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Lung Epithelioid Hemangioendothelioma

MedGen UID:
91061
•Concept ID:
C0345961
•
Neoplastic Process
Synonyms: Epithelioid Angioendothelioma of Lung; Epithelioid Angioendothelioma of the Lung; Epithelioid hemangioendothelioma of lung; Epithelioid Hemangioendothelioma of Lung; Epithelioid Hemangioendothelioma of the Lung; Intravascular bronchoalveolar tumor; IVBALT - Intravascular bronchoalveolar tumor; Lung Epithelioid Angioendothelioma; Pulmonary Epithelioid Angioendothelioma; Pulmonary Epithelioid Hemangioendothelioma
SNOMED CT: Epithelioid hemangioendothelioma of lung (254635004); Intravascular bronchoalveolar tumor (254635004); IVBALT - Intravascular bronchoalveolar tumor (254635004)

Definition

A low-grade malignant blood vessel neoplasm arising from the lung. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLung Epithelioid Hemangioendothelioma

Professional guidelines

PubMed

Management Strategies for Patients With Epithelioid Hemangioendothelioma: Charting an Indolent Disease Course.
Yurkiewicz IR, Zhou M, Ganjoo KN, Charville GW, Bolleddu S, Lohman M, Bui N
Am J Clin Oncol 2021 Aug 1;44(8):419-422. doi: 10.1097/COC.0000000000000827. PMID: 34028371
Epithelioid Hemangioendothelioma: Update on Diagnosis and Treatment.
Rosenberg A, Agulnik M
Curr Treat Options Oncol 2018 Mar 15;19(4):19. doi: 10.1007/s11864-018-0536-y. PMID: 29546487
Primary sarcomas of the lung.
Suster S
Semin Diagn Pathol 1995 May;12(2):140-57. PMID: 7638447

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