Erdheim-Chester Disease

A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.

Year introduced: 2003

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Tree Number(s): C15.604.250.410.224

MeSH Unique ID: D031249

Entry Terms:

• Erdheim Chester Disease
• Granulomatosis, Lipid
• Lipid Granulomatosis

Previous Indexing:

• Histiocytosis (1989-2002)
• Histiocytosis, Langerhans-Cell (1988-2002)
• Histiocytosis, Non-Langerhans-Cell (1991-2002)
• Lipidosis (1979-2002)
• Xanthomatosis (1979-2002)

All MeSH Categories
Diseases Category
Hemic and Lymphatic Diseases
Lymphatic Diseases
Histiocytosis
Histiocytosis, Non-Langerhans-Cell
Erdheim-Chester Disease