Survival Rates, and Treatment in Anaplastic Hemangiopericytoma.
Zhang GJ, Zhang LW, Li D, Wu Z, Zhang JT
World Neurosurg 2017 Aug;104:795-801. Epub 2017 May 25 doi: 10.1016/j.wneu.2017.05.092. PMID: 28552736
Hemangiopericytoma of the cervicothoracic spine: a case report and literature review.
Zhang P, Hu J, Zhou D
Turk Neurosurg 2014;24(6):948-53. doi: 10.5137/1019-5149.JTN.8299-13.1. PMID: 25448214
Primary sarcoma of the liver in the adult. Report of five surgically treated patients.
Zornig C, Kremer B, Henne-Bruns D, Weh HJ, Schröder S, Brölsch CE
Hepatogastroenterology 1992 Aug;39(4):319-21. PMID: 1427575
Variability of histologic pattern in recurrent soft tissue sarcomas originally diagnosed as liposarcoma.
Snover DC, Sumner HW, Dehner LP
Cancer 1982 Mar 1;49(5):1005-15. doi: 10.1002/1097-0142(19820301)49:5<1005::aid-cncr2820490526>3.0.co;2-o. PMID: 6277453

Diagnosis

Presurgical differentiation between malignant haemangiopericytoma and angiomatous meningioma by a radiomics approach based on texture analysis.
Li X, Lu Y, Xiong J, Wang D, She D, Kuai X, Geng D, Yin B
J Neuroradiol 2019 Sep;46(5):281-287. Epub 2019 Jun 18 doi: 10.1016/j.neurad.2019.05.013. PMID: 31226327
Analysis of Prognostic Factors, Survival Rates, and Treatment in Anaplastic Hemangiopericytoma.
Zhang GJ, Zhang LW, Li D, Wu Z, Zhang JT
World Neurosurg 2017 Aug;104:795-801. Epub 2017 May 25 doi: 10.1016/j.wneu.2017.05.092. PMID: 28552736
Malignant Myopericytoma: Report of a New Case and Review of the Literature.
Patrick A, Soares-de-Almeida L, Heinz K
Am J Dermatopathol 2016 Apr;38(4):307-11. doi: 10.1097/DAD.0000000000000463. PMID: 26863056
'Papillary' solitary fibrous tumor/hemangiopericytoma with nuclear STAT6 expression and NAB2-STAT6 fusion.
Ishizawa K, Tsukamoto Y, Ikeda S, Suzuki T, Homma T, Mishima K, Nishikawa R, Sasaki A
Brain Tumor Pathol 2016 Apr;33(2):151-6. Epub 2016 Jan 8 doi: 10.1007/s10014-015-0247-z. PMID: 26746203
Rapidly progressing left atrial hemangiopericytoma.
Nakamura T, Ito H, Sakata K, Kobayashi Y
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1056-9. Epub 2014 Apr 2 doi: 10.1177/0218492314530979. PMID: 24696103

Therapy

Primary sarcoma of the liver in the adult. Report of five surgically treated patients.
Zornig C, Kremer B, Henne-Bruns D, Weh HJ, Schröder S, Brölsch CE
Hepatogastroenterology 1992 Aug;39(4):319-21. PMID: 1427575

Prognosis

A dedifferentiated intracranial solitary fibrous tumor with osteosarcoma components: rapid tumor progression and lethal clinical course.
Kambe A, Nakada S, Nagao Y, Uno T, Sakamoto M, Shomori K, Tanabe M, Kondo S, Kurosaki M
Brain Tumor Pathol 2020 Oct;37(4):165-170. Epub 2020 Aug 2 doi: 10.1007/s10014-020-00374-y. PMID: 32740753
Analysis of Prognostic Factors, Survival Rates, and Treatment in Anaplastic Hemangiopericytoma.
Zhang GJ, Zhang LW, Li D, Wu Z, Zhang JT
World Neurosurg 2017 Aug;104:795-801. Epub 2017 May 25 doi: 10.1016/j.wneu.2017.05.092. PMID: 28552736
Rapidly progressing left atrial hemangiopericytoma.
Nakamura T, Ito H, Sakata K, Kobayashi Y
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1056-9. Epub 2014 Apr 2 doi: 10.1177/0218492314530979. PMID: 24696103
Primary epidural hemangiopericytoma in the sacrum: a rare case and literature review.
Liu J, Cao L, Liu L, Guo S, Tai H, Chen Z
Tumour Biol 2014 Nov;35(11):11655-8. Epub 2014 Aug 20 doi: 10.1007/s13277-014-2455-2. PMID: 25139096
Primary osseous hemangiopericytoma in the thoracic spine.
Ren K, Zhou X, Wu S, Sun X
Clin Neuropathol 2014 Sep-Oct;33(5):364-70. doi: 10.5414/NP300741. PMID: 24887400

Clinical prediction guides

Malignant Myopericytoma: Report of a New Case and Review of the Literature.
Patrick A, Soares-de-Almeida L, Heinz K
Am J Dermatopathol 2016 Apr;38(4):307-11. doi: 10.1097/DAD.0000000000000463. PMID: 26863056
Rapidly progressing left atrial hemangiopericytoma.
Nakamura T, Ito H, Sakata K, Kobayashi Y
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1056-9. Epub 2014 Apr 2 doi: 10.1177/0218492314530979. PMID: 24696103

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