IgG4-related orbital disease
Arch Soc Esp Oftalmol (Engl Ed). 2018 Oct;93(10):494-496.
doi: 10.1016/j.oftal.2018.04.003.
Epub 2018 Jun 1.
[Article in
English,
Spanish]
Affiliations
- 1 Servicio de Reumatología, Hospital Privado Universitario de Córdoba, Córdoba, Argentina.
- 2 Servicio de Reumatología, Hospital Privado Universitario de Córdoba, Córdoba, Argentina. Electronic address: baenashospitalprivado@gmail.com.
- 3 Servicio de Anatomía Patológica, Hospital Privado Universitario de Córdoba, Córdoba, Argentina.
- 4 Servicio de Oftalmología, Hospital Privado Universitario de Córdoba, Córdoba, Argentina.
Abstract
Case report:
The case is presented of a 64-year-old woman with bilateral palpebral swelling and dacryoadenitis, exophthalmos, and a history of chronic rhinitis and asthma. An increase in serum IgG4 was observed, and an incisional biopsy of lacrimal glands was performed, which showed fibrosis and a lymphoplasmacytic infiltrate with IgG4 producing cells.
Discussion:
Orbital involvement in IgG4-related disease is frequent. Bilateral dacryoadenitis is the most common manifestation. Histopathology is essential for the diagnosis and to exclude malignancy.
Keywords:
Dacrioadenitis; Dacryoadenitis; Enfermedad relacionada con IgG4; IgG4-related disease; Inflamación orbitaria inespecífica; Non-specific orbital inflammation; Orbit; Órbita.
Copyright © 2018 Sociedad Española de Oftalmología. Publicado por Elsevier España, S.L.U. All rights reserved.
MeSH terms
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Asthma / complications
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Biopsy
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Dacryocystitis / etiology*
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Dacryocystitis / immunology
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Dacryocystitis / pathology
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Diagnosis, Differential
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Exophthalmos / etiology
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Female
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Fibrosis
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Humans
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Immunoglobulin G4-Related Disease / complications
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Immunoglobulin G4-Related Disease / diagnosis*
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Immunoglobulin G4-Related Disease / pathology
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Lacrimal Apparatus / immunology
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Lacrimal Apparatus / pathology
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Middle Aged
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Orbital Diseases / complications
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Orbital Diseases / diagnosis*
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Orbital Diseases / immunology
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Orbital Diseases / pathology
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Orbital Neoplasms / diagnosis
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Plasma Cells / pathology
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Rhinitis / complications
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Salivary Glands, Minor / pathology
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Xerophthalmia / complications