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Pelvic Fibromatosis

MedGen UID:
925946
•Concept ID:
C4288414
•
Neoplastic Process
Synonym: Pelvic Desmoid Tumor

Definition

Fibromatosis that occurs in the pelvis. It affects almost always females. It is characterized by the presence of elongated spindle-shaped fibroblasts, collagenous stroma formation, and an infiltrative growth pattern. It recurs if incompletely resected but lacks metastatic potential. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPelvic Fibromatosis

Professional guidelines

PubMed

ACR Appropriateness Criteria(®) Clinically Suspected Adnexal Mass, No Acute Symptoms.
Expert Panel on Women’s Imaging:, Atri M, Alabousi A, Reinhold C, Akin EA, Benson CB, Bhosale PR, Kang SK, Lakhman Y, Nicola R, Pandharipande PV, Patel MD, Salazar GM, Shipp TD, Simpson L, Sussman BL, Uyeda JW, Wall DJ, Whitcomb BP, Zelop CM, Glanc P
J Am Coll Radiol 2019 May;16(5S):S77-S93. doi: 10.1016/j.jacr.2019.02.011. PMID: 31054761
Surgical management of desmoid tumors of the female pelvis.
Mariani A, Nascimento AG, Webb MJ, Sim FH, Podratz KC
J Am Coll Surg 2000 Aug;191(2):175-83. doi: 10.1016/s1072-7515(00)00323-9. PMID: 10945361
Nonsurgical management of children with recurrent or unresectable fibromatosis.
Raney B, Evans A, Granowetter L, Schnaufer L, Uri A, Littman P
Pediatrics 1987 Mar;79(3):394-8. PMID: 3103093

Recent clinical studies

Etiology

Aggressive pelvic angiomyxoma and its mimics: can imaging be the guiding light?
Kumar N, Goyal A, Manchanda S, Sharma R, Kumar A, Bansal VK
Br J Radiol 2020 Jul;93(1111):20200255. Epub 2020 May 21 doi: 10.1259/bjr.20200255. PMID: 32401545Free PMC Article
Large pelvic masses of obscure origin: urologist's perspective.
Kumar S, Sarkar D, Prasad S, Gupta V, Ghosala P, Kaman L, Yadav TD, Ganesamoni R, Singh SK
Urol Int 2012;88(2):215-24. Epub 2012 Feb 23 doi: 10.1159/000334332. PMID: 22377534
Fibromatosis of the female pelvis.
Adcock LL, Downey GO, Votel JL
Obstet Gynecol Surv 1989 May;44(5):347-54. doi: 10.1097/00006254-198905000-00012. PMID: 2657520

Diagnosis

Aggressive pelvic angiomyxoma and its mimics: can imaging be the guiding light?
Kumar N, Goyal A, Manchanda S, Sharma R, Kumar A, Bansal VK
Br J Radiol 2020 Jul;93(1111):20200255. Epub 2020 May 21 doi: 10.1259/bjr.20200255. PMID: 32401545Free PMC Article
Treatment of Aggressive Pelvic Fibromatosis With Interferon.
Ariën F, Aleman JM, Op de Beeck B, Tjalma WAA
Obstet Gynecol 2015 Dec;126(6):1219-1221. doi: 10.1097/AOG.0000000000001158. PMID: 26551174
Large pelvic masses of obscure origin: urologist's perspective.
Kumar S, Sarkar D, Prasad S, Gupta V, Ghosala P, Kaman L, Yadav TD, Ganesamoni R, Singh SK
Urol Int 2012;88(2):215-24. Epub 2012 Feb 23 doi: 10.1159/000334332. PMID: 22377534
Fibromatosis of the female pelvis.
Adcock LL, Downey GO, Votel JL
Obstet Gynecol Surv 1989 May;44(5):347-54. doi: 10.1097/00006254-198905000-00012. PMID: 2657520
Pelvic fibromatosis: case report and review of literature.
Manetta A, Abt AB, Mamourian AC, Podczaski ES, Larson JE, Misas JE, Mortel R
Gynecol Oncol 1989 Jan;32(1):91-4. doi: 10.1016/0090-8258(89)90859-7. PMID: 2642456

Therapy

Treatment of Aggressive Pelvic Fibromatosis With Interferon.
Ariën F, Aleman JM, Op de Beeck B, Tjalma WAA
Obstet Gynecol 2015 Dec;126(6):1219-1221. doi: 10.1097/AOG.0000000000001158. PMID: 26551174
Large pelvic masses of obscure origin: urologist's perspective.
Kumar S, Sarkar D, Prasad S, Gupta V, Ghosala P, Kaman L, Yadav TD, Ganesamoni R, Singh SK
Urol Int 2012;88(2):215-24. Epub 2012 Feb 23 doi: 10.1159/000334332. PMID: 22377534
Long-term survival following aggressive surgery and radiotherapy for pelvic fibromatosis.
Seoud M, Abbas J, Kaspar H, Khalil A, Geara F
Int J Gynecol Cancer 2005 Nov-Dec;15(6):1112-4. doi: 10.1111/j.1525-1438.2005.00171.x. PMID: 16343190
Pelvic fibromatosis (desmoid)--treatment with steroids and tamoxifen.
Mukherjee A, Malcolm A, de la Hunt M, Neal DE
Br J Urol 1995 Apr;75(4):559-60. doi: 10.1111/j.1464-410x.1995.tb07289.x. PMID: 7788276
Diffuse intra-abdominal fibromatosis in association with bilateral ovarian fibromatosis and oedema.
Antoniuk P, Tjandra JJ, Lavery IC
Aust N Z J Surg 1993 Apr;63(4):315-8. doi: 10.1111/j.1445-2197.1993.tb00391.x. PMID: 8311821

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