Pigment dispersion syndrome associated with optic nerve melanocytoma
Arch Soc Esp Oftalmol. 2015 Oct;90(10):484-6.
doi: 10.1016/j.oftal.2015.04.005.
Epub 2015 May 23.
[Article in
English,
Spanish]
Affiliations
- 1 Unidad de Glaucoma, Servicio de Oftalmología, Hospital Clínico San Carlos, Instituto de Investigación Sanitaria del Hospital Clínico San Carlos (IdISSC), Madrid, España. Electronic address: Almudena.asorey@gmail.com.
- 2 Unidad de Glaucoma, Servicio de Oftalmología, Hospital Clínico San Carlos, Instituto de Investigación Sanitaria del Hospital Clínico San Carlos (IdISSC), Madrid, España.
Abstract
Case report:
A 60-year old patient was referred for cataract surgery. The examination showed retrokeratic pigment in the left eye, which had an intraocular pressure of 24 mm Hg. The funduscopy showed a brown lesion on the left optic disk, with adjacent vitreous seeding of pigment. The patient was thus diagnosed with secondary pigment dispersion syndrome due to optic disk melanocytoma.
Discussion:
Although melanocytoma is most commonly a benign, stationary tumor, it may present with major complications leading to significant visual loss. A patient with melanocytoma of the optic disk should be examined periodically.
Keywords:
Glaucoma melanocitomalítico; Melanocitoma; Melanocitoma de nervio óptico; Melanocytic glaucoma; Melanocytoma; Optic disk melanocytoma; Pigment dispersion syndrome; Síndrome de dispersión pigmentaria.
Copyright © 2014 Sociedad Española de Oftalmología. Published by Elsevier España, S.L.U. All rights reserved.
MeSH terms
-
Adrenergic alpha-2 Receptor Agonists / administration & dosage
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Adrenergic alpha-2 Receptor Agonists / therapeutic use
-
Brimonidine Tartrate / administration & dosage
-
Brimonidine Tartrate / therapeutic use
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Cataract / complications
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Cataract Extraction
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Exfoliation Syndrome / etiology*
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Female
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Follow-Up Studies
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Humans
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Incidental Findings
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Middle Aged
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Nevus, Pigmented / complications*
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Nevus, Pigmented / diagnosis
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Ocular Hypertension / drug therapy
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Ocular Hypertension / etiology
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Ophthalmic Solutions
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Optic Nerve Neoplasms / complications*
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Optic Nerve Neoplasms / diagnosis
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Watchful Waiting
Substances
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Adrenergic alpha-2 Receptor Agonists
-
Ophthalmic Solutions
-
Brimonidine Tartrate