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Porokeratosis

A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.

Year introduced: 1993

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Subheadings:

Tree Number(s): C16.320.850.730, C17.800.428.750, C17.800.827.730

MeSH Unique ID: D017499

Entry Terms:

  • Porokeratosis, Disseminated Superficial Actinic
  • Disseminated Superficial Actinic Porokeratosis
  • Porokeratosis, Palmoplantar
  • Palmoplantar Porokeratosis
  • Keratoderma Palmoplantar, Punctate Type 2
  • Porokeratosis Plantaris, Palmaris, Et Disseminata
  • Porokeratosis Plantaris Palmaris et Disseminata
  • Porokeratosis, Palmar, Plantar, And Disseminated 1
  • Porokeratosis Palmaris et Plantaris Disseminata
  • Type 2 Punctate PPK
  • Porokeratosis, Linear
  • Linear Porokeratosis
  • Porokeratosis, Mibelli
  • Mibelli Porokeratosis
  • Porokeratosis of Mibelli
  • Porokeratosis, Punctate
  • Punctate Porokeratosis
  • Porokeratosis, Disseminated Superficial Actinic 2
  • Porokeratosis, Disseminated Superficial Actinic, 2

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