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Intravascular papillary endothelial hyperplasia

MedGen UID:
91005
Concept ID:
C0343083
Neoplastic Process
Synonyms: Masson's pseudoangiosarcoma; Masson's tumor; Masson's vegetant intravascular hemangio-endothelioma
SNOMED CT: Intravascular papillary endothelial hyperplasia (238770007); Masson's pseudosarcoma (238770007)
 
Monarch Initiative: MONDO:0043349

Definition

A reactive, well-circumscribed vascular lesion. It is characterized by the formation of thin papillae projecting within the lumen of blood vessels. The papillae are lined by plump endothelial cells. Blood clots are also present. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIntravascular papillary endothelial hyperplasia

Professional guidelines

PubMed

Suster S, Wong TY
Am J Dermatopathol 1994 Aug;16(4):355-63. doi: 10.1097/00000372-199408000-00001. PMID: 7526723

Recent clinical studies

Etiology

Custer PL, Ho TC, Boulos F
Ophthalmic Plast Reconstr Surg 2023 Jan-Feb 01;39(1):58-63. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002241. PMID: 35793665
Yang K, Pan CX, Russell-Goldman EE, Nambudiri VE
Clin Exp Dermatol 2022 Aug;47(8):1550-1553. Epub 2022 Apr 28 doi: 10.1111/ced.15182. PMID: 35297528
Maktabi AM, Almater AI, Alkatan HM
Eur J Ophthalmol 2022 Jul;32(4):1934-1941. Epub 2021 Oct 7 doi: 10.1177/11206721211048111. PMID: 34615394
Díaz-Flores L, Gutiérrez R, Gayoso S, García MP, González-Gómez M, Díaz-Flores L Jr, Sánchez R, Carrasco JL, Madrid JF
Histol Histopathol 2020 Oct;35(10):1083-1103. Epub 2020 Apr 24 doi: 10.14670/HH-18-222. PMID: 32329808
Kim OH, Kim YM, Choo HJ, Lee SJ, Kim YM, Yi JH, Lee YH
Skeletal Radiol 2016 Feb;45(2):227-33. Epub 2015 Nov 12 doi: 10.1007/s00256-015-2281-7. PMID: 26559670

Diagnosis

Campbell SN, Jones JM, Balikani L, Saltrick KR
J Foot Ankle Surg 2023 May-Jun;62(3):458-464. Epub 2022 Nov 20 doi: 10.1053/j.jfas.2022.11.007. PMID: 36496339
Yang K, Pan CX, Russell-Goldman EE, Nambudiri VE
Clin Exp Dermatol 2022 Aug;47(8):1550-1553. Epub 2022 Apr 28 doi: 10.1111/ced.15182. PMID: 35297528
Luigi L, Diana R, Luca F, Pierluigi M, Gregorio L, Cicciù M
J Craniofac Surg 2022 Jun 1;33(4):e431-e433. Epub 2021 Nov 10 doi: 10.1097/SCS.0000000000008372. PMID: 34759253
Maktabi AM, Almater AI, Alkatan HM
Eur J Ophthalmol 2022 Jul;32(4):1934-1941. Epub 2021 Oct 7 doi: 10.1177/11206721211048111. PMID: 34615394
Kim OH, Kim YM, Choo HJ, Lee SJ, Kim YM, Yi JH, Lee YH
Skeletal Radiol 2016 Feb;45(2):227-33. Epub 2015 Nov 12 doi: 10.1007/s00256-015-2281-7. PMID: 26559670

Therapy

Agarwal S, Gaur K, Arya V
Indian J Pathol Microbiol 2023 Apr-Jun;66(2):366-368. doi: 10.4103/ijpm.ijpm_356_21. PMID: 37077086
Sim SY, Lim YC, Won KS, Cho KG
J Neurosurg Pediatr 2015 Apr;15(4):384-91. Epub 2015 Jan 16 doi: 10.3171/2014.9.PEDS13518. PMID: 25580513
Pegado PF, Ordi QC, Roche S, Rivas AG, Domiguez RO
Skeletal Radiol 2015 Jun;44(6):859-62. Epub 2014 Nov 28 doi: 10.1007/s00256-014-2058-4. PMID: 25427786
Cohen A, Maly A, Azaz B
Gerodontology 2009 Dec;26(4):305-8. Epub 2009 Aug 21 doi: 10.1111/j.1741-2358.2009.00287.x. PMID: 19702673
Steffee CH, Iskandar SS
Hum Pathol 1996 Sep;27(9):986-9. doi: 10.1016/s0046-8177(96)90230-0. PMID: 8816898

Prognosis

Massimilla EA, Panetti G, Motta G, Fiorelli A, Montella M, Testa D, Motta G
Am J Case Rep 2022 Aug 28;23:e936402. doi: 10.12659/AJCR.936402. PMID: 36030377Free PMC Article
Espinosa A, González J, García-Navas F
J Foot Ankle Surg 2017 Jan-Feb;56(1):72-74. doi: 10.1053/j.jfas.2016.09.016. PMID: 27989349
Fabre AB, Passos PC, Lima BZ, Fabricio L, Fillus Neto J, Bonalumi Filho A
An Bras Dermatol 2014 Jul-Aug;89(4):677-8. doi: 10.1590/abd1806-4841.20142787. PMID: 25054765Free PMC Article
Akdur NC, Donmez M, Gozel S, Ustun H, Hucumenoglu S
Diagn Pathol 2013 Oct 14;8:167. doi: 10.1186/1746-1596-8-167. PMID: 24125024Free PMC Article
Clearkin KP, Enzinger FM
Arch Pathol Lab Med 1976 Aug;100(8):441-4. PMID: 947306

Clinical prediction guides

Campbell SN, Jones JM, Balikani L, Saltrick KR
J Foot Ankle Surg 2023 May-Jun;62(3):458-464. Epub 2022 Nov 20 doi: 10.1053/j.jfas.2022.11.007. PMID: 36496339
Custer PL, Ho TC, Boulos F
Ophthalmic Plast Reconstr Surg 2023 Jan-Feb 01;39(1):58-63. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002241. PMID: 35793665
Maktabi AM, Almater AI, Alkatan HM
Eur J Ophthalmol 2022 Jul;32(4):1934-1941. Epub 2021 Oct 7 doi: 10.1177/11206721211048111. PMID: 34615394
Díaz-Flores L, Gutiérrez R, García MDP, Carrasco JL, Sáez FJ, Díaz-Flores L Jr, González-Gómez M, Madrid JF
Anat Rec (Hoboken) 2019 Nov;302(11):2003-2013. Epub 2019 Jul 8 doi: 10.1002/ar.24204. PMID: 31228317
Akdur NC, Donmez M, Gozel S, Ustun H, Hucumenoglu S
Diagn Pathol 2013 Oct 14;8:167. doi: 10.1186/1746-1596-8-167. PMID: 24125024Free PMC Article

Recent systematic reviews

Manoranjan B, Mann JA, Joseph JT, Kelly JJ
J Neurosurg Sci 2022 Oct;66(5):420-424. Epub 2021 Aug 3 doi: 10.23736/S0390-5616.21.05372-8. PMID: 34342194
Vieira CC, Gomes APN, Galdino Dos Santos L, de Almeida DS, Hildebrand LC, Flores IL, Dos Santos JN, Schuch LF, Vasconcelos ACU
J Oral Pathol Med 2021 Jan;50(1):103-113. Epub 2020 Dec 7 doi: 10.1111/jop.13127. PMID: 33188642

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