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Year | Number of Results |
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2016 | 1 |
2017 | 1 |
2018 | 5 |
2019 | 1 |
2024 | 0 |
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6 results
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Page 1
R560S: A class II CFTR mutation that is not rescued by current modulators.
J Cyst Fibros. 2019 Mar;18(2):182-189. doi: 10.1016/j.jcf.2018.07.001. Epub 2018 Jul 18.
J Cyst Fibros. 2019.
PMID: 30030066
Free article.
Genotype-phenotype correlation and functional studies in patients with cystic fibrosis bearing CFTR complex alleles.
Terlizzi V, Castaldo G, Salvatore D, Lucarelli M, Raia V, Angioni A, Carnovale V, Cirilli N, Casciaro R, Colombo C, Di Lullo AM, Elce A, Iacotucci P, Comegna M, Scorza M, Lucidi V, Perfetti A, Cimino R, Quattrucci S, Seia M, Sofia VM, Zarrilli F, Amato F.
Terlizzi V, et al.
J Med Genet. 2017 Apr;54(4):224-235. doi: 10.1136/jmedgenet-2016-103985. Epub 2016 Oct 13.
J Med Genet. 2017.
PMID: 27738188
Free article.
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Ivacaftor-induced sweat chloride reductions correlate with increases in airway surface liquid pH in cystic fibrosis.
Abou Alaiwa MH, Launspach JL, Grogan B, Carter S, Zabner J, Stoltz DA, Singh PK, McKone EF, Welsh MJ.
Abou Alaiwa MH, et al.
JCI Insight. 2018 Aug 9;3(15):e121468. doi: 10.1172/jci.insight.121468. eCollection 2018 Aug 9.
JCI Insight. 2018.
PMID: 30089726
Free PMC article.
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Changes in Lung Clearance Index in Preschool-aged Patients with Cystic Fibrosis Treated with Ivacaftor (GOAL): A Clinical Trial.
Ratjen F, Klingel M, Black P, Powers MR, Grasemann H, Solomon M, Sagel SD, Donaldson SH, Rowe SM, Rosenfeld M.
Ratjen F, et al.
Am J Respir Crit Care Med. 2018 Aug 15;198(4):526-528. doi: 10.1164/rccm.201802-0243LE.
Am J Respir Crit Care Med. 2018.
PMID: 29614238
Free PMC article.
No abstract available.
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PLCB3 Loss of Function Reduces Pseudomonas aeruginosa-Dependent IL-8 Release in Cystic Fibrosis.
Rimessi A, Bezzerri V, Salvatori F, Tamanini A, Nigro F, Dechecchi MC, Santangelo A, Prandini P, Munari S, Provezza L, Garreau de Loubresse N, Muller J, Ribeiro CMP, Lippi G, Gambari R, Pinton P, Cabrini G.
Rimessi A, et al.
Am J Respir Cell Mol Biol. 2018 Oct;59(4):428-436. doi: 10.1165/rcmb.2017-0267OC.
Am J Respir Cell Mol Biol. 2018.
PMID: 29668297
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Clinical Characteristics and Predictors of Reduced Survival for Adult-diagnosed Cystic Fibrosis. Analysis of the Canadian CF Registry.
Desai S, Wong H, Sykes J, Stephenson AL, Singer J, Quon BS.
Desai S, et al.
Ann Am Thorac Soc. 2018 Oct;15(10):1177-1185. doi: 10.1513/AnnalsATS.201801-037OC.
Ann Am Thorac Soc. 2018.
PMID: 29944384
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