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Supraventricular arrhythmia

MedGen UID:
96544
Concept ID:
C0428974
Disease or Syndrome
Synonym: Arrhythmias, supraventricular
SNOMED CT: Supraventricular arrhythmia (72654001)
 
HPO: HP:0005115

Definition

A type of arrhythmia that originates above the ventricles, whereby the electrical impulse propagates down the normal His Purkinje system similar to normal sinus rhythm. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSupraventricular arrhythmia

Conditions with this feature

Autosomal dominant familial hematuria-retinal arteriolar tortuosity-contractures syndrome
MedGen UID:
382033
Concept ID:
C2673195
Disease or Syndrome
The spectrum of COL4A1-related disorders includes: small-vessel brain disease of varying severity including porencephaly, variably associated with eye defects (retinal arterial tortuosity, Axenfeld-Rieger anomaly, cataract) and systemic findings (kidney involvement, muscle cramps, cerebral aneurysms, Raynaud phenomenon, cardiac arrhythmia, and hemolytic anemia). On imaging studies, small-vessel brain disease is manifest as diffuse periventricular leukoencephalopathy, lacunar infarcts, microhemorrhage, dilated perivascular spaces, and deep intracerebral hemorrhages. Clinically, small-vessel brain disease manifests as infantile hemiparesis, seizures, single or recurrent hemorrhagic stroke, ischemic stroke, and isolated migraine with aura. Porencephaly (fluid-filled cavities in the brain detected by CT or MRI) is typically manifest as infantile hemiparesis, seizures, and intellectual disability; however, on occasion it can be an incidental finding. HANAC (hereditary angiopathy with nephropathy, aneurysms, and muscle cramps) syndrome usually associates asymptomatic small-vessel brain disease, cerebral large vessel involvement (i.e., aneurysms), and systemic findings involving the kidney, muscle, and small vessels of the eye. Two additional phenotypes include isolated retinal artery tortuosity and nonsyndromic autosomal dominant congenital cataract.

Professional guidelines

PubMed

Gutierrez C, Blanchard DG
Am Fam Physician 2016 Sep 15;94(6):442-52. PMID: 27637120
Al-Zaiti SS, Magdic KS
Crit Care Nurs Clin North Am 2016 Sep;28(3):309-16. Epub 2016 Jun 7 doi: 10.1016/j.cnc.2016.04.005. PMID: 27484659
Penninga EI, Graudal N, Ladekarl MB, Jürgens G
Basic Clin Pharmacol Toxicol 2016 Jan;118(1):37-44. Epub 2015 Jul 28 doi: 10.1111/bcpt.12434. PMID: 26096314

Recent clinical studies

Etiology

Balik M, Maly M, Brozek T, Rulisek J, Porizka M, Sachl R, Otahal M, Brestovansky P, Svobodova E, Flaksa M, Stach Z, Horejsek J, Volny L, Jurisinova I, Novotny A, Trachta P, Kunstyr J, Kopecky P, Tencer T, Pazout J, Belohlavek J, Duska F, Krajcova A, Waldauf P
Intensive Care Med 2023 Nov;49(11):1283-1292. Epub 2023 Sep 12 doi: 10.1007/s00134-023-07208-3. PMID: 37698594
Young M
Crit Care Nurs Clin North Am 2019 Mar;31(1):77-90. doi: 10.1016/j.cnc.2018.11.005. PMID: 30736937
Gutierrez C, Blanchard DG
Am Fam Physician 2016 Sep 15;94(6):442-52. PMID: 27637120
Penninga EI, Graudal N, Ladekarl MB, Jürgens G
Basic Clin Pharmacol Toxicol 2016 Jan;118(1):37-44. Epub 2015 Jul 28 doi: 10.1111/bcpt.12434. PMID: 26096314
Marrakchi S, Kanoun F, Idriss S, Kammoun I, Kachboura S
Herz 2015 Apr;40 Suppl 2:101-9. Epub 2014 Jul 4 doi: 10.1007/s00059-014-4123-0. PMID: 24990773

Diagnosis

Holmes S, Hornberger LK, Jaeggi E, Howley L, Moon-Grady AJ, Uzun O, Kaizer A, Gilicze O, Cuneo BF
Ultrasound Obstet Gynecol 2023 Oct;62(4):552-557. Epub 2023 Sep 6 doi: 10.1002/uog.26239. PMID: 37128167
Ramlakhan KP, Kauling RM, Schenkelaars N, Segers D, Yap SC, Post MC, Cornette J, Roos-Hesselink JW
Heart 2022 Oct 13;108(21):1674-1681. doi: 10.1136/heartjnl-2021-320451. PMID: 35086889Free PMC Article
Young M
Crit Care Nurs Clin North Am 2019 Mar;31(1):77-90. doi: 10.1016/j.cnc.2018.11.005. PMID: 30736937
Gutierrez C, Blanchard DG
Am Fam Physician 2016 Sep 15;94(6):442-52. PMID: 27637120
Marrakchi S, Kanoun F, Idriss S, Kammoun I, Kachboura S
Herz 2015 Apr;40 Suppl 2:101-9. Epub 2014 Jul 4 doi: 10.1007/s00059-014-4123-0. PMID: 24990773

Therapy

Balik M, Maly M, Brozek T, Rulisek J, Porizka M, Sachl R, Otahal M, Brestovansky P, Svobodova E, Flaksa M, Stach Z, Horejsek J, Volny L, Jurisinova I, Novotny A, Trachta P, Kunstyr J, Kopecky P, Tencer T, Pazout J, Belohlavek J, Duska F, Krajcova A, Waldauf P
Intensive Care Med 2023 Nov;49(11):1283-1292. Epub 2023 Sep 12 doi: 10.1007/s00134-023-07208-3. PMID: 37698594
Ramlakhan KP, Kauling RM, Schenkelaars N, Segers D, Yap SC, Post MC, Cornette J, Roos-Hesselink JW
Heart 2022 Oct 13;108(21):1674-1681. doi: 10.1136/heartjnl-2021-320451. PMID: 35086889Free PMC Article
Young M
Crit Care Nurs Clin North Am 2019 Mar;31(1):77-90. doi: 10.1016/j.cnc.2018.11.005. PMID: 30736937
Gutierrez C, Blanchard DG
Am Fam Physician 2016 Sep 15;94(6):442-52. PMID: 27637120
Penninga EI, Graudal N, Ladekarl MB, Jürgens G
Basic Clin Pharmacol Toxicol 2016 Jan;118(1):37-44. Epub 2015 Jul 28 doi: 10.1111/bcpt.12434. PMID: 26096314

Prognosis

Hygrell T, Stridh M, Friberg L, Svennberg E
Am J Cardiol 2021 Jul 15;151:57-63. doi: 10.1016/j.amjcard.2021.04.020. PMID: 34167689
Balik M, Matousek V, Maly M, Brozek T
Anaesthesiol Intensive Ther 2017;49(5):419-429. Epub 2017 Nov 18 doi: 10.5603/AIT.a2017.0061. PMID: 29151002
Hernandez-Betancor I, Izquierdo-Gomez MM, Garcia-Niebla J, Laynez-Cerdena I, Garcia-Gonzalez MJ, Barragan-Acea A, Irribarren-Sarria JL, Jimenez-Rivera JJ, Lacalzada-Almeida J
Curr Cardiol Rev 2017;13(4):263-273. doi: 10.2174/1573403X13666170713122600. PMID: 28707575Free PMC Article
Marrakchi S, Kanoun F, Idriss S, Kammoun I, Kachboura S
Herz 2015 Apr;40 Suppl 2:101-9. Epub 2014 Jul 4 doi: 10.1007/s00059-014-4123-0. PMID: 24990773
Corradi D
Cardiovasc Pathol 2014 Mar-Apr;23(2):71-84. Epub 2013 Dec 15 doi: 10.1016/j.carpath.2013.12.001. PMID: 24462196

Clinical prediction guides

Balik M, Maly M, Brozek T, Rulisek J, Porizka M, Sachl R, Otahal M, Brestovansky P, Svobodova E, Flaksa M, Stach Z, Horejsek J, Volny L, Jurisinova I, Novotny A, Trachta P, Kunstyr J, Kopecky P, Tencer T, Pazout J, Belohlavek J, Duska F, Krajcova A, Waldauf P
Intensive Care Med 2023 Nov;49(11):1283-1292. Epub 2023 Sep 12 doi: 10.1007/s00134-023-07208-3. PMID: 37698594
Xue L, Yang YC, Zhao Q, Zhao ZH, Zeng QX, Yang T, Luo Q, Liu BY, Ma XP, Liu ZH, Xiong CM
Clin Cardiol 2022 May;45(5):495-502. Epub 2022 Mar 7 doi: 10.1002/clc.23803. PMID: 35253244Free PMC Article
Hernandez-Betancor I, Izquierdo-Gomez MM, Garcia-Niebla J, Laynez-Cerdena I, Garcia-Gonzalez MJ, Barragan-Acea A, Irribarren-Sarria JL, Jimenez-Rivera JJ, Lacalzada-Almeida J
Curr Cardiol Rev 2017;13(4):263-273. doi: 10.2174/1573403X13666170713122600. PMID: 28707575Free PMC Article
Gutierrez C, Blanchard DG
Am Fam Physician 2016 Sep 15;94(6):442-52. PMID: 27637120
Karam R, Marcello S, Brooks RR, Corey AE, Moore A
Am J Cardiol 1998 Mar 19;81(6A):40D-46D. doi: 10.1016/s0002-9149(98)00152-0. PMID: 9537222

Recent systematic reviews

Shafi I, Hassan AAI, Akers KG, Bashir R, Alkhouli M, Weinberger JJ, Abidov A
Int J Cardiol 2020 Sep 15;315:29-35. Epub 2020 May 8 doi: 10.1016/j.ijcard.2020.05.017. PMID: 32434672
Salaminia S, Sayehmiri F, Angha P, Sayehmiri K, Motedayen M
BMC Cardiovasc Disord 2018 Jun 28;18(1):129. doi: 10.1186/s12872-018-0857-6. PMID: 29954320Free PMC Article
Lin Z, Ge H, Xue J, Wu G, Du J, Hu X, Zhao Q
Congenit Heart Dis 2017 Dec;12(6):711-720. Epub 2017 Aug 28 doi: 10.1111/chd.12503. PMID: 28845580
Penninga EI, Graudal N, Ladekarl MB, Jürgens G
Basic Clin Pharmacol Toxicol 2016 Jan;118(1):37-44. Epub 2015 Jul 28 doi: 10.1111/bcpt.12434. PMID: 26096314
Anselmino M, Battaglia A, Gallo C, Gili S, Matta M, Castagno D, Ferraris F, Giustetto C, Gaita F
J Cardiovasc Med (Hagerstown) 2015 Dec;16(12):795-801. doi: 10.2459/JCM.0000000000000239. PMID: 25806470

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