The authors report the case of a 6-month-old boy seen at Ankara Numune Hospital because of a papillomatous lesion centrally located on the chin. The lesion was excised under local anesthesia, and histologic examination revealed numerous eccrine glands and muscle bundles, neuronal tissues, and fatty tissue covered by stratified squamous epithelium. According to the histologic findings, the lesion was diagnosed as rhabdomyomatous mesenchymal hamartoma, which is known to be a rare lesion of childhood.