Congenital simple hamartoma of the retinal pigment epithelium (CSHRPE) is a rare tumor speculated to arise from the retinal pigment epithelium (RPE). A case of CSHRPE is presented herein along with the related literature. A healthy 20-year-old Middle-Eastern man was evaluated for an asymptomatic retinal lesion found on routine examination of his left eye. Fluorescein angiogram, spectral domain optical coherence tomography, and A and B scan ultrasonography confirmed the suspected clinical diagnosis. For the first time high-definition OCT images are shown, which have an RPE origin for this tumor.
Keywords: CSHRPE; OCT; RPE; congenital simple hamartoma of the retinal pigment epithelium; hamartoma.