Malignant Atrophic Papulosis
Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
Year introduced: 2008
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Subheadings:
Tree Number(s): C14.907.137.520, C14.907.940.530, C17.800.862.457
MeSH Unique ID: D054853
Entry Terms:
- Atrophic Papuloses, Malignant
- Atrophic Papulosis, Malignant
- Malignant Atrophic Papuloses
- Papuloses, Malignant Atrophic
- Degos Syndrome
- Syndrome, Degos
- Degos's Malignant Atrophic Papulosis
- Degos Disease
- Disease, Degos
- Kohlmeier-Degos Disease
- Disease, Kohlmeier-Degos
- Papulosis, Malignant Atrophic
- Erythrokeratoderma en cocardes