Pancreatic insufficiency in Cystic Fibrosis

Vikesh K Singh; Sarah Jane Schwarzenberg

doi:10.1016/j.jcf.2017.06.011

Pancreatic insufficiency in Cystic Fibrosis

J Cyst Fibros. 2017 Nov:16 Suppl 2:S70-S78. doi: 10.1016/j.jcf.2017.06.011.

Authors

Vikesh K Singh¹, Sarah Jane Schwarzenberg²

Affiliations

¹ Division of Gastroenterology, Johns Hopkins University School of Medicine, Baltimore, MD, United States.
² Pediatric Gastroenterology, Hepatology, and Nutrition, University of Minnesota Masonic Children's Hospital, Minneapolis, MN, United States. Electronic address: schwa005@umn.edu.

PMID: 28986019
DOI: 10.1016/j.jcf.2017.06.011

Abstract

Pancreatic insufficiency (PI) affects about 85% of the cystic fibrosis population. Although most are PI soon after birth, some will have pancreatic sufficiency (PS) for some or all of their life. Understanding the clinical presentation, diagnosis, and management of PI is crucial to the care of people with cystic fibrosis.

Keywords: Fat soluble vitamins; Pancreas; Pancreatic enzyme therapy; Pancreatic insufficiency; Pancreatitis.

Publication types

Review

MeSH terms

Cystic Fibrosis* / complications
Cystic Fibrosis* / therapy
Disease Management
Exocrine Pancreatic Insufficiency* / diagnosis
Exocrine Pancreatic Insufficiency* / etiology
Exocrine Pancreatic Insufficiency* / physiopathology
Exocrine Pancreatic Insufficiency* / therapy
Humans