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Vulvar Alveolar Rhabdomyosarcoma

MedGen UID:
925379
•Concept ID:
C4287847
•
Neoplastic Process

Definition

An extremely rare malignant mesenchymal neoplasm of the vulva exhibiting skeletal muscle differentiation with an alveolar pattern. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar Alveolar Rhabdomyosarcoma

Professional guidelines

PubMed

Treatment strategies and outcomes for spinal rhabdomyosarcoma: A series of 11 cases in a single center and review of the literature.
Wang T, Gao X, Yang J, Guo W, Wu Z, Tang L, Cao S, Cai X, Liu T, Jia Q, Xiao J
Clin Neurol Neurosurg 2020 May;192:105729. Epub 2020 Feb 6 doi: 10.1016/j.clineuro.2020.105729. PMID: 32058205
Risk-based management: current concepts of treating malignant solid tumors of childhood.
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Recent clinical studies

Etiology

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Treatment strategies and outcomes for spinal rhabdomyosarcoma: A series of 11 cases in a single center and review of the literature.
Wang T, Gao X, Yang J, Guo W, Wu Z, Tang L, Cao S, Cai X, Liu T, Jia Q, Xiao J
Clin Neurol Neurosurg 2020 May;192:105729. Epub 2020 Feb 6 doi: 10.1016/j.clineuro.2020.105729. PMID: 32058205
Clinicopathologic features of rhabdomyosarcoma of gynecologic origin in adults.
Ferguson SE, Gerald W, Barakat RR, Chi DS, Soslow RA
Am J Surg Pathol 2007 Mar;31(3):382-9. doi: 10.1097/01.pas.0000213352.87885.75. PMID: 17325479
Risk-based management: current concepts of treating malignant solid tumors of childhood.
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467
Rhabdomyosarcoma of the clitoris.
Bond SJ, Seibel N, Kapur S, Newman KD
Cancer 1994 Apr 1;73(7):1984-6. doi: 10.1002/1097-0142(19940401)73:7<1984::aid-cncr2820730733>3.0.co;2-v. PMID: 8137226

Diagnosis

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Alveolar rhabdomyosarcoma of the vulva in an adult: a case report and literature review.
He W, Jin Y, Zhou X, Zhou K, Zhu R
J Int Med Res 2020 Mar;48(3):300060520905438. doi: 10.1177/0300060520905438. PMID: 32223663Free PMC Article
Treatment strategies and outcomes for spinal rhabdomyosarcoma: A series of 11 cases in a single center and review of the literature.
Wang T, Gao X, Yang J, Guo W, Wu Z, Tang L, Cao S, Cai X, Liu T, Jia Q, Xiao J
Clin Neurol Neurosurg 2020 May;192:105729. Epub 2020 Feb 6 doi: 10.1016/j.clineuro.2020.105729. PMID: 32058205
Fine needle aspiration cytolog of perineal alveolar rhabdomyosarcoma: cytohistopathologic and immunocytochemical correlations.
Fulciniti F, Botti G, De Chiara A, Parlato V, Russo S, Vosa L, Nappi MM
Acta Cytol 2007 May-Jun;51(3):385-9. doi: 10.1159/000325752. PMID: 17536540
Risk-based management: current concepts of treating malignant solid tumors of childhood.
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Therapy

Treatment strategies and outcomes for spinal rhabdomyosarcoma: A series of 11 cases in a single center and review of the literature.
Wang T, Gao X, Yang J, Guo W, Wu Z, Tang L, Cao S, Cai X, Liu T, Jia Q, Xiao J
Clin Neurol Neurosurg 2020 May;192:105729. Epub 2020 Feb 6 doi: 10.1016/j.clineuro.2020.105729. PMID: 32058205
Alveolar rhabdomyosarcoma of the vulva. Report of two cases.
Imachi M, Tsukamoto N, Kamura T, Shigematsu T, Funakoshi K, Nakano H
Acta Cytol 1991 May-Jun;35(3):345-9. PMID: 2042436
Alveolar rhabdomyosarcoma of the female genitalia.
Copeland LJ, Sneige N, Stringer CA, Gershenson DM, Saul PB, Kavanagh JJ
Cancer 1985 Aug 15;56(4):849-55. doi: 10.1002/1097-0142(19850815)56:4<849::aid-cncr2820560424>3.0.co;2-l. PMID: 4016676

Prognosis

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Alveolar rhabdomyosarcoma of the vulva in an adult: a case report and literature review.
He W, Jin Y, Zhou X, Zhou K, Zhu R
J Int Med Res 2020 Mar;48(3):300060520905438. doi: 10.1177/0300060520905438. PMID: 32223663Free PMC Article
Treatment strategies and outcomes for spinal rhabdomyosarcoma: A series of 11 cases in a single center and review of the literature.
Wang T, Gao X, Yang J, Guo W, Wu Z, Tang L, Cao S, Cai X, Liu T, Jia Q, Xiao J
Clin Neurol Neurosurg 2020 May;192:105729. Epub 2020 Feb 6 doi: 10.1016/j.clineuro.2020.105729. PMID: 32058205
Fine needle aspiration cytolog of perineal alveolar rhabdomyosarcoma: cytohistopathologic and immunocytochemical correlations.
Fulciniti F, Botti G, De Chiara A, Parlato V, Russo S, Vosa L, Nappi MM
Acta Cytol 2007 May-Jun;51(3):385-9. doi: 10.1159/000325752. PMID: 17536540
Risk-based management: current concepts of treating malignant solid tumors of childhood.
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Clinical prediction guides

Fine needle aspiration cytolog of perineal alveolar rhabdomyosarcoma: cytohistopathologic and immunocytochemical correlations.
Fulciniti F, Botti G, De Chiara A, Parlato V, Russo S, Vosa L, Nappi MM
Acta Cytol 2007 May-Jun;51(3):385-9. doi: 10.1159/000325752. PMID: 17536540
Risk-based management: current concepts of treating malignant solid tumors of childhood.
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467
Alveolar rhabdomyosarcoma of the vulva. Report of two cases.
Imachi M, Tsukamoto N, Kamura T, Shigematsu T, Funakoshi K, Nakano H
Acta Cytol 1991 May-Jun;35(3):345-9. PMID: 2042436

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