Pelvic Fibromatosis

MedGen UID:: 925946
•Concept ID:: C4288414
•: Neoplastic Process

Synonym:

Pelvic Desmoid Tumor

Definition

Fibromatosis that occurs in the pelvis. It affects almost always females. It is characterized by the presence of elongated spindle-shaped fibroblasts, collagenous stroma formation, and an infiltrative growth pattern. It recurs if incompletely resected but lacks metastatic potential. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVPelvic Fibromatosis

Benign neoplasm
- Benign connective and soft tissue neoplasm
  - Benign soft tissue neoplasm
    - Benign Fibroblastic Neoplasm
      - Fibroma
        Desmoid tumor
        Pelvic Fibromatosis

Professional guidelines

PubMed

ACR Appropriateness Criteria(®) Clinically Suspected Adnexal Mass, No Acute Symptoms.

Expert Panel on Women’s Imaging:, Atri M, Alabousi A, Reinhold C, Akin EA, Benson CB, Bhosale PR, Kang SK, Lakhman Y, Nicola R, Pandharipande PV, Patel MD, Salazar GM, Shipp TD, Simpson L, Sussman BL, Uyeda JW, Wall DJ, Whitcomb BP, Zelop CM, Glanc P
J Am Coll Radiol 2019 May;16(5S):S77-S93. doi: 10.1016/j.jacr.2019.02.011. PMID: 31054761

Thecoma of the ovary: a report of 70 cases emphasizing aspects of its histopathology different from those often portrayed and its differential diagnosis.

Burandt E, Young RH
Am J Surg Pathol 2014 Aug;38(8):1023-32. doi: 10.1097/PAS.0000000000000252. PMID: 25025365

Surgical management of desmoid tumors of the female pelvis.

Mariani A, Nascimento AG, Webb MJ, Sim FH, Podratz KC
J Am Coll Surg 2000 Aug;191(2):175-83. doi: 10.1016/s1072-7515(00)00323-9. PMID: 10945361

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Recent clinical studies

Therapy

Treatment of Aggressive Pelvic Fibromatosis With Interferon.

Ariën F, Aleman JM, Op de Beeck B, Tjalma WAA
Obstet Gynecol 2015 Dec;126(6):1219-1221. doi: 10.1097/AOG.0000000000001158. PMID: 26551174

Large pelvic masses of obscure origin: urologist's perspective.

Kumar S, Sarkar D, Prasad S, Gupta V, Ghosala P, Kaman L, Yadav TD, Ganesamoni R, Singh SK
Urol Int 2012;88(2):215-24. Epub 2012 Feb 23 doi: 10.1159/000334332. PMID: 22377534

Mucosal pigmentation caused by imatinib: report of three cases.

Li CC, Malik SM, Blaeser BF, Dehni WJ, Kabani SP, Boyle N, Toner M, Woo SB
Head Neck Pathol 2012 Jun;6(2):290-5. Epub 2011 Dec 31 doi: 10.1007/s12105-011-0325-4. PMID: 22209988 Free PMC Article

Long-term survival following aggressive surgery and radiotherapy for pelvic fibromatosis.

Seoud M, Abbas J, Kaspar H, Khalil A, Geara F
Int J Gynecol Cancer 2005 Nov-Dec;15(6):1112-4. doi: 10.1111/j.1525-1438.2005.00171.x. PMID: 16343190

Diffuse intra-abdominal fibromatosis in association with bilateral ovarian fibromatosis and oedema.

Antoniuk P, Tjandra JJ, Lavery IC
Aust N Z J Surg 1993 Apr;63(4):315-8. doi: 10.1111/j.1445-2197.1993.tb00391.x. PMID: 8311821

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