Renovascular hypertension is known to occur due to varied causes. Absence of Renal artery stenosis or changes in renal vascular flow make it tough to establish a diagnosis of renovascular hypertension in the absence of invasive investigations. Segmental renal hypoplasia is not only a rare cause for renin mediated hypertension but also requires expertise and high index of suspicion while evaluating children with hypertension. We describe the classical imaging findings of a child with secondary hypertension which was due to hypoplasia of a renal segment.