Monoclonal gammopathy of renal significance: Early diagnosis is key

Nefrologia (Engl Ed). 2021 Sep-Oct;41(5):502-513. doi: 10.1016/j.nefroe.2021.11.008.

Abstract

Monoclonal gammopathy of renal significance is a clinical-pathological entity grouping renal disorders secondary to the secretion of a monoclonal immunoglobulin synthesized by a B-cell-derived clone and/or plasma cells in a patient with no diagnostic criteria for multiple myeloma. This term applies to a concept recently introduced owing to the need to differentiate this entity from monoclonal gammopathy of undetermined significance, given the negative prognostic impact of its high morbidity and mortality resulting from both renal and systemic involvement, occasionally even progressing to advanced chronic kidney disease. The renal damage occurs via both direct pathogenic mechanisms, with the deposition of the monoclonal protein in different renal structures, as well as indirect mechanisms, acting as an autoantibody provoking dysregulation of the alternative complement pathway. The detection of this monoclonal protein and an early hematologic study are essential, as is the need for a kidney biopsy to establish the associated nephropathological diagnosis. Consequently, this then leads to the start of specific hematologic treatment to detain the production of the monoclonal protein and minimize renal and systemic injury.

Keywords: Cadena ligera libre; Enfermedad por depósito de inmunoglobulina monoclonal; Free light chain; Gammapatía monoclonal; Gammapatía monoclonal de significado incierto; Gammapatía monoclonal de significado renal; Glomerulonefritis membranoproliferativa con depósitos de inmunoglobulinas monoclonales; Membranoproliferative glomerulonephritis with monoclonal immunoglobulin deposits; Mieloma múltiple; Monoclonal gammopathy; Monoclonal gammopathy of renal significance; Monoclonal gammopathy of uncertain significance; Monoclonal immunoglobulin deposition disease; Multiple myeloma.

MeSH terms

  • Early Diagnosis
  • Humans
  • Kidney / pathology
  • Monoclonal Gammopathy of Undetermined Significance* / complications
  • Monoclonal Gammopathy of Undetermined Significance* / diagnosis
  • Monoclonal Gammopathy of Undetermined Significance* / pathology
  • Paraproteinemias* / complications
  • Paraproteinemias* / diagnosis
  • Paraproteins
  • Renal Insufficiency, Chronic* / complications

Substances

  • Paraproteins