Coated aorta in Erdheim-Chester disease

Rheumatology (Oxford). 2021 Feb 1;60(2):986-987. doi: 10.1093/rheumatology/keaa430.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Antirheumatic Agents / administration & dosage
  • Aorta / diagnostic imaging*
  • Biopsy / methods
  • Computed Tomography Angiography / methods*
  • Cyclophosphamide / administration & dosage*
  • Echocardiography / methods
  • Erdheim-Chester Disease* / diagnosis
  • Erdheim-Chester Disease* / drug therapy
  • Erdheim-Chester Disease* / genetics
  • Erdheim-Chester Disease* / physiopathology
  • Female
  • Humans
  • Lymph Nodes / pathology*
  • Middle Aged
  • Mutation
  • Pericardial Effusion* / diagnostic imaging
  • Pericardial Effusion* / etiology
  • Prednisone / administration & dosage*
  • Proto-Oncogene Proteins B-raf / genetics
  • Treatment Outcome

Substances

  • Antirheumatic Agents
  • Cyclophosphamide
  • BRAF protein, human
  • Proto-Oncogene Proteins B-raf
  • Prednisone