Hirschsprung Disease
Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.
Year introduced: 1983
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Subheadings:
Tree Number(s): C06.198.439, C06.405.469.158.701.439, C16.131.314.439
MeSH Unique ID: D006627
Entry Terms:
- Disease, Hirschsprung
- Megacolon, Congenital
- Hirschsprung's Disease
- Disease, Hirschsprung's
- Hirschsprungs Disease
- Megacolon, Aganglionic
- Aganglionic Megacolon
- Congenital Megacolon
- Aganglionosis, Rectosigmoid Colon
- Rectosigmoid Colon Aganglionosis
- Rectosigmoid Aganglionosis
- Aganglionosis, Rectosigmoid
- Congenital Intestinal Aganglionosis
- Aganglionosis, Colonic
- Colonic Aganglionosis
- Total Colonic Aganglionosis
- Aganglionosis, Total Colonic
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