Simultaneous absence of alpha-1,4-glucosidase and alpha-1,6-glucosidase activities (pH 4) in tissues of children with type II glycogen storage disease

MeSH terms

• Autopsy
• Biopsy
• Child
• Culture Techniques
• Disaccharides
• Drug Stability
• Fibroblasts / enzymology
• Glucosidases / antagonists & inhibitors
• Glucosidases / metabolism*
• Glycogen
• Glycogen Storage Disease / enzymology*
• Glycoside Hydrolases / metabolism
• Glycosides
• Humans
• Hydrogen-Ion Concentration
• Kinetics
• Leukocytes / enzymology
• Liver / enzymology*
• Lysosomes / enzymology
• Maltose
• Muscles / enzymology*
• Myocardium / enzymology