No abstract available
MeSH terms
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Adolescent
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Amino Acid Metabolism, Inborn Errors / blood
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Amino Acid Metabolism, Inborn Errors / metabolism*
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Amino Acid Metabolism, Inborn Errors / therapy
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Amino Acid Metabolism, Inborn Errors / urine
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Ammonia / blood
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Ammonia / metabolism*
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Arginine / metabolism
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Arginine / therapeutic use
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Diet Therapy
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Growth Disorders / metabolism
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Humans
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Intellectual Disability / metabolism
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Intestinal Absorption
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Kidney Concentrating Ability
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Lysine / metabolism*
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Lysine / urine
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Male
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Protein Biosynthesis
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Syndrome
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Urea / metabolism
Substances
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Ammonia
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Urea
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Arginine
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Lysine