Idiopathic dilation cardiomyopathy [Supplementary Concept]
Dilated cardiomyopathy that is characterized by cardiac dilatation and reduced systolic function. It is the most frequent form of cardiomyopathy and accounts for more than half of all cardiac transplantations performed in children between 1 and 10 years of age. For CMD1A, 20 to 30% of cases are heritable and show an autosomal dominant inheritance pattern. Germline mutations in the LMNA gene have been identified. OMIM: 115200
Date introduced: August 25, 2010
MeSH Unique ID: C536277
Heading Mapped to:
Entry Terms:
- Cardiomyopathy, Dilated, With Conduction Defect
- Dilated cardiomyopathy with conduction defect
- Cardiomyopathy, Dilated, 1h