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Malignant exocrine pancreas neoplasm

MedGen UID:
91108
Concept ID:
C0346648
Neoplastic Process
Synonyms: cancer of exocrine pancreas; exocrine pancreas cancer; Malignant Exocrine Pancreas Neoplasm; malignant exocrine pancreas neoplasm; Malignant Exocrine Pancreas Tumor; malignant exocrine pancreas tumor; Malignant Neoplasm of Exocrine Pancreas; malignant neoplasm of exocrine pancreas; Malignant Neoplasm of the Exocrine Pancreas; malignant neoplasm of the exocrine pancreas; Malignant tumor of exocrine pancreas; Malignant Tumor of Exocrine Pancreas; malignant tumor of exocrine pancreas; Malignant Tumor of the Exocrine Pancreas; malignant tumor of the exocrine pancreas; Pancreatic exocrine cancer; tumor of exocrine pancreas
SNOMED CT: Malignant tumor of exocrine pancreas (255088001); Pancreatic exocrine cancer (255088001)
 
Monarch Initiative: MONDO:0002116

Definition

A malignant neoplasm that arises from the epithelial cells of the exocrine pancreatic tissue. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMalignant exocrine pancreas neoplasm

Professional guidelines

PubMed

De Luca R, Gianotti L, Pedrazzoli P, Brunetti O, Rizzo A, Sandini M, Paiella S, Pecorelli N, Pugliese L, Pietrabissa A, Zerbi A, Salvia R, Boggi U, Casirati A, Falconi M, Caccialanza R
Eur J Surg Oncol 2023 Mar;49(3):542-549. Epub 2022 Dec 22 doi: 10.1016/j.ejso.2022.12.006. PMID: 36577556
Skórzewska M, Kurzawa P, Ciszewski T, Pelc Z, Polkowski WP
Surg Oncol 2022 Sep;44:101853. Epub 2022 Sep 14 doi: 10.1016/j.suronc.2022.101853. PMID: 36152420
Seufferlein T, Porzner M, Heinemann V, Tannapfel A, Stuschke M, Uhl W
Dtsch Arztebl Int 2014 May 30;111(22):396-402. doi: 10.3238/arztebl.2014.0396. PMID: 24980565Free PMC Article

Recent clinical studies

Etiology

Vlavcheski F, O'Neill EJ, Gagacev F, Tsiani E
Molecules 2022 Dec 6;27(23) doi: 10.3390/molecules27238630. PMID: 36500723Free PMC Article
Li S, Xie K
Biochim Biophys Acta Rev Cancer 2022 Mar;1877(2):188698. Epub 2022 Feb 15 doi: 10.1016/j.bbcan.2022.188698. PMID: 35176433
Grossberg AJ, Chu LC, Deig CR, Fishman EK, Hwang WL, Maitra A, Marks DL, Mehta A, Nabavizadeh N, Simeone DM, Weekes CD, Thomas CR Jr
CA Cancer J Clin 2020 Sep;70(5):375-403. Epub 2020 Jul 19 doi: 10.3322/caac.21626. PMID: 32683683Free PMC Article
Singh VK, Haupt ME, Geller DE, Hall JA, Quintana Diez PM
World J Gastroenterol 2017 Oct 21;23(39):7059-7076. doi: 10.3748/wjg.v23.i39.7059. PMID: 29093615Free PMC Article
Hart PA, Bellin MD, Andersen DK, Bradley D, Cruz-Monserrate Z, Forsmark CE, Goodarzi MO, Habtezion A, Korc M, Kudva YC, Pandol SJ, Yadav D, Chari ST; Consortium for the Study of Chronic Pancreatitis, Diabetes, and Pancreatic Cancer(CPDPC)
Lancet Gastroenterol Hepatol 2016 Nov;1(3):226-237. Epub 2016 Oct 12 doi: 10.1016/S2468-1253(16)30106-6. PMID: 28404095Free PMC Article

Diagnosis

Grossberg AJ, Chu LC, Deig CR, Fishman EK, Hwang WL, Maitra A, Marks DL, Mehta A, Nabavizadeh N, Simeone DM, Weekes CD, Thomas CR Jr
CA Cancer J Clin 2020 Sep;70(5):375-403. Epub 2020 Jul 19 doi: 10.3322/caac.21626. PMID: 32683683Free PMC Article
Sarvepalli D, Rashid MU, Rahman AU, Ullah W, Hussain I, Hasan B, Jehanzeb S, Khan AK, Jain AG, Khetpal N, Ahmad S
Crit Rev Oncog 2019;24(2):199-212. doi: 10.1615/CritRevOncog.2019031641. PMID: 31679214
Gilliland TM, Villafane-Ferriol N, Shah KP, Shah RM, Tran Cao HS, Massarweh NN, Silberfein EJ, Choi EA, Hsu C, McElhany AL, Barakat O, Fisher W, Van Buren G
Nutrients 2017 Mar 7;9(3) doi: 10.3390/nu9030243. PMID: 28272344Free PMC Article
Hart PA, Bellin MD, Andersen DK, Bradley D, Cruz-Monserrate Z, Forsmark CE, Goodarzi MO, Habtezion A, Korc M, Kudva YC, Pandol SJ, Yadav D, Chari ST; Consortium for the Study of Chronic Pancreatitis, Diabetes, and Pancreatic Cancer(CPDPC)
Lancet Gastroenterol Hepatol 2016 Nov;1(3):226-237. Epub 2016 Oct 12 doi: 10.1016/S2468-1253(16)30106-6. PMID: 28404095Free PMC Article
Geokas MC, Baltaxe HA, Banks PA, Silva J Jr, Frey CF
Ann Intern Med 1985 Jul;103(1):86-100. doi: 10.7326/0003-4819-103-1-86. PMID: 3890660

Therapy

Grossberg AJ, Chu LC, Deig CR, Fishman EK, Hwang WL, Maitra A, Marks DL, Mehta A, Nabavizadeh N, Simeone DM, Weekes CD, Thomas CR Jr
CA Cancer J Clin 2020 Sep;70(5):375-403. Epub 2020 Jul 19 doi: 10.3322/caac.21626. PMID: 32683683Free PMC Article
Sarvepalli D, Rashid MU, Rahman AU, Ullah W, Hussain I, Hasan B, Jehanzeb S, Khan AK, Jain AG, Khetpal N, Ahmad S
Crit Rev Oncog 2019;24(2):199-212. doi: 10.1615/CritRevOncog.2019031641. PMID: 31679214
Singh VK, Haupt ME, Geller DE, Hall JA, Quintana Diez PM
World J Gastroenterol 2017 Oct 21;23(39):7059-7076. doi: 10.3748/wjg.v23.i39.7059. PMID: 29093615Free PMC Article
Gilliland TM, Villafane-Ferriol N, Shah KP, Shah RM, Tran Cao HS, Massarweh NN, Silberfein EJ, Choi EA, Hsu C, McElhany AL, Barakat O, Fisher W, Van Buren G
Nutrients 2017 Mar 7;9(3) doi: 10.3390/nu9030243. PMID: 28272344Free PMC Article
Geokas MC, Baltaxe HA, Banks PA, Silva J Jr, Frey CF
Ann Intern Med 1985 Jul;103(1):86-100. doi: 10.7326/0003-4819-103-1-86. PMID: 3890660

Prognosis

Grossberg AJ, Chu LC, Deig CR, Fishman EK, Hwang WL, Maitra A, Marks DL, Mehta A, Nabavizadeh N, Simeone DM, Weekes CD, Thomas CR Jr
CA Cancer J Clin 2020 Sep;70(5):375-403. Epub 2020 Jul 19 doi: 10.3322/caac.21626. PMID: 32683683Free PMC Article
Gilliland TM, Villafane-Ferriol N, Shah KP, Shah RM, Tran Cao HS, Massarweh NN, Silberfein EJ, Choi EA, Hsu C, McElhany AL, Barakat O, Fisher W, Van Buren G
Nutrients 2017 Mar 7;9(3) doi: 10.3390/nu9030243. PMID: 28272344Free PMC Article
Grant TJ, Hua K, Singh A
Prog Mol Biol Transl Sci 2016;144:241-275. Epub 2016 Oct 15 doi: 10.1016/bs.pmbts.2016.09.008. PMID: 27865459Free PMC Article
Bailey P, Chang DK, Nones K, Johns AL, Patch AM, Gingras MC, Miller DK, Christ AN, Bruxner TJ, Quinn MC, Nourse C, Murtaugh LC, Harliwong I, Idrisoglu S, Manning S, Nourbakhsh E, Wani S, Fink L, Holmes O, Chin V, Anderson MJ, Kazakoff S, Leonard C, Newell F, Waddell N, Wood S, Xu Q, Wilson PJ, Cloonan N, Kassahn KS, Taylor D, Quek K, Robertson A, Pantano L, Mincarelli L, Sanchez LN, Evers L, Wu J, Pinese M, Cowley MJ, Jones MD, Colvin EK, Nagrial AM, Humphrey ES, Chantrill LA, Mawson A, Humphris J, Chou A, Pajic M, Scarlett CJ, Pinho AV, Giry-Laterriere M, Rooman I, Samra JS, Kench JG, Lovell JA, Merrett ND, Toon CW, Epari K, Nguyen NQ, Barbour A, Zeps N, Moran-Jones K, Jamieson NB, Graham JS, Duthie F, Oien K, Hair J, Grützmann R, Maitra A, Iacobuzio-Donahue CA, Wolfgang CL, Morgan RA, Lawlor RT, Corbo V, Bassi C, Rusev B, Capelli P, Salvia R, Tortora G, Mukhopadhyay D, Petersen GM; Australian Pancreatic Cancer Genome Initiative, Munzy DM, Fisher WE, Karim SA, Eshleman JR, Hruban RH, Pilarsky C, Morton JP, Sansom OJ, Scarpa A, Musgrove EA, Bailey UM, Hofmann O, Sutherland RL, Wheeler DA, Gill AJ, Gibbs RA, Pearson JV, Waddell N, Biankin AV, Grimmond SM
Nature 2016 Mar 3;531(7592):47-52. Epub 2016 Feb 24 doi: 10.1038/nature16965. PMID: 26909576
Geokas MC, Baltaxe HA, Banks PA, Silva J Jr, Frey CF
Ann Intern Med 1985 Jul;103(1):86-100. doi: 10.7326/0003-4819-103-1-86. PMID: 3890660

Clinical prediction guides

Capurso G, Pecorelli N, Burini A, Orsi G, Palumbo D, Macchini M, Mele R, de Cobelli F, Falconi M, Arcidiacono PG, Reni M
Expert Rev Anticancer Ther 2022 Feb;22(2):155-167. Epub 2022 Jan 12 doi: 10.1080/14737140.2022.2026771. PMID: 34989653
Hosein AN, Dangol G, Okumura T, Roszik J, Rajapakshe K, Siemann M, Zaid M, Ghosh B, Monberg M, Guerrero PA, Singhi A, Haymaker CL, Clevers H, Abou-Elkacem L, Woermann SM, Maitra A
Gastroenterology 2022 Apr;162(4):1303-1318.e18. Epub 2021 Dec 30 doi: 10.1053/j.gastro.2021.12.273. PMID: 34973294Free PMC Article
Puleo F, Nicolle R, Blum Y, Cros J, Marisa L, Demetter P, Quertinmont E, Svrcek M, Elarouci N, Iovanna J, Franchimont D, Verset L, Galdon MG, Devière J, de Reyniès A, Laurent-Puig P, Van Laethem JL, Bachet JB, Maréchal R
Gastroenterology 2018 Dec;155(6):1999-2013.e3. Epub 2018 Aug 27 doi: 10.1053/j.gastro.2018.08.033. PMID: 30165049
Singh VK, Haupt ME, Geller DE, Hall JA, Quintana Diez PM
World J Gastroenterol 2017 Oct 21;23(39):7059-7076. doi: 10.3748/wjg.v23.i39.7059. PMID: 29093615Free PMC Article
Geokas MC, Baltaxe HA, Banks PA, Silva J Jr, Frey CF
Ann Intern Med 1985 Jul;103(1):86-100. doi: 10.7326/0003-4819-103-1-86. PMID: 3890660

Recent systematic reviews

Farrarons SS, van Bodegraven EA, Sauvanet A, Hilal MA, Besselink MG, Dokmak S
Surgery 2022 Nov;172(5):1490-1501. Epub 2022 Aug 18 doi: 10.1016/j.surg.2022.06.024. PMID: 35987787
Radulescu L, Crisan D, Grapa C, Radulescu D
J Gastrointestin Liver Dis 2021 Dec 21;30(4):506-516. doi: 10.15403/jgld-3671. PMID: 34752584
Iglesia D, Avci B, Kiriukova M, Panic N, Bozhychko M, Sandru V, de-Madaria E, Capurso G
United European Gastroenterol J 2020 Nov;8(9):1115-1125. Epub 2020 Jul 6 doi: 10.1177/2050640620938987. PMID: 32631175Free PMC Article
Manuel-Vazquez A, Ramia JM, Latorre-Fragua R, Valle-Rubio A, Arteaga-Peralta V, Ramiro-Pérez C, de la Plaza-Llamas R
Pancreas 2018 May/Jun;47(5):551-555. doi: 10.1097/MPA.0000000000001048. PMID: 29683974
Epstein AS, O'Reilly EM
J Natl Compr Canc Netw 2012 Jul 1;10(7):835-46. doi: 10.6004/jnccn.2012.0087. PMID: 22773799

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