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Achenbach syndrome

MedGen UID:
99176
Concept ID:
C0473563
Pathologic Function
Synonyms: Achenbach Syndrome; Achenbach's syndrome; Paroxysmal hematoma of the finger; paroxysmal hematoma of the finger
SNOMED CT: Achenbach's syndrome (238824006); Paroxysmal hematoma of the finger (238824006)
 
Monarch Initiative: MONDO:0006520

Definition

A rare disorder which affects the volar surfaces of fingers. Clinical signs include recurrent, spontaneous or post-traumatic bruising of fingers. The clinical course of the resultant hematoma usually follows a pattern of resolution within days. [from NCI]

Term Hierarchy

Professional guidelines

PubMed

Knuuti J, Wijns W, Saraste A, Capodanno D, Barbato E, Funck-Brentano C, Prescott E, Storey RF, Deaton C, Cuisset T, Agewall S, Dickstein K, Edvardsen T, Escaned J, Gersh BJ, Svitil P, Gilard M, Hasdai D, Hatala R, Mahfoud F, Masip J, Muneretto C, Valgimigli M, Achenbach S, Bax JJ; ESC Scientific Document Group
Eur Heart J 2020 Jan 14;41(3):407-477. doi: 10.1093/eurheartj/ehz425. PMID: 31504439
Adler Y, Charron P, Imazio M, Badano L, Barón-Esquivias G, Bogaert J, Brucato A, Gueret P, Klingel K, Lionis C, Maisch B, Mayosi B, Pavie A, Ristic AD, Sabaté Tenas M, Seferovic P, Swedberg K, Tomkowski W; ESC Scientific Document Group
Eur Heart J 2015 Nov 7;36(42):2921-2964. Epub 2015 Aug 29 doi: 10.1093/eurheartj/ehv318. PMID: 26320112Free PMC Article
Erbel R, Aboyans V, Boileau C, Bossone E, Bartolomeo RD, Eggebrecht H, Evangelista A, Falk V, Frank H, Gaemperli O, Grabenwöger M, Haverich A, Iung B, Manolis AJ, Meijboom F, Nienaber CA, Roffi M, Rousseau H, Sechtem U, Sirnes PA, Allmen RS, Vrints CJ; ESC Committee for Practice Guidelines
Eur Heart J 2014 Nov 1;35(41):2873-926. Epub 2014 Aug 29 doi: 10.1093/eurheartj/ehu281. PMID: 25173340

Recent clinical studies

Etiology

Godoy A, Tabares AH
Vasc Med 2019 Aug;24(4):361-366. Epub 2019 Jun 4 doi: 10.1177/1358863X19849627. PMID: 31159682
Harper CM, Waters PM
J Hand Surg Am 2013 Oct;38(10):1980-2. Epub 2013 Sep 8 doi: 10.1016/j.jhsa.2013.07.022. PMID: 24021741

Diagnosis

Kadian-Dodov D
Med Clin North Am 2023 Sep;107(5):829-844. Epub 2023 Jun 4 doi: 10.1016/j.mcna.2023.04.005. PMID: 37541711
Chiang C, Gooderham MJ
J Cutan Med Surg 2022 Sep-Oct;26(5):544. Epub 2022 Jan 23 doi: 10.1177/12034754211073318. PMID: 35067101
Godoy A, Tabares AH
Vasc Med 2019 Aug;24(4):361-366. Epub 2019 Jun 4 doi: 10.1177/1358863X19849627. PMID: 31159682
Notomi K, Harada T
CMAJ 2019 May 27;191(21):E584. doi: 10.1503/cmaj.181293. PMID: 31133606Free PMC Article
Kordzadeh A, Caine PL, Jonas A, Rhodes KM, Panayiotopolous YP
Eur J Trauma Emerg Surg 2016 Aug;42(4):439-443. Epub 2015 Dec 15 doi: 10.1007/s00068-015-0610-0. PMID: 26669687

Prognosis

Aguirre-Bejarano P, Tuta-Quintero E, Mora-Karam C, Quiroga-Segura S, Pimentel J
WMJ 2023 Mar;122(1):74-76. PMID: 36940129
Godoy A, Tabares AH
Vasc Med 2019 Aug;24(4):361-366. Epub 2019 Jun 4 doi: 10.1177/1358863X19849627. PMID: 31159682
Harper CM, Waters PM
J Hand Surg Am 2013 Oct;38(10):1980-2. Epub 2013 Sep 8 doi: 10.1016/j.jhsa.2013.07.022. PMID: 24021741

Clinical prediction guides

Godoy A, Tabares AH
Vasc Med 2019 Aug;24(4):361-366. Epub 2019 Jun 4 doi: 10.1177/1358863X19849627. PMID: 31159682

Recent systematic reviews

Kordzadeh A, Caine PL, Jonas A, Rhodes KM, Panayiotopolous YP
Eur J Trauma Emerg Surg 2016 Aug;42(4):439-443. Epub 2015 Dec 15 doi: 10.1007/s00068-015-0610-0. PMID: 26669687

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