Hemangioblastoma

A benign tumor of the nervous system that may occur sporadically or in association with VON HIPPEL-LINDAU DISEASE. It accounts for approximately 2% of intracranial tumors, arising most frequently in the cerebellar hemispheres and vermis. Histologically, the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial cells and clusters of lipid-laden pseudoxanthoma cells. Usually solitary, these tumors can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial compartment. Cerebellar hemangioblastomas usually present in the third decade with INTRACRANIAL HYPERTENSION, and ataxia. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, pp2071-2)

Year introduced: 1994

PubMed search builder options

Subheadings:

Restrict to MeSH Major Topic.

Do not include MeSH terms found below this term in the MeSH hierarchy.

Tree Number(s): C04.557.645.375.380.370

MeSH Unique ID: D018325

Entry Terms:

• Hemangioblastomas
• Multiple Hemangioblastomas
• Hemangioblastoma, Multiple
• Hemangioblastomas, Multiple
• Multiple Hemangioblastoma

Previous Indexing:

• Hemangiosarcoma (1966-1993)

All MeSH Categories
Diseases Category
Neoplasms
Neoplasms by Histologic Type
Neoplasms, Vascular Tissue
Hemangioma
Hemangioma, Capillary
Hemangioblastoma